Corticobasal syndrome

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5Active trials40Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Corticobasal syndrome (CBS), sometimes called corticobasal degeneration syndrome, is a rare neurological condition that affects the brain's ability to control movement and thinking. It belongs to a group of diseases called neurodegenerative disorders, meaning brain cells gradually break down over time. CBS typically affects one side of the body more than the other, causing stiffness, difficulty moving a limb, and a strange feeling that the affected arm or leg has a "mind of its own" — a phenomenon called alien limb syndrome. Over time, the condition can also affect memory, language, and the ability to perform everyday tasks. The underlying cause of CBS is the abnormal buildup of a protein called tau in certain areas of the brain, particularly the cortex (the outer layer) and the basal ganglia (deep brain structures involved in movement). However, CBS is a clinical diagnosis, meaning it describes a pattern of symptoms. In some cases, the underlying brain pathology may turn out to be Alzheimer's disease, progressive supranuclear palsy, or other conditions rather than true corticobasal degeneration. There is currently no cure for corticobasal syndrome, and no treatment can slow or stop the disease from progressing. Treatment focuses on managing symptoms and improving quality of life. Medications such as levodopa (used in Parkinson's disease) are sometimes tried but usually provide limited benefit. Physical therapy, occupational therapy, and speech therapy play important roles in helping patients maintain function for as long as possible. Research is ongoing to better understand the disease and develop new therapies.

Key symptoms:

Stiffness and rigidity in one arm or legDifficulty controlling movements on one side of the bodyAlien limb phenomenon — a limb that seems to move on its ownJerky, involuntary muscle movements (myoclonus)Difficulty with balance and walkingTrouble performing skilled hand movements like buttoning a shirtSlowed movement (bradykinesia)Abnormal posture of a hand or foot (dystonia)Speech and language difficultiesTrouble understanding or using numbersMemory problemsDifficulty swallowingChanges in behavior or personalityLoss of sensation or numbness in a limbDepression or apathy

Clinical phenotype terms (22)— hover any for plain English
Progressive extrapyramidal muscular rigidityHP:0007158Frontal release signsHP:0000743AkinesiaHP:0002304Oromotor apraxiaHP:0007301Limb apraxiaHP:0030217Limb myoclonusHP:0045084Speech apraxiaHP:0011098
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Late onset

Begins later in life, typically after age 50

Orphanet ↗NORD ↗

FDA & Trial Timeline

8 events
Feb 2026Digital Measurements of Motor and Voice Functions in FTD

BioSensics

TrialNOT YET RECRUITING
Dec 2025Research Study for Patients With Neurological Diseases Which Evaluates the Patient Experience of the MemorEM Device

eQ8Health Corporation d/b/a CareONE Concierge — NA

TrialENROLLING BY INVITATION
Jul 2025Pilot Trial Evaluating Patient Experience With the MemorEM for Patients With Neurological Diseases

NeuroEM Therapeutics, Inc. — NA

TrialENROLLING BY INVITATION
Jun 2025STELLA-FTD: Examination of a Behavior Change Intervention for FTD Family Care Partners

Oregon Health and Science University — NA

TrialRECRUITING
Oct 2024The CurePSP Genetics Program

Massachusetts General Hospital

TrialRECRUITING
Apr 2024Scrambler Therapy for Corticobasal Syndrome-Associated Pain

Johns Hopkins University — NA

TrialRECRUITING
Dec 2023PROFIL Study to Investigate the Effect of GPB on NfL Levels in Patients With Corticobasal Syndrome (CBS)

Technical University of Munich — PHASE2

TrialACTIVE NOT RECRUITING
Apr 2022Music and Brain Stimulation for Upper Extremity Performance in Patients With Corticobasal Syndrome

Johns Hopkins University — NA

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Corticobasal syndrome.

