Genetic skin vascular disorder

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ORPHA:183478
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16Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Genetic skin vascular disorder (Orphanet code 183478) is a broad category that refers to a group of rare inherited conditions affecting the blood vessels in the skin. These disorders cause abnormalities in how blood vessels form, grow, or function within the skin and sometimes in deeper tissues. Patients may notice visible changes on the skin such as red, purple, or blue marks, patches, or raised areas caused by abnormal blood vessels. Some of these conditions are present at birth, while others develop during childhood or later in life. The severity of these disorders varies widely. Some people have only mild cosmetic concerns, while others may experience pain, bleeding, swelling, or complications if internal organs are also affected. The blood vessel abnormalities can range from small capillary malformations (sometimes called port-wine stains) to larger venous or arteriovenous malformations that may grow over time. Treatment depends on the specific type of vascular disorder and its severity. Options may include laser therapy to reduce visible skin marks, medications to slow abnormal vessel growth, compression garments, or surgical procedures. In recent years, targeted drug therapies such as sirolimus (rapamycin) have shown promise for certain vascular anomalies. Because this is a group of conditions rather than a single disease, management is highly individualized and often requires a team of specialists working together.

Key symptoms:

Red, purple, or blue skin marks or patchesVisible blood vessels on the skin surfaceSkin swelling or lumpsWarm areas on the skin over abnormal vesselsPain or tenderness in affected areasBleeding from skin lesionsSkin ulcers or sores that are slow to healAsymmetric growth of a limb or body partSkin discoloration that changes with position or temperatureThickening or hardening of the skin in affected areasEasy bruisingFatigue if bleeding is significant

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

3 events
May 2025Multicenter, Randomized, Non-inferiority Study to Compare the Performance and Safety of Debrisoft® Duo With Debrisoft® Pad in the Debridement of Wounds

Lohmann & Rauscher — NA

TrialRECRUITING
Jan 2025Identification of Pathogenic Bacteria of Diabetes Foot Ulcer

Shanghai Jiao Tong University School of Medicine

TrialNOT YET RECRUITING
Feb 2023Multi-modal Quantitative Imaging of the Skin

HJN Sverige AB/Neko Health

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Genetic skin vascular disorder.

View clinical trials →

No actively recruiting trials found for Genetic skin vascular disorder at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Genetic skin vascular disorder community →

Specialists

16 foundView all specialists →
MM
Marcus Maurer, MD
PUEBLO, CO
Specialist
PI on 5 active trials
AM
Amel Karaa, MD
BOSTON, MA
Specialist
PI on 3 active trials
PM
Paul Martin
Specialist
PI on 3 active trials73 Genetic skin vascular disorder publications
TM
Tammuella Chrisentery-Singleton, MD
Phoenix, Arizona
Specialist

Rare Disease Specialist

PI on 2 active trials
MM
Michael Recht, MD, PhD, MBA
CLEVELAND, OH
Specialist
PI on 1 active trial
XM
Xiao-Hui Zhang, MD
Specialist
PI on 16 active trials
EM
Eric Hachulla, MD,PhD
Specialist
PI on 3 active trials
FM
Fereydoun Davatchi, MD
Specialist
PI on 4 active trials
FM
Farhad Shahram, MD
Specialist
PI on 1 active trial
BM
Bahar Sadeghi, MD
Specialist
PI on 1 active trial
MM
Maryam Noroozian, MD
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Genetic skin vascular disorder.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Genetic skin vascular disorderForum →

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Latest news about Genetic skin vascular disorder

Disease timeline:

New recruiting trial: Multicenter, Randomized, Non-inferiority Study to Compare the Performance and Safety of Debrisoft® Duo With Debrisoft® Pad in the Debridement of Wounds

A new clinical trial is recruiting patients for Genetic skin vascular disorder

New recruiting trial: Multi-modal Quantitative Imaging of the Skin

A new clinical trial is recruiting patients for Genetic skin vascular disorder

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific type of vascular disorder does my child or I have, and what gene is involved?,Will this condition get worse over time, and how should we monitor for changes?,What treatment options are available, and what are the risks and benefits of each?,Are there any activities or situations we should avoid to prevent complications?,Should other family members be tested for this condition?,Are there any clinical trials or new therapies we should know about?,What emergency signs should prompt us to seek immediate medical care?

Common questions about Genetic skin vascular disorder

What is Genetic skin vascular disorder?

Genetic skin vascular disorder (Orphanet code 183478) is a broad category that refers to a group of rare inherited conditions affecting the blood vessels in the skin. These disorders cause abnormalities in how blood vessels form, grow, or function within the skin and sometimes in deeper tissues. Patients may notice visible changes on the skin such as red, purple, or blue marks, patches, or raised areas caused by abnormal blood vessels. Some of these conditions are present at birth, while others develop during childhood or later in life. The severity of these disorders varies widely. Some peop

Which specialists treat Genetic skin vascular disorder?

16 specialists and care centers treating Genetic skin vascular disorder are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.