Primary eosinophilic gastrointestinal disease

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27Active trials7Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Primary eosinophilic gastrointestinal disease (EGID) is a group of rare conditions where a type of white blood cell called an eosinophil builds up in one or more parts of the digestive tract without another clear cause. Eosinophils are normally involved in fighting infections and allergies, but in EGID they accumulate in the walls of the esophagus, stomach, small intestine, or colon and cause inflammation and damage. The most well-known form is eosinophilic esophagitis (EoE), which affects the swallowing tube, but EGID can also involve the stomach (eosinophilic gastritis), the small bowel (eosinophilic enteritis), or the colon (eosinophilic colitis). Some patients have more than one area affected at the same time. Symptoms depend on which part of the gut is involved and can include difficulty swallowing, abdominal pain, nausea, vomiting, diarrhea, bloating, poor appetite, and weight loss. In children, failure to thrive and feeding difficulties are common. The disease can come and go, with flare-ups followed by quieter periods. Treatment typically involves dietary changes (such as eliminating certain trigger foods), corticosteroids (like budesonide or fluticasone) to reduce inflammation, and in some cases proton pump inhibitors. For eosinophilic esophagitis specifically, dupilumab (Dupixent) was approved by the FDA in 2022 as the first biologic therapy. Management is usually long-term and aims to control symptoms and prevent complications like scarring or narrowing of the digestive tract. Research into new targeted therapies is ongoing.

Also known as:

Key symptoms:

Difficulty swallowing or food getting stuckAbdominal pain or crampingNausea and vomitingDiarrhea, sometimes with bloodBloating and feeling full quicklyHeartburn or chest painPoor appetiteUnintended weight lossFailure to thrive in childrenFeeding difficulties in infantsFatigueNutritional deficienciesFluid buildup in the abdomen (ascites) in severe cases

Inheritance

Multifactorial

Caused by a mix of several genes and environmental factors

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

10 events
Oct 2025A Study in Adult Participants With EoE to Evaluate Vonoprazan 20 mg Compared to Placebo After 12 Weeks and to Evaluate Vonoprazan 20 mg Up to 24 Weeks

Phathom Pharmaceuticals, Inc. — PHASE2

TrialRECRUITING
Apr 2025Patient-Centered Decision Support for Eosinophilic Esophagitis

University of Michigan — NA

TrialRECRUITING
Dec 2024A Non-interventional Observational Study to Assess Long-term Efficacy and Safety of Dupilumab for the Treatment of Patients (>= 12 Years) With Eosinophilic Esophagitis Under Real-world-conditions in Germany

Sanofi

TrialRECRUITING
May 2024Dupilumab for Eosinophilic Esophagitis With Severe Strictures

University of North Carolina, Chapel Hill — PHASE4

TrialENROLLING BY INVITATION
Dec 2023Pediatric Eosinophilic Esophagitis (pedEoE): Effect of Allergen Heat Denaturation on EoE Remission: a Pilot Trial

Universitaire Ziekenhuizen KU Leuven — NA

TrialRECRUITING
Oct 2023Eosinophilic Esophagitis: Towards Improved Management

Oslo University Hospital

TrialRECRUITING
Jul 2023Capsule Sponge Study in Eosinophilic Oesophagitis

East and North Hertfordshire NHS Trust — NA

TrialRECRUITING
Apr 2023An Intervention Study to Improve Therapeutic Compliance in Adult Patients With Eosinophilic Esophagitis.

Academisch Medisch Centrum - Universiteit van Amsterdam (AMC-UvA) — NA

TrialRECRUITING
Mar 2023A Trial to Evaluate EP-104GI in Adults With Eosinophilic Esophagitis (EoE).

Eupraxia Pharmaceuticals Inc. — PHASE1, PHASE2

TrialRECRUITING
Jan 2023Study of Gastric Motility in Eosinophilic Gastritis

Children's Hospital Medical Center, Cincinnati

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Primary eosinophilic gastrointestinal disease.

