Myxofibrosarcoma

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ORPHA:79105C49.9
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12Specialists8Treatment centers

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Overview

Myxofibrosarcoma (sometimes called myxoid malignant fibrous histiocytoma or MFS) is a type of soft tissue cancer that grows in the connective tissues of the body — the tissues that support, connect, and surround muscles, fat, and other structures. It most often appears as a slow-growing lump or mass under the skin, most commonly in the arms or legs, though it can develop in the trunk or other areas. The tumor tends to have a jelly-like (myxoid) texture and can spread along tissue planes, which makes it tricky to remove completely. Myxofibrosarcoma is one of the more common soft tissue sarcomas in older adults. It can range from low-grade (slow-growing, less likely to spread) to high-grade (faster-growing, higher risk of spreading to other parts of the body like the lungs). Symptoms often include a painless or mildly painful lump that gradually gets bigger. Some people notice swelling, tenderness, or limited movement in the affected area. Treatment usually involves surgery to remove the tumor, often combined with radiation therapy to reduce the chance of it coming back. Chemotherapy may be used for high-grade or advanced cases. Because this cancer can recur locally (come back in the same area), close follow-up after treatment is very important. Early detection and treatment at a specialized sarcoma center give the best outcomes.

Also known as:

Key symptoms:

A painless or mildly painful lump or swelling under the skinA lump that slowly grows larger over weeks or monthsSwelling or puffiness in an arm, leg, or trunkTenderness or soreness around the lumpLimited movement or stiffness near the affected areaA firm or rubbery mass that feels attached to deeper tissueSkin changes over the lump such as redness or warmthFatigue or unexplained weight loss in advanced casesShortness of breath if the cancer has spread to the lungs

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Myxofibrosarcoma.

View clinical trials →

No actively recruiting trials found for Myxofibrosarcoma at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Myxofibrosarcoma community →

Specialists

12 foundView all specialists →
SM
Sandra D'Angelo, MD
SPRINGFIELD, MO
Specialist
PI on 4 active trials
IP
Ivar Hompland, MD, PhD
Specialist
PI on 2 active trials
KP
Kjetil Boye, MD, PhD
Specialist
PI on 2 active trials
CH
Candace L Haddox
BOSTON, MA
Specialist
PI on 1 active trial
AW
Aaron R Weiss
Specialist
PI on 1 active trial56 Myxofibrosarcoma publications
EM
Edmund Bartlett, MD
Specialist
PI on 1 