Erythema multiforme major

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:502499L51.8
Who is this for?
Show terms as
18Specialists8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Erythema multiforme major (also sometimes called Stevens-Johnson syndrome overlap or severe erythema multiforme) is a serious skin and mucous membrane condition where the immune system reacts strongly, usually triggered by an infection or a medication. The name 'erythema multiforme' means 'redness in many forms,' which describes the variety of skin changes that appear. In the major form, the reaction is more severe than the mild version and affects not just the skin but also the moist linings of the body — including the mouth, eyes, and genitals. The condition causes painful, target-shaped or bull's-eye-looking sores on the skin, along with blistering and raw, open areas on the lips, inside the mouth, and sometimes the eyes. These sores can make eating, drinking, and seeing very difficult. The most common triggers are the herpes simplex virus (the virus that causes cold sores) and certain medications such as antibiotics or anti-seizure drugs. Treatment focuses on finding and stopping the trigger, managing pain, protecting the skin, and keeping the eyes and mouth moist and free from infection. Most people recover fully, but the condition can come back, especially if the herpes virus is the cause. In severe cases, hospitalization may be needed. With proper care, the outlook is generally good, though complications involving the eyes can sometimes cause lasting problems.

Also known as:

Key symptoms:

Target-shaped or bull's-eye skin sores, often on the hands, feet, and armsPainful blisters or raw areas on the lips and inside the mouthSores or redness in the eyes, causing pain and sensitivity to lightSores on the genitals or around the anusFever and feeling generally unwell before or during the rashSkin peeling or crusting around the mouthDifficulty eating or swallowing due to mouth soresSwollen or crusted eyelidsWidespread redness and tenderness of the skinBurning or itching sensation on the skin

Inheritance

Multifactorial

Caused by a mix of several genes and environmental factors

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

5 events
Jul 2025Temsirolimus Adventitial Delivery to Improve ANGioplasty and/or Atherectomy Revascularization Outcomes Below the Knee

Mercator MedSystems, Inc. — PHASE3

TrialRECRUITING
Jul 2025DCB for CAD With Type 2 Diabetes

Shanghai 10th People's Hospital — NA

TrialNOT YET RECRUITING
May 2024Severe Erythema Multiforme - CORTICO

Assistance Publique - Hôpitaux de Paris — PHASE3

TrialNOT YET RECRUITING
Apr 2018RESOLUTE ONYX China RCT Study

Medtronic Vascular — NA

TrialACTIVE NOT RECRUITING
Mar 2018RESOLUTE ONYX China Single Arm Study

Medtronic Vascular — NA

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Erythema multiforme major.

View clinical trials →

No actively recruiting trials found for Erythema multiforme major at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Erythema multiforme major community →

Specialists

18 foundView all specialists →
CC
Chun Bing Chen
Specialist
PI on 1 active trial891 Erythema multiforme major publications
PM
Pinnita Prabhasawat, MD
Specialist
PI on 3 active trials
EM
Elizabeth J Phillips, MD
Specialist
PI on 1 active trial
JM
Joseph Ciolino, MD
BOSTON, MA
Specialist
PI on 1 active trial
BM
Ben He, MD
Specialist
PI on 1 active trial
YM
Yongjian Wu, MD
Specialist
PI on 1 active trial
MM
Maja Strozzi, MD
Specialist
PI on 1 active trial
LM
Lianglong Chen, MD
Specialist
PI on 1 active trial1 Erythema multiforme major publication
RM
Ruanne Barnabas, MD
BOSTON, MA
Specialist
PI on 1 active trial
CM
Candy Estevez, M.Sc
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Erythema multiforme major.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Erythema multiforme majorForum →

No community posts yet. Be the first to share your experience with Erythema multiforme major.

Start the conversation →

Latest news about Erythema multiforme major

Disease timeline:

New recruiting trial: Temsirolimus Adventitial Delivery to Improve ANGioplasty and/or Atherectomy Revascularization Outcomes Below the Knee

A new clinical trial is recruiting patients for Erythema multiforme major

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What triggered my episode — was it an infection, a medication, or something else?,Do I need to avoid any specific medications permanently because of this reaction?,Should I take daily antiviral medication to prevent future episodes?,How do I protect my eyes, and when should I see an eye specialist?,What are the warning signs that I need to go to the emergency room?,How likely is it that this will come back, and what can I do to reduce that risk?,Are there any genetic tests I should have before taking certain medications in the future?

Common questions about Erythema multiforme major

What is Erythema multiforme major?

Erythema multiforme major (also sometimes called Stevens-Johnson syndrome overlap or severe erythema multiforme) is a serious skin and mucous membrane condition where the immune system reacts strongly, usually triggered by an infection or a medication. The name 'erythema multiforme' means 'redness in many forms,' which describes the variety of skin changes that appear. In the major form, the reaction is more severe than the mild version and affects not just the skin but also the moist linings of the body — including the mouth, eyes, and genitals. The condition causes painful, target-shaped or

How is Erythema multiforme major inherited?

Erythema multiforme major follows a multifactorial inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Which specialists treat Erythema multiforme major?

18 specialists and care centers treating Erythema multiforme major are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.