Neonatal lupus erythematosus

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23Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Neonatal lupus erythematosus (NLE), also called neonatal lupus syndrome, is a rare condition that affects newborn babies. It occurs when certain antibodies from the mother cross the placenta during pregnancy and affect the developing baby. These antibodies, known as anti-Ro/SSA and anti-La/SSB, are found in mothers who may have lupus, Sjögren syndrome, or sometimes no known autoimmune disease at all. The mother may not even know she carries these antibodies until her baby is diagnosed. The most common signs of neonatal lupus include a skin rash that often appears on the face and scalp, and heart problems — most notably congenital heart block, where the electrical signals that control the heartbeat are disrupted. Other features can include low blood cell counts and liver problems. The skin rash and blood or liver issues usually resolve on their own within the first six months of life as the mother's antibodies naturally clear from the baby's system. However, congenital heart block is permanent and may require a pacemaker. Treatment depends on which parts of the body are affected. Skin rashes are managed by protecting the baby from sun exposure. Congenital heart block may need monitoring, medication, or pacemaker placement. Babies with blood count or liver abnormalities are monitored closely, as these typically improve without specific treatment. Early detection during pregnancy through maternal antibody screening can help doctors plan appropriate care at delivery.

Key symptoms:

Red or ring-shaped skin rash, often on the face and scalpSlow heartbeat in the baby (heart block)Low blood platelet count (easy bruising or bleeding)Low red blood cell count (anemia, pale skin)Low white blood cell countLiver inflammation or abnormal liver testsEnlarged liverEnlarged spleenSensitivity to sunlight making the rash worseFluid buildup around the heart (pericardial effusion)Heart failure in severe casesJaundice (yellowing of the skin)

Clinical phenotype terms (36)— hover any for plain English
Abnormality of blood and blood-forming tissuesHP:0001871ParakeratosisHP:0001036Atrioventricular blockHP:0001678Heart blockHP:0012722Malar rashHP:0025300
Inheritance

Multifactorial

Caused by a mix of several genes and environmental factors

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Neonatal lupus erythematosus.

View clinical trials →

No actively recruiting trials found for Neonatal lupus erythematosus at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Neonatal lupus erythematosus community →

Specialists

23 foundView all specialists →
JB
Jill P. Buyon
NEW YORK, NY
Specialist
PI on 1 active trial115 Neonatal lupus erythematosus publications
YR
Yanis RAMDANI
Specialist
PI on 1 active trial
ZL
Zhanguo Li
Specialist
PI on 7 active trials819 Neonatal lupus erythematosus publications
JM
Jill P. Buyon, MD
NEW YORK, NY
Specialist
PI on 2 active trials
FR
Frédéric Rieux-Laucat
Specialist
PI on 1 active trial12 Neonatal lupus erythematosus publications
MM
Monique Hinchcliff, MD
NORTH HAVEN, CT
Specialist
PI on 2 active trials
DM
David T. Teachey, MD
PHILADELPHIA, PA
Specialist
PI on 1 active trial
HP
Hao Trong Nguyen, PhD
Specialist
PI on 1 active trial
BM
Bettina F Cuneo, MD
AURORA, CO
Specialist
PI on 2 active trials
TP
Thuy Thu Nguyen, PhD
Specialist
PI on 1 active trial
AM
Alice Bertaina, MD
PALO ALTO, CA
Specialist
PI on 1 active trial1 Neonatal lupus erythematosus publication
PM
Paul Grimm, MD
MERRITT ISLAND, FL
Specialist
PI on 1 active trial
CP
Christine Pellegrini, PhD
PITTSBURGH, PA
Specialist
PI on 1 active trial
CS
Candace H Feldman, MD, ScD
BOSTON, MA
Specialist
PI on 2 active trials
AP
Antonio Luca Brucato, Prof
PORTLAND, ME
Specialist
PI on 1 active trial
VP
Valérie GOUILLEUX, PhD
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Neonatal lupus erythematosus.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Neonatal lupus erythematosus

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Does my baby have heart block, and if so, how severe is it? Will a pacemaker be needed?,How often will my baby need blood tests and heart monitoring?,Should I take hydroxychloroquine during future pregnancies to reduce the risk of NLE?,What is the chance that my next baby will also have neonatal lupus?,Will the skin rash leave any permanent marks or scars?,Is my baby at higher risk of developing lupus or other autoimmune diseases later in life?,Are there any activity restrictions my child should follow as they grow up?

Common questions about Neonatal lupus erythematosus

What is Neonatal lupus erythematosus?

Neonatal lupus erythematosus (NLE), also called neonatal lupus syndrome, is a rare condition that affects newborn babies. It occurs when certain antibodies from the mother cross the placenta during pregnancy and affect the developing baby. These antibodies, known as anti-Ro/SSA and anti-La/SSB, are found in mothers who may have lupus, Sjögren syndrome, or sometimes no known autoimmune disease at all. The mother may not even know she carries these antibodies until her baby is diagnosed. The most common signs of neonatal lupus include a skin rash that often appears on the face and scalp, and he

How is Neonatal lupus erythematosus inherited?

Neonatal lupus erythematosus follows a multifactorial inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Neonatal lupus erythematosus typically begin?

Typical onset of Neonatal lupus erythematosus is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Neonatal lupus erythematosus?

23 specialists and care centers treating Neonatal lupus erythematosus are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.