Bullous pemphigoid

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4Active trials20Specialists8Treatment centers1Financial resources

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Bullous pemphigoid (BP) is a rare skin disease where the body's own immune system mistakenly attacks a thin layer just beneath the outer skin. This causes large, fluid-filled blisters to form, most often on the arms, legs, belly, and groin. The blisters can be very itchy and painful, and the skin around them often looks red or inflamed. Before the blisters appear, many people experience intense itching or a rash that looks like hives for weeks or even months. Bullous pemphigoid is classified as an autoimmune blistering disease. It is the most common condition in this group of disorders. It mainly affects older adults, typically those over 60 years of age, though it can rarely occur in younger people and even children. The exact trigger is not always known, but certain medications, neurological conditions, and other health problems have been linked to its development. Treatment focuses on calming the immune system and healing the skin. Corticosteroids, especially a cream called clobetasol propionate applied to the skin, are often the first choice. Oral steroids like prednisone are also commonly used. Other medicines that suppress the immune system, such as doxycycline, dapsone, methotrexate, or azathioprine, may be added. A newer targeted therapy called dupilumab has shown promise. With proper treatment, many people achieve remission, meaning the disease goes quiet, though it can come back.

Key symptoms:

Large, tense fluid-filled blisters on the skinIntense itching, often severeRed or inflamed skin around the blistersHive-like rash before blisters appearBlisters on the arms, legs, belly, and groinBlisters in the mouth or other mucous membranes (less common)Skin that is tender or painful to touchBlisters that may break open and form soresThickened or crusted skin after blisters healSwelling in the affected areas

Clinical phenotype terms (15)— hover any for plain English
Psoriasiform dermatitisHP:0003765Elevated circulating D-dimer concentrationHP:0033106Anti-BP230 antibody positivityHP:4000019Anti-BP180 antibody positivityHP:4000020
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Late onset

Begins later in life, typically after age 50

Orphanet ↗NORD ↗

FDA & Trial Timeline

7 events
Jun 2026Subconjunctival Humira for Boston Keratoprosthesis

Massachusetts Eye and Ear Infirmary — PHASE1

TrialNOT YET RECRUITING
Nov 2025Study of Stapokibart Injection in Subjects With Moderate to Severe Bullous Pemphigoid

Chengdu Kangnuoxing Biopharma,Inc. — PHASE3

TrialNOT YET RECRUITING
Oct 2024Peridontal and Intestinal Microbiota in Patients With Gingival Scarring Pemphigoid

Centre Hospitalier Universitaire de Nice

TrialRECRUITING
Jul 2022Validation of a Simplified Severity Score (Investigator Global Assessment: IGA) in Bullous Pemphigoid

University Hospital, Rouen

TrialNOT YET RECRUITING
Feb 2022Deciphering IL-17-dependant Inflammatory Response in Bullous Pemphigoid

CHU de Reims — NA

TrialRECRUITING
Feb 2020Proteomic and Metabolomic Lacrimal Fingerprint in Diverse Pathologies of the Ocular Surface

Centre hospitalier de l'Université de Montréal (CHUM)

TrialRECRUITING
Jul 2019Randomized Clinical Trial Comparing the Safety and Efficacy of Rituximab Versus Oral Cyclophosphamide in Severe Forms of Mucous Membrane Pemphigoid

University Hospital, Rouen — PHASE3

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Bullous pemphigoid.

4 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

4 recruitingView all trials with filters →
Phase 31 trial
Randomized Clinical Trial Comparing the Safety and Efficacy of Rituximab Versus Oral Cyclophosphamide in Severe Forms of Mucous Membrane Pemphigoid
Phase 3
Actively Recruiting
PI: Pascal JOLY, Pr (University Hospital, Rouen) · Sites: Amiens; Angers +25 more · Age: 1880 yrs
N/A1 trial
Deciphering IL-17-dependant Inflammatory Response in Bullous Pemphigoid
N/A
Actively Recruiting
· Sites: Reims · Age: 1899 yrs
Other2 trials
Peridontal and Intestinal Microbiota in Patients With Gingival Scarring Pemphigoid
Actively Recruiting
· Sites: Nice; Paris +1 more · Age: 1899 yrs
Proteomic and Metabolomic Lacrimal Fingerprint in Diverse Pathologies of the Ocular Surface
Actively Recruiting
PI: Marie-Claude Robert, MD, M.Sc (Centre hospitalier de l'Université de Montréal (CH) · Sites: Montreal, Quebec; Montreal, Quebec · Age: 1899 yrs

