Muscle-eye-brain disease

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ORPHA:588OMIM:236670G71.0
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27Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Muscle-eye-brain disease (MEB disease) is a rare genetic condition that affects the muscles, eyes, and brain all at the same time. It belongs to a group of conditions called congenital muscular dystrophies, which means the muscle problems are present from birth. MEB disease is caused by changes (mutations) in genes that help add sugar molecules to proteins — a process called glycosylation. When this process does not work correctly, it affects how muscles, the brain, and the eyes develop. Babies born with MEB disease typically have very weak muscles (called hypotonia or 'floppy baby'), structural changes in the brain that can be seen on brain scans, and serious eye problems including glaucoma, nearsightedness, and abnormal retinas. Most children with MEB disease have significant intellectual disability and developmental delays. Seizures are also very common. There is currently no cure for MEB disease. Treatment focuses on managing symptoms, improving quality of life, and supporting development. This includes physical therapy, occupational therapy, seizure medications, and eye care. Early intervention and a strong team of specialists can make a meaningful difference in a child's comfort and development.

Also known as:

Key symptoms:

Very weak muscle tone from birth (floppy baby)Intellectual disability and significant developmental delaysSeizures or epilepsySevere nearsightedness (myopia)Glaucoma (high pressure in the eyes)Abnormal retina developmentStructural brain abnormalities visible on MRI (such as lissencephaly or cobblestone brain)Difficulty or inability to walk independentlyLimited or absent speechFeeding difficulties in infancyEnlarged head size (macrocephaly) in some casesAbnormal eye movements or crossed eyes (strabismus)Elevated muscle enzyme levels in blood (creatine kinase)

Clinical phenotype terms (23)— hover any for plain English
MeningoceleHP:0002435
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Muscle-eye-brain disease.

View clinical trials →

No actively recruiting trials found for Muscle-eye-brain disease at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Muscle-eye-brain disease community →

Specialists

Showing 25 of 27View all specialists →
LM
Laurent Servais, MD
Specialist
PI on 6 active trials1 Muscle-eye-brain disease publication
MM
Michio Hirano, MD
NEW YORK, NY
Specialist
PI on 10 active trials
WM
William B Rizzo, MD
ORLANDO, FL
Specialist
PI on 3 active trials1 Muscle-eye-brain disease publication
TD
Thomas Klopstock, Prof. Dr.
Specialist
PI on 3 active trials
DP
Debra Regier, M.D., Ph.D.
WASHINGTON, DC
Specialist
PI on 1 active trial
AP
Anne Chiaramello, Ph.D.
Specialist
PI on 1 active trial
AM
Anna Pawlowska, MD
DUARTE, CA
Specialist
PI on 3 active trials
MM
Matilda Hugerth, MSc
Specialist
PI on 1 active trial2 Muscle-eye-brain disease publications
MM
Monique Hinchcliff, MD
NORTH HAVEN, CT
Specialist
PI on 2 active trials
TP
Todd Durham, PhD
Specialist
PI on 1 active trial
MD
Michelangelo Mancuso, Prof. Dr.
Specialist
PI on 1 active trial
PP
Patrick Chinnery, Prof.
Specialist
PI on 1 active trial
KM
Kevin Houston, OD MSc
Specialist
PI on 1 active trial
AM
Ashish Gupta, MBBS, MPH
Specialist
PI on 4 active trials
CP
Chi Hornik, PharmD
DURHAM, NC
Specialist
PI on 1 active trial
AM
Amany Abdel Wahid, M.Sc
Specialist
PI on 1 active trial
MP
Moises Aguilar-Domingo, PhD
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Muscle-eye-brain disease.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Muscle-eye-brain disease

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which specific gene mutation does my child have, and how does that affect their prognosis?,What therapies should we start right away, and how often should they happen?,What seizure medications are recommended, and what are the warning signs that seizures are not well controlled?,How should we monitor my child's breathing, and when might breathing support be needed?,Are there any clinical trials or research studies we should consider enrolling in?,What specialists should be part of my child's care team, and how often should we see each one?,What support services and early intervention programs are available in our area?

Common questions about Muscle-eye-brain disease

What is Muscle-eye-brain disease?

Muscle-eye-brain disease (MEB disease) is a rare genetic condition that affects the muscles, eyes, and brain all at the same time. It belongs to a group of conditions called congenital muscular dystrophies, which means the muscle problems are present from birth. MEB disease is caused by changes (mutations) in genes that help add sugar molecules to proteins — a process called glycosylation. When this process does not work correctly, it affects how muscles, the brain, and the eyes develop. Babies born with MEB disease typically have very weak muscles (called hypotonia or 'floppy baby'), structu

How is Muscle-eye-brain disease inherited?

Muscle-eye-brain disease follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Muscle-eye-brain disease typically begin?

Typical onset of Muscle-eye-brain disease is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Muscle-eye-brain disease?

25 specialists and care centers treating Muscle-eye-brain disease are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.