Walker-Warburg syndrome

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ORPHA:899OMIM:236670G71.0
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6Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Walker-Warburg syndrome (WWS) is a very rare and severe genetic condition that affects the brain, eyes, and muscles. It belongs to a group of diseases called congenital muscular dystrophies, specifically those linked to problems with a process called glycosylation — the way the body attaches sugar molecules to proteins. When this process does not work correctly, it disrupts the normal development of the brain and other organs before birth. Walker-Warburg syndrome is sometimes also called Warburg syndrome, HARD syndrome (which stands for Hydrocephalus, Agyria, Retinal Dysplasia), or cerebro-ocular dysplasia-muscular dystrophy syndrome. Babies born with Walker-Warburg syndrome typically have a smooth brain (a condition called lissencephaly or agyria), fluid buildup in the brain (hydrocephalus), severe eye abnormalities, and very weak muscles. The brain does not form its normal folds and ridges, which severely affects brain function. Eye problems can include underdeveloped or malformed eyes, detached retinas, and cataracts, often leading to blindness. Muscle weakness is present from birth and tends to be profound. Unfortunately, there is currently no cure for Walker-Warburg syndrome. Treatment focuses on managing symptoms and keeping the child as comfortable as possible. This includes managing fluid in the brain, controlling seizures with medication, and providing supportive care. The condition is life-limiting, and most affected children do not survive beyond the first few years of life. Families are encouraged to work closely with a team of specialists and to seek support from palliative care services.

Also known as:

Key symptoms:

Smooth brain without normal folds (lissencephaly)Fluid buildup in the brain (hydrocephalus)Severe muscle weakness from birth (floppy baby)Eye abnormalities such as small eyes (microphthalmia) or absent eyes (anophthalmia)Detached retina leading to vision loss or blindnessCataracts (clouding of the eye lens)SeizuresIntellectual disability (severe)Difficulty feedingAbnormal brain structure including malformed cerebellumEncephalocele (brain tissue protruding through the skull) in some casesVery limited or absent voluntary movementBreathing difficulties

Clinical phenotype terms (50)— hover any for plain English
LissencephalyHP:0001339Aplasia/Hypoplasia involving the skeletal musculatureHP:0001460Abnormal cerebellar vermis morphologyHP:0002334Abnormal cortical gyrationHP:0002536Chorioretinal dysplasiaHP:0007731Retinal dysplasiaHP:0007973Metatarsus valgusHP:0010508Abnormal circulating aldolase concentrationHP:0012400Abnormal circulating creatine kinase concentrationHP:0040081Abnormal circulating lactate dehydrogenase concentrationHP:0045040
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Walker-Warburg syndrome.

View clinical trials →

No actively recruiting trials found for Walker-Warburg syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Walker-Warburg syndrome community →

Specialists

6 foundView all specialists →

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Walker-Warburg syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Walker-Warburg syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which specific gene mutation has been found in my child, and what does that mean for their prognosis?,What signs should prompt me to take my child to the emergency room immediately?,What specialists should be part of my child's care team, and how often should we see each one?,Are there any clinical trials or research studies that my child might be eligible for?,What support services are available for our family, including palliative care and respite care?,Since this is an autosomal recessive condition, what is the chance that a future pregnancy would be affected, and is prenatal testing available?,What can we do to maximize our child's comfort and quality of life?

Common questions about Walker-Warburg syndrome

What is Walker-Warburg syndrome?

Walker-Warburg syndrome (WWS) is a very rare and severe genetic condition that affects the brain, eyes, and muscles. It belongs to a group of diseases called congenital muscular dystrophies, specifically those linked to problems with a process called glycosylation — the way the body attaches sugar molecules to proteins. When this process does not work correctly, it disrupts the normal development of the brain and other organs before birth. Walker-Warburg syndrome is sometimes also called Warburg syndrome, HARD syndrome (which stands for Hydrocephalus, Agyria, Retinal Dysplasia), or cerebro-ocu

How is Walker-Warburg syndrome inherited?

Walker-Warburg syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Walker-Warburg syndrome typically begin?

Typical onset of Walker-Warburg syndrome is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Walker-Warburg syndrome?

6 specialists and care centers treating Walker-Warburg syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.