Specialists

20 foundView all specialists →
PP
Pascal JOLY, Pr
Specialist
PI on 1 active trial
AM
Aaron Mangold, MD
SCOTTSDALE, AZ
Specialist
PI on 3 active trials1 Bullous pemphigoid publication
PP
Passeron Thierry, PhD
Specialist
PI on 10 active trials
AM
Alessandro Villa, DDS, PhD, MPH
Specialist
PI on 1 active trial
SM
Stefan Beissert, MD
Specialist
PI on 1 active trial
DS
Dagmar Simon
Specialist
PI on 1 active trial31 Bullous pemphigoid publications
JM
Joseph Ciolino, MD
BOSTON, MA
Specialist
PI on 1 active trial
MM
Marie-Claude Robert, MD, M.Sc
BOSTON, MA
Specialist
PI on 1 active trial
RM
Russell Hall, III, MD
Specialist
PI on 1 active trial
CB
Christine BODEMER
Bobigny
Specialist

Rare Disease Specialist

PI on 2 active trials
SD
Sophie Myriem DRIDI
Specialist
PI on 1 active trial1 Bullous pemphigoid publication
RP
Ron Feldman, MD, PhD
Specialist
PI on 1 active trial
MP
Mehmet Salih Gurel, Professor
Specialist
PI on 1 active trial1 Bullous pemphigoid publication
JM
Janet A Fairley, MD
IOWA CITY, IA
Specialist
PI on 1 active trial
TD
Thomas Dohlman
BOSTON, MA
Specialist
PI on 1 active trial
RG
rehab f ghouraba
Specialist
PI on 1 active trial
GC
Guillaume Chaby
Specialist
PI on 1 active trial
MK
Mee Kum Kim
Specialist
PI on 1 active trial
MH
Mona Harissi-Dagher
BOSTON, MA
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Financial Resources

1 resources

Dupixent

Regeneron Pharmaceuticals, Inc.

Dupixent Patient Support (Regeneron Patient Services)

Patient Assistance
Manufacturer Program
Accepting applications

Travel Grants

No travel grants are currently matched to Bullous pemphigoid.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Bullous pemphigoid

Disease timeline:

New recruiting trial: Randomized Clinical Trial Comparing the Safety and Efficacy of Rituximab Versus Oral Cyclophosphamide in Severe Forms of Mucous Membrane Pemphigoid

A new clinical trial is recruiting patients for Bullous pemphigoid

New recruiting trial: Proteomic and Metabolomic Lacrimal Fingerprint in Diverse Pathologies of the Ocular Surface

A new clinical trial is recruiting patients for Bullous pemphigoid

New recruiting trial: Peridontal and Intestinal Microbiota in Patients With Gingival Scarring Pemphigoid

A new clinical trial is recruiting patients for Bullous pemphigoid

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What treatment do you recommend for me, and how long will I need to take it?,How will we know if the treatment is working, and what tests will you use to monitor my progress?,What are the risks and side effects of the medications you are prescribing?,Is there a chance this disease will go into remission, and what are the chances it will come back?,Are there any medications I am currently taking that could have triggered this condition?,Should I see any other specialists, such as a wound care nurse or immunologist?,Are there any clinical trials or newer treatments I should consider?

Common questions about Bullous pemphigoid

What is Bullous pemphigoid?

Bullous pemphigoid (BP) is a rare skin disease where the body's own immune system mistakenly attacks a thin layer just beneath the outer skin. This causes large, fluid-filled blisters to form, most often on the arms, legs, belly, and groin. The blisters can be very itchy and painful, and the skin around them often looks red or inflamed. Before the blisters appear, many people experience intense itching or a rash that looks like hives for weeks or even months. Bullous pemphigoid is classified as an autoimmune blistering disease. It is the most common condition in this group of disorders. It ma

How is Bullous pemphigoid inherited?

Bullous pemphigoid follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Bullous pemphigoid typically begin?

Typical onset of Bullous pemphigoid is late onset. Age of onset can vary across affected individuals.

Are there clinical trials for Bullous pemphigoid?

Yes — 4 recruiting clinical trials are currently listed for Bullous pemphigoid on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Bullous pemphigoid?

20 specialists and care centers treating Bullous pemphigoid are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.

What treatment and support options exist for Bullous pemphigoid?

1 patient support program are currently tracked on UniteRare for Bullous pemphigoid. See the treatments and support programs sections for copay assistance, eligibility, and contact details.