20 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

20 recruitingView all trials with filters →
Phase 33 trials
Efficacy and Safety of Tezepelumab in Patients With Eosinophilic Esophagitis
Phase 3
Active
· Sites: Phoenix, Arizona; Little Rock, Arkansas +123 more · Age: 1280 yrs
Once Daily Versus Twice Daily Budesonide Orodispersible Tablets for Induction of Remission in EoE
Phase 3
Actively Recruiting
PI: Alfredo J Lucendo, MD, PhD (Department of Gastroenterology, Hospital General d) · Sites: Scottsdale, Arizona; Little Rock, Arkansas +24 more · Age: 1875 yrs
Safety Study of CC-93538 in Adult and Adolescent Participants With Eosinophilic Esophagitis
Phase 3
Active
PI: Bristol-Myers Squibb (Bristol-Myers Squibb) · Sites: Birmingham, Alabama; Phoenix, Arizona +165 more · Age: 1275 yrs
Phase 42 trials
Dupilumab for Eosinophilic Esophagitis With Severe Strictures
Phase 4
Enrolling by Invitation
PI: Evan S Dellon, MD, MPH (University of North Carolina, Chapel Hill) · Sites: Chapel Hill, North Carolina · Age: 1699 yrs
Proton Pump Inhibitor (PPI) Response in Eosinophilic Esophagitis Assessed by Transnasal Endoscopy (TNE)
Phase 4
Active
PI: Nathalie Nguyen, MD (Children's Hospital Colorado) · Sites: Aurora, Colorado · Age: 822 yrs
Phase 21 trial
A Study in Adult Participants With EoE to Evaluate Vonoprazan 20 mg Compared to Placebo After 12 Weeks and to Evaluate Vonoprazan 20 mg Up to 24 Weeks
Phase 2
Actively Recruiting
PI: Medical Director (Phathom Pharmaceuticals) · Sites: Little Rock, Arkansas; Chula Vista, California +37 more · Age: 1899 yrs
Other14 trials
Eosinophilic Esophagitis: Towards Improved Management
Actively Recruiting
PI: Ketil Størdal, PhD (University of Oslo) · Sites: Bergen; Oslo · Age: 017 yrs
Data and Sample Collection Study to Elucidate the Mechanisms of Eosinophilic Disorders
Actively Recruiting
PI: Marc E. Rothenberg, M.D., Ph.D. (Cincinnati Children's Hospital Medical Center) · Sites: Cincinnati, Ohio
Morphological Markers of Gastroesophageal Reflux Disease (GERD)
Active
PI: Eric H Chiou, MD (Baylor College of Medicine) · Sites: Houston, Texas · Age: 818 yrs
A Prospective Study of the Four Food Elimination Diet for Treatment of Eosinophilic Esophagitis
Active
PI: Joshua B Wechsler, MD (Ann & Robert H Lurie Children's Hospital of Chicag) · Sites: Chicago, Illinois · Age: 118 yrs
Cow's Milk Elimination for Treatment of Eosinophilic Esophagitis
Active
PI: Joshua B Wechsler, MD (Ann & Robert H Lurie Children's Hospital of Chicag) · Sites: Chicago, Illinois · Age: 118 yrs
A Registry for the Food Allergy Community
Actively Recruiting
PI: Jennifer Bufford, MS (Food Allergy Research & Education) · Sites: McLean, Virginia
Risk Factors and Biomarkers for Diagnosis and Treatment of EoE
Active
PI: Evan S Dellon, MD, MPH (University of North Carolina, Chapel Hill) · Sites: Chapel Hill, North Carolina · Age: 1899 yrs
A Non-interventional Observational Study to Assess Long-term Efficacy and Safety of Dupilumab for the Treatment of Patients (>= 12 Years) With Eosinophilic Esophagitis Under Real-world-conditions in Germany
Actively Recruiting
PI: Clinical Sciences & Operations (Sanofi) · Sites: Dachau, Bavaria · Age: 1299 yrs
Indiana University Gastrointestinal Motility Diagnosis Registry
Actively Recruiting
PI: John m Wo, MD (Indiana University) · Sites: Indianapolis, Indiana
Study of Gastric Motility in Eosinophilic Gastritis
Actively Recruiting
PI: Paneez Khoury, MD (National Institutes of Health (NIH)) · Sites: Chicago, Illinois; Bethesda, Maryland +1 more · Age: 1859 yrs
Inflammatory Mediators as Potential Non-Invasive Biomarkers in Subjects With Eosinophilic Esophagitis
Active
PI: Joshua Wechsler, MD (Ann & Robert H Lurie Children's Hospital of Chicag) · Sites: Chicago, Illinois; Chicago, Illinois · Age: 118 yrs
Efficacy of Low-Dose Topical Steroids in Maintaining Remission of Eosinophilic Esophagitis in Children
Active
PI: Joshua B Wechsler, MD (Ann & Robert H Lurie Children's Hospital of Chicag) · Sites: Chicago, Illinois · Age: 121 yrs
Changes in Esophageal Distensibility With Proton Pump Inhibitors in Patients With Esophageal Eosinophilia: A Pilot Study
Actively Recruiting
PI: Akiro Saito, MD (Indiana University School of Medicine) · Sites: Indianapolis, Indiana; Indianapolis, Indiana · Age: 1865 yrs
Prospective Database for Eosinophilic Esophagitis (EoE) of Pediatric Population
Active
PI: Joshua B Wechsler, MD (Ann & Robert H Lurie Children's Hospital of Chicag) · Sites: Chicago, Illinois · Age: 021 yrs

