OBSOLETE: Pleomorphic undifferentiated sarcoma

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:293190
Who is this for?
Show terms as
6Active trials8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Pleomorphic undifferentiated sarcoma, formerly known as malignant fibrous histiocytoma (MFH), is a type of soft tissue cancer (sarcoma) that develops most often in adults. The term 'OBSOLETE' in the disease name reflects that this diagnosis has been reclassified in modern medical practice. What was once called malignant fibrous histiocytoma is now more accurately categorized under other sarcoma subtypes using updated pathology techniques. However, the term pleomorphic undifferentiated sarcoma is still used when a soft tissue tumor cannot be classified into a more specific sarcoma type after thorough testing. This cancer most commonly appears in the arms, legs, or the area behind the abdominal organs (called the retroperitoneum). It typically presents as a painless or sometimes painful lump that grows over weeks to months. The tumor is made up of abnormal cells that look very different from one another under the microscope, which is what 'pleomorphic' means. Treatment usually involves surgery to remove the tumor, often combined with radiation therapy. Chemotherapy may be used in cases where the cancer has spread or cannot be fully removed surgically. The outlook depends on the tumor's size, location, depth, and whether it has spread to other parts of the body. Because this is an aggressive cancer, early detection and treatment by a specialized sarcoma team are very important for the best possible outcomes.

Key symptoms:

A painless or painful lump under the skin or deep in the bodySwelling in an arm or legA mass that grows over weeks to monthsPain or discomfort near the tumorLimited movement if the tumor is near a jointAbdominal fullness or bloating if the tumor is in the belly areaUnexplained weight lossFatigueNumbness or tingling if the tumor presses on nervesDifficulty breathing if the cancer spreads to the lungs

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

FDA & Trial Timeline

7 events
Nov 2025Prospective Phase I/II Study Evaluating the Safety and Efficacy of Preoperative Carbon Ion Radiotherapy in Patients With Soft Tissue Sarcoma : The SARCOMA-01 Trial by the Severance sARCOma Multidisciplinary Team

Yonsei University — NA

TrialNOT YET RECRUITING
Sep 2025SATURN-STS: Phase II Study of Neoadjuvant Atezolizumab With Doxorubicin, Concurrent Atezolizumab With Pre-operative Radiation Therapy and Adjuvant Atezolizumab in Patients With High-risk Surgically Resectable Extremity and Truncal Soft Tissue Sarcoma

M.D. Anderson Cancer Center — PHASE2

TrialRECRUITING
Mar 2024Neoadjuvant ADI-PEG 20 + Ifosfamide + Radiotherapy in Soft Tissue Sarcoma

Washington University School of Medicine — PHASE1

TrialACTIVE NOT RECRUITING
Aug 2023Feasibility Trial of Preoperative 5-Day Hypofractionated Radiotherapy for Primary Soft Tissue Sarcoma

Medical University of South Carolina — NA

TrialACTIVE NOT RECRUITING
Aug 2023Study Comparing Negative Pressure Dressing vs Conventional in Patients With Resected STS After Radiotherapy

Centre Leon Berard — NA

TrialRECRUITING
Oct 2021tTF-NGR Randomized Study - STS

Universität Münster — PHASE3

TrialRECRUITING
Jun 2021Neoadjuvant Irradiation of Extremity Soft Tissue Sarcoma With Ions

University Hospital Heidelberg — NA

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for OBSOLETE: Pleomorphic undifferentiated sarcoma.

6 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

6 recruitingView all trials with filters →
Phase 31 trial
tTF-NGR Randomized Study - STS
Phase 3
Actively Recruiting
PI: Christoph Schliemann, Prof. Dr. (University Hospital Muenster (Department of Medici) · Sites: Bad Saarow; Berlin +7 more · Age: 1875 yrs
Phase 21 trial
SATURN-STS: Phase II Study of Neoadjuvant Atezolizumab With Doxorubicin, Concurrent Atezolizumab With Pre-operative Radiation Therapy and Adjuvant Atezolizumab in Patients With High-risk Surgically Resectable Extremity and Truncal Soft Tissue Sarcoma
Phase 2
Actively Recruiting
PI: Ahsan S Farooqi, MD, PHD (M.D. Anderson Cancer Center) · Sites: Houston, Texas · Age: 1899 yrs
Phase 11 trial
Neoadjuvant ADI-PEG 20 + Ifosfamide + Radiotherapy in Soft Tissue Sarcoma
Phase 1
Active
PI: Mia Weiss, M.D. (Washington University School of Medicine) · Sites: St Louis, Missouri · Age: 1899 yrs
N/A3 trials
Neoadjuvant Irradiation of Extremity Soft Tissue Sarcoma With Ions
N/A
Actively Recruiting
· Sites: Heidelberg, Baden-Wurttemberg · Age: 1899 yrs
Feasibility Trial of Preoperative 5-Day Hypofractionated Radiotherapy for Primary Soft Tissue Sarcoma
N/A
Active
· Sites: Charleston, South Carolina · Age: 1899 yrs
Study Comparing Negative Pressure Dressing vs Conventional in Patients With Resected STS After Radiotherapy
N/A
Actively Recruiting
PI: François Gouin, MD, Chirurgien (Centre Leon Berard) · Sites: Nantes, Pays de Loire; Lyon, Rhône-Alpes Auvergne +13 more · Age: 1899 yrs

No specialists are currently listed for OBSOLETE: Pleomorphic undifferentiated sarcoma.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to OBSOLETE: Pleomorphic undifferentiated sarcoma.

Search all travel grants →NORD Financial Assistance ↗

Community

Open OBSOLETE: Pleomorphic undifferentiated sarcomaForum →

No community posts yet. Be the first to share your experience with OBSOLETE: Pleomorphic undifferentiated sarcoma.

Start the conversation →

Latest news about OBSOLETE: Pleomorphic undifferentiated sarcoma

No recent news articles for OBSOLETE: Pleomorphic undifferentiated sarcoma.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the exact size, grade, and stage of my sarcoma?,Can the tumor be completely removed with surgery, and will I need radiation or chemotherapy?,Should I seek a second opinion at a specialized sarcoma center?,Are there any clinical trials available for my type and stage of cancer?,What is my risk of the cancer coming back after treatment?,How will treatment affect my daily activities and ability to work?,What follow-up schedule and imaging will I need after treatment is completed?

Common questions about OBSOLETE: Pleomorphic undifferentiated sarcoma

What is OBSOLETE: Pleomorphic undifferentiated sarcoma?

Pleomorphic undifferentiated sarcoma, formerly known as malignant fibrous histiocytoma (MFH), is a type of soft tissue cancer (sarcoma) that develops most often in adults. The term 'OBSOLETE' in the disease name reflects that this diagnosis has been reclassified in modern medical practice. What was once called malignant fibrous histiocytoma is now more accurately categorized under other sarcoma subtypes using updated pathology techniques. However, the term pleomorphic undifferentiated sarcoma is still used when a soft tissue tumor cannot be classified into a more specific sarcoma type after th

How is OBSOLETE: Pleomorphic undifferentiated sarcoma inherited?

OBSOLETE: Pleomorphic undifferentiated sarcoma follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does OBSOLETE: Pleomorphic undifferentiated sarcoma typically begin?

Typical onset of OBSOLETE: Pleomorphic undifferentiated sarcoma is adult. Age of onset can vary across affected individuals.

Are there clinical trials for OBSOLETE: Pleomorphic undifferentiated sarcoma?

Yes — 6 recruiting clinical trials are currently listed for OBSOLETE: Pleomorphic undifferentiated sarcoma on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.