5 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

5 recruitingView all trials with filters →
Phase 21 trial
PROFIL Study to Investigate the Effect of GPB on NfL Levels in Patients With Corticobasal Syndrome (CBS)
Phase 2
Active
· Sites: Munich, Bavaria; Munich, Bavaria · Age: 1899 yrs
N/A3 trials
Scrambler Therapy for Corticobasal Syndrome-Associated Pain
N/A
Actively Recruiting
PI: Alexander Pantelyat, MD (Department of Neurology, Johns Hopkins School of M) · Sites: Baltimore, Maryland · Age: 5089 yrs
Music and Brain Stimulation for Upper Extremity Performance in Patients With Corticobasal Syndrome
N/A
Active
PI: Alexander Pantelyat, MD (Department of Neurology, Johns Hopkins School of M) · Sites: Baltimore, Maryland · Age: 1889 yrs
STELLA-FTD: Examination of a Behavior Change Intervention for FTD Family Care Partners
N/A
Actively Recruiting
PI: Allison Lindauer, PhD, APRN (Oregon Health and Science University) · Sites: Portland, Oregon · Age: 18100 yrs
Other1 trial
The CurePSP Genetics Program
Actively Recruiting
· Sites: Boston, Massachusetts · Age: 3599 yrs

Specialists

Showing 25 of 40View all specialists →
AM
Alexander Pantelyat, MD
BALTIMORE, MD
Specialist
PI on 2 active trials
BM
benzi Kluger, MD
AURORA, CO
Specialist
PI on 1 active trial
AP
Adam Boxer, MD, PhD
SAN FRANCISCO, CA
Specialist
PI on 12 active trials
AM
Audrey Gabelle, MD
Specialist
PI on 1 active trial1 Corticobasal syndrome publication
TP
Tyler Roncero, Ph.D
Specialist
PI on 1 active trial
LP
Laura Andres-Martin, PhD
Specialist
PI on 1 active trial
HM
Howard Chertkow, MD
Specialist
PI on 1 active trial
AA
Allison Lindauer, PhD, APRN
PORTLAND, OR
Specialist
PI on 1 active trial
AC
Aimee Mooney, MA, CCC-SLP
Specialist
PI on 1 active trial
AP
Adam L. Boxer, M.D., Ph.D.
SAN FRANCISCO, CA
Specialist
PI on 2 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Corticobasal syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Corticobasal syndrome

Disease timeline:

New recruiting trial: Scrambler Therapy for Corticobasal Syndrome-Associated Pain

A new clinical trial is recruiting patients for Corticobasal syndrome

New recruiting trial: STELLA-FTD: Examination of a Behavior Change Intervention for FTD Family Care Partners

A new clinical trial is recruiting patients for Corticobasal syndrome

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the expected progression of my symptoms, and what should I watch for next?,Are there any medications that might help with my stiffness, muscle jerks, or other symptoms?,What types of therapy — physical, occupational, or speech — would benefit me most right now?,Should I consider genetic testing, especially if there is a family history of brain diseases?,Are there any clinical trials I might be eligible for?,When should we start discussing advance care planning and palliative care options?,What resources and support groups are available for me and my family?

Common questions about Corticobasal syndrome

What is Corticobasal syndrome?

Corticobasal syndrome (CBS), sometimes called corticobasal degeneration syndrome, is a rare neurological condition that affects the brain's ability to control movement and thinking. It belongs to a group of diseases called neurodegenerative disorders, meaning brain cells gradually break down over time. CBS typically affects one side of the body more than the other, causing stiffness, difficulty moving a limb, and a strange feeling that the affected arm or leg has a "mind of its own" — a phenomenon called alien limb syndrome. Over time, the condition can also affect memory, language, and the ab

How is Corticobasal syndrome inherited?

Corticobasal syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Corticobasal syndrome typically begin?

Typical onset of Corticobasal syndrome is late onset. Age of onset can vary across affected individuals.

Are there clinical trials for Corticobasal syndrome?

Yes — 5 recruiting clinical trials are currently listed for Corticobasal syndrome on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Corticobasal syndrome?

25 specialists and care centers treating Corticobasal syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.