Specialists

7 foundView all specialists →
WM
William E Shomali, MD
STANFORD, CA
Specialist
PI on 1 active trial1 Primary eosinophilic gastrointestinal disease publication
PM
Paul Martin
Specialist
PI on 3 active trials73 Primary eosinophilic gastrointestinal disease publications
ES
Emma Scott
Specialist
PI on 1 active trial18 Primary eosinophilic gastrointestinal disease publications
MP
Marcelo Serra, PhD
Buenos Aires, Buenos Aires
Specialist

Rare Disease Specialist

PI on 1 active trial
RR
Ramesh Ramanathan
PITTSBURGH, PA
Specialist
PI on 3 active trials7 Primary eosinophilic gastrointestinal disease publications
MP
Maria Lourdes Posadas Martinez, PhD
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Primary eosinophilic gastrointestinal disease.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which parts of my digestive tract are affected, and how severe is the inflammation?,Should I try dietary elimination therapy, and if so, which foods should I remove first?,What medications do you recommend, and what are the potential side effects of long-term use?,How often will I need endoscopies to monitor my condition?,Am I a candidate for biologic therapy like dupilumab?,Are there any clinical trials I should consider?,What should I do if I have a food impaction or a sudden worsening of symptoms?

Common questions about Primary eosinophilic gastrointestinal disease

What is Primary eosinophilic gastrointestinal disease?

Primary eosinophilic gastrointestinal disease (EGID) is a group of rare conditions where a type of white blood cell called an eosinophil builds up in one or more parts of the digestive tract without another clear cause. Eosinophils are normally involved in fighting infections and allergies, but in EGID they accumulate in the walls of the esophagus, stomach, small intestine, or colon and cause inflammation and damage. The most well-known form is eosinophilic esophagitis (EoE), which affects the swallowing tube, but EGID can also involve the stomach (eosinophilic gastritis), the small bowel (eos

How is Primary eosinophilic gastrointestinal disease inherited?

Primary eosinophilic gastrointestinal disease follows a multifactorial inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Are there clinical trials for Primary eosinophilic gastrointestinal disease?

Yes — 20 recruiting clinical trials are currently listed for Primary eosinophilic gastrointestinal disease on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Primary eosinophilic gastrointestinal disease?

7 specialists and care centers treating Primary eosinophilic gastrointestinal disease are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.