Hairy cell leukemia variant

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21Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Hairy cell leukemia variant (HCL-V) is a rare type of blood cancer that affects white blood cells called B-lymphocytes. It is considered a separate disease from classic hairy cell leukemia, even though the names sound similar. In HCL-V, abnormal white blood cells build up in the blood, bone marrow, and spleen. These abnormal cells can crowd out healthy blood cells, leading to low blood counts, an enlarged spleen, and increased risk of infections. Unlike classic hairy cell leukemia, the variant form tends to have a higher white blood cell count and the abnormal cells look slightly different under the microscope — they have a prominent nucleolus (a visible dot inside the cell nucleus). Patients often notice fatigue, frequent infections, easy bruising or bleeding, and a feeling of fullness in the abdomen due to an enlarged spleen. HCL-V is generally more difficult to treat than classic hairy cell leukemia. Standard treatments for classic HCL, such as cladribine and pentostatin, are often less effective in the variant form. Treatment options may include splenectomy (surgical removal of the spleen), rituximab (a targeted antibody therapy), or combination chemotherapy regimens. Newer targeted therapies are being studied in clinical trials. Because HCL-V is rare and behaves differently from classic HCL, it is important to get an accurate diagnosis so the right treatment plan can be developed. The disease primarily affects older adults and tends to follow a more aggressive course than classic hairy cell leukemia.

Also known as:

Key symptoms:

Extreme tiredness and fatigueEnlarged spleen causing fullness or pain in the upper left abdomenFrequent or severe infectionsEasy bruising or unusual bleedingLow red blood cell count (anemia)Low platelet countHigh white blood cell count with abnormal cellsUnexplained weight lossNight sweatsWeaknessPale skinShortness of breath with activityFeeling of heaviness in the belly

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Hairy cell leukemia variant.

View clinical trials →

No actively recruiting trials found for Hairy cell leukemia variant at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Hairy cell leukemia variant community →

Specialists

21 foundView all specialists →
RK
Robert J Kreitman
OLNEY, MD
Specialist
PI on 1 active trial1 Hairy cell leukemia variant publication
KR
Kerry A Rogers
Specialist
PI on 1 active trial19 Hairy cell leukemia variant publications
MD
Mathias J Rummel, Prof. Dr.
COLORADO SPRINGS, CO
Specialist
PI on 2 active trials
RB
Richard Burack
Specialist
2 Hairy cell leukemia variant publications
AR
Akshaya Radhakrishnan
Specialist
2 Hairy cell leukemia variant publications
RP
Reshmi Parameswaran
Specialist
2 Hairy cell leukemia variant publications
MG
Michael Grever
COLUMBUS, OH
Specialist
1 Hairy cell leukemia variant publication
LA
Leslie Andritsos
ALBUQUERQUE, NM
Specialist
1 Hairy cell leukemia variant publication
MA
Mirela Anghelina
Specialist
1 Hairy cell leukemia variant publication
VB
Versha Banerji
Specialist
1 Hairy cell leukemia variant publication
JB
James Blachly
COLUMBUS, OH
Specialist
1 Hairy cell leukemia variant publication
AB
Alessandro Broccoli
BOSTON, MA
Specialist
1 Hairy cell leukemia variant publication
TC
Timothy Call
ROCHESTER, MN
Specialist
1 Hairy cell leukemia variant publication
MT
Martin S Tallman
CHICAGO, IL
Specialist
2 Hairy cell leukemia variant publications
PR
Philip Rock
WILMINGTON, CA
Specialist
2 Hairy cell leukemia variant publications
JB
Jacqueline Barrientos
MIAMI BEACH, FL
Specialist
1 Hairy cell leukemia variant publication
EA
Evgeny Arons
Specialist
2 Hairy cell leukemia variant publications
CF
Claire Fritz
LONDON, OH
Specialist
2 Hairy cell leukemia variant publications
RM
Robert J Kreitman, M.D.
OLNEY, MD
Specialist
PI on 12 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Hairy cell leukemia variant.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Hairy cell leukemia variantForum →

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Latest news about Hairy cell leukemia variant

No recent news articles for Hairy cell leukemia variant.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How do you know this is hairy cell leukemia variant and not classic hairy cell leukemia?,What molecular or genetic testing has been done on my cancer cells, and do I have a MAP2K1 mutation?,What treatment do you recommend as a first approach, and what are the expected response rates for HCL-V specifically?,Are there any clinical trials available for hairy cell leukemia variant that I might be eligible for?,How often will I need blood tests and follow-up visits to monitor my disease?,What signs or symptoms should prompt me to seek emergency care?,Should I be referred to a center with specific expertise in rare leukemias?

Common questions about Hairy cell leukemia variant

What is Hairy cell leukemia variant?

Hairy cell leukemia variant (HCL-V) is a rare type of blood cancer that affects white blood cells called B-lymphocytes. It is considered a separate disease from classic hairy cell leukemia, even though the names sound similar. In HCL-V, abnormal white blood cells build up in the blood, bone marrow, and spleen. These abnormal cells can crowd out healthy blood cells, leading to low blood counts, an enlarged spleen, and increased risk of infections. Unlike classic hairy cell leukemia, the variant form tends to have a higher white blood cell count and the abnormal cells look slightly different und

How is Hairy cell leukemia variant inherited?

Hairy cell leukemia variant follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Hairy cell leukemia variant typically begin?

Typical onset of Hairy cell leukemia variant is adult. Age of onset can vary across affected individuals.

Which specialists treat Hairy cell leukemia variant?

21 specialists and care centers treating Hairy cell leukemia variant are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.