Tumor of endocrine glands

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ORPHA:182130
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29Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Tumor of endocrine glands (Orphanet code 182130) is a broad classification category encompassing neoplasms that arise within the endocrine system, which includes hormone-producing glands such as the thyroid, parathyroid, adrenal glands, pituitary gland, and the endocrine pancreas. These tumors may be benign (adenomas) or malignant (carcinomas) and can be functioning (hormone-secreting) or non-functioning. When functioning, they may cause clinical syndromes related to hormone overproduction, such as hyperthyroidism, Cushing syndrome, hyperaldosteronism, hyperparathyroidism, acromegaly, or hypoglycemia, depending on the gland and cell type involved. Endocrine gland tumors can occur sporadically or as part of hereditary tumor syndromes such as Multiple Endocrine Neoplasia (MEN) types 1, 2A, and 2B, Von Hippel-Lindau syndrome, or Carney complex. Symptoms vary widely depending on the specific gland affected and whether the tumor produces excess hormones. Common presentations include a palpable mass, hormonal imbalance symptoms, fatigue, weight changes, and metabolic disturbances. Some tumors are discovered incidentally on imaging studies performed for other reasons. Treatment approaches depend on the tumor type, location, size, and whether it is benign or malignant. Options include surgical resection, which remains the primary treatment for most endocrine tumors, as well as targeted therapies, radioactive iodine therapy (for thyroid cancers), hormone-suppressive medications, chemotherapy, and radiation therapy. Surveillance and monitoring of hormone levels are important components of long-term management. Genetic counseling and testing are recommended when a hereditary syndrome is suspected.

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

10 events
Apr 2026Stereotactic Body Radiotherapy Plus FAK and RAF/MEK Inhibition in Advanced Pancreatic Adenocarcinoma

Washington University School of Medicine — PHASE2

TrialNOT YET RECRUITING
Mar 2026Signatera-Guided CDK4/6 Inhibitor Therapy in Breast Cancer

Natera, Inc. — NA

TrialNOT YET RECRUITING
Feb 2026A Study of FG-M108+Chemotherapy vs Placebo+Chemotherapy in Claudin18.2-positive Pancreatic Cancer

FutureGen Biopharmaceutical (Beijing) Co., Ltd — PHASE3

TrialNOT YET RECRUITING
Feb 2026A Study to Evaluate the Effectiveness and Safety of Setidegrasib, Given With Either mFOLFIRINOX or NALIRIFOX Chemotherapies, in People With Pancreatic Cancer

Astellas Pharma Global Development, Inc. — PHASE3

TrialRECRUITING
Jan 2026Olaptesed With Pembrolizumab and Nanoliposomal Irinotecan or Gemcitabine/Nab-Paclitaxel in MSS Pancreatic Cancer

TME Pharma AG — PHASE2

TrialNOT YET RECRUITING
Jan 2026A Phase 1 Study to Evaluate Safety and Efficacy of XER-001 (Amifostine for Nasoduodenal Delivery) in Combination With Sterotactic Body Radiotherapy for Treatment in Patients With Locally Advanced Pancreatic Cancer.

Xerient Pharma — PHASE1, PHASE2

TrialRECRUITING
Dec 2025Alpha Radiation Emitters Device for the Treatment of Pancreatic Cancer Emitters for the Treatment of Locally Advanced Pancreatic Cancer

Alpha Tau Medical LTD. — NA

TrialRECRUITING
Aug 2025Safety & Feasibility of Ultrasound-assisted Non-invasive Measurement of Compressibility of the Thyroid Gland in Patients Scheduled for Surgical Removal

Insel Gruppe AG, University Hospital Bern — NA

TrialRECRUITING
Jul 2025A Real-world Study of Liposomal Irinotecan (Onivyde)-Based Therapy in Patients With Locally Advanced/Metastatic Pancreatic Cancer in China

RenJi Hospital

TrialNOT YET RECRUITING
Apr 2025PTM-101 in Pancreatic Ductal Adenocarcinoma (PDAC)

PanTher Therapeutics — PHASE1

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Tumor of endocrine glands.

