Congenital muscular dystrophy with intellectual disability

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ORPHA:370968OMIM:618992G71.2
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4Specialists8Treatment centers

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Overview

Congenital muscular dystrophy with intellectual disability (sometimes called CMD with intellectual disability) is a rare inherited condition that affects both the muscles and the brain from birth or very early in life. The term 'congenital' means the condition is present at birth, and 'muscular dystrophy' refers to progressive muscle weakness and wasting. In this form, children also experience intellectual disability, meaning they have difficulties with learning, reasoning, and problem-solving that are noticeable from early development. Babies with this condition are often described as 'floppy' (having low muscle tone) and may have trouble feeding, breathing, or moving in the first weeks or months of life. As children grow, they may have delayed motor milestones such as sitting, crawling, or walking, and some may never achieve independent walking. Intellectual disability can range from mild to severe, and some children may also have seizures, eye abnormalities, or structural brain changes visible on MRI. There is currently no cure for this condition. Treatment focuses on managing symptoms and improving quality of life. This includes physical therapy to maintain muscle function and prevent joint contractures, occupational therapy, speech therapy, and educational support. Respiratory care and nutritional support may also be needed. A team of specialists typically works together to provide comprehensive care for affected individuals and their families.

Also known as:

Key symptoms:

Muscle weakness present from birthLow muscle tone (floppiness)Intellectual disability or learning difficultiesDelayed motor milestones such as sitting and walkingDifficulty feeding as a babyJoint stiffness or contracturesBreathing difficultiesSeizures in some casesEye problems or vision difficultiesSpeech and language delaysScoliosis or spinal curvaturePoor head control in infancyDifficulty gaining weight or growingBrain abnormalities seen on MRI

Clinical phenotype terms (43)— hover any for plain English
Hypoglycosylation of alpha-dystroglycanHP:0030046Reduced muscle fiber alpha dystroglycanHP:0030099Limb-girdle muscle weaknessHP:0003325Poor gross motor coordinationHP:0007015Fatigable weakness of skeletal musclesHP:0030197
Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Congenital muscular dystrophy with intellectual disability.

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No actively recruiting trials found for Congenital muscular dystrophy with intellectual disability at this time.

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Specialists

4 foundView all specialists →
WM
Walter Truong, MD
ST. PAUL, MN
Specialist
PI on 2 active trials1 Congenital muscular dystrophy with intellectual disability publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Congenital muscular dystrophy with intellectual disability.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic subtype does my child have, and what does that mean for their outlook?,What therapies should we start right away, and how often should they occur?,Are there any clinical trials or emerging treatments that might be relevant for my child?,What signs of respiratory problems should I watch for, and when should I seek emergency care?,How will this condition affect my child's learning, and what educational supports are available?,Should other family members be tested for this genetic condition?,What specialists should be part of my child's care team, and how often should we see them?

Common questions about Congenital muscular dystrophy with intellectual disability

What is Congenital muscular dystrophy with intellectual disability?

Congenital muscular dystrophy with intellectual disability (sometimes called CMD with intellectual disability) is a rare inherited condition that affects both the muscles and the brain from birth or very early in life. The term 'congenital' means the condition is present at birth, and 'muscular dystrophy' refers to progressive muscle weakness and wasting. In this form, children also experience intellectual disability, meaning they have difficulties with learning, reasoning, and problem-solving that are noticeable from early development. Babies with this condition are often described as 'flopp

At what age does Congenital muscular dystrophy with intellectual disability typically begin?

Typical onset of Congenital muscular dystrophy with intellectual disability is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Congenital muscular dystrophy with intellectual disability?

4 specialists and care centers treating Congenital muscular dystrophy with intellectual disability are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.