View clinical trials →

No actively recruiting trials found for Tumor of endocrine glands at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Tumor of endocrine glands community →

Specialists

Showing 25 of 29View all specialists →
CM
Christelle De La Fouchardière, MD
Specialist
PI on 1 active trial
BP
BioNTech Responsible Person
Specialist
PI on 18 active trials
CF
Carmen C Solorzano, MD, FACS
OAKLAND, CA
Specialist
PI on 2 active trials
RM
Ravinder Grewal, MD
NEW YORK, NY
Specialist
PI on 2 active trials
AM
Andrew Poklepovic, MD
RICHMOND, VA
Specialist
PI on 3 active trials1 Tumor of endocrine glands publication
NM
Naoki Takahashi, M.D.
ROCHESTER, MN
Specialist
PI on 2 active trials
DM
Divyesh V Sejpal, MD
PHOENIX, AZ
Specialist
PI on 1 active trial
RC
Robert L Coleman
Anchorage, Alaska
Specialist

Rare Disease Specialist

PI on 1 active trial16 Tumor of endocrine glands publications
TM
Thanh H Dellinger, MD
DUARTE, CA
Specialist
PI on 1 active trial
AM
Ankona Ghosh, MD
LOS ANGELES, CA
Specialist
PI on 1 active trial1 Tumor of endocrine glands publication
FM
Funda Meric-Bernstam, MD
HOUSTON, TX
Specialist
PI on 1 active trial
AM
Alexander Olawaiye, MD
PITTSBURGH, PA
Specialist
PI on 1 active trial1 Tumor of endocrine glands publication
TC
Taiho Central
Specialist
PI on 2 active trials
AM
Arthur Bertolino, MD
HOLLAND, MI
Specialist
PI on 1 active trial1 Tumor of endocrine glands publication
GM
Gilberto Lopes, MD
MIAMI, FL
Specialist
PI on 1 active trial1 Tumor of endocrine glands publication
MM
Mustafa Raoof, MD
DUARTE, CA
Specialist
PI on 1 active trial
MM
Marco Braga, MD
Specialist
PI on 1 active trial
WM
William E Gillanders, M.D.
MILWAUKIE, OR
Specialist
PI on 1 active trial
AM
Angeles A Secord, MD
DURHAM, NC
Specialist
PI on 3 active trials1 Tumor of endocrine glands publication
BM
Ben Tran, Medicine
Specialist
PI on 1 active trial1 Tumor of endocrine glands publication
AM
Andrea Enzinger, MD
BOSTON, MA
Specialist
PI on 1 active trial1 Tumor of endocrine glands publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Tumor of endocrine glands.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Tumor of endocrine glands

Disease timeline:

New recruiting trial: Multicenter Study of Circulating Tumor DNA in Patients With Pancreatic Cancer Using a Personalized Panel

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: Safety & Feasibility of Ultrasound-assisted Non-invasive Measurement of Compressibility of the Thyroid Gland in Patients Scheduled for Surgical Removal

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: Intraoperative Hypotension in Pancreatoduodenectomy: A Randomized Trial of General Versus Combined Anesthesia

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: Evaluate the Safety and Efficacy of BGT007H Cell Therapy in Patients With Relapsed/Refractory Pancreatic Cancer

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: A Phase I Clinical Study of IX001 TCR-T Injection in the Treatment of Advanced Pancreatic Cancer Patients With KRAS G12V Mutation

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: Preoperative Hemogram Parameters and BRAF Molecular Test Detected by Bethesda 3 Cytology.

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: Echo-endoscopy Biopsy Impact on the Circulating Tumor Cell Level

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: A Study Evaluating Anvumetostat in Combination With Other Therapies in Participants With Advanced Gastrointestinal, Biliary Tract, or Pancreatic Cancers With Homozygous Methylthioadenosine Phosphorylase (MTAP)-Deletion (MTAPESTRY 103)

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: PTM-101 in Pancreatic Ductal Adenocarcinoma (PDAC)

A new clinical trial is recruiting patients for Tumor of endocrine glands

New recruiting trial: PACAREG: a Multicenter Registry Trial in Pancreatic Ductal Adencarcinoma

A new clinical trial is recruiting patients for Tumor of endocrine glands

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Common questions about Tumor of endocrine glands

What is Tumor of endocrine glands?

Tumor of endocrine glands (Orphanet code 182130) is a broad classification category encompassing neoplasms that arise within the endocrine system, which includes hormone-producing glands such as the thyroid, parathyroid, adrenal glands, pituitary gland, and the endocrine pancreas. These tumors may be benign (adenomas) or malignant (carcinomas) and can be functioning (hormone-secreting) or non-functioning. When functioning, they may cause clinical syndromes related to hormone overproduction, such as hyperthyroidism, Cushing syndrome, hyperaldosteronism, hyperparathyroidism, acromegaly, or hypog

Which specialists treat Tumor of endocrine glands?

25 specialists and care centers treating Tumor of endocrine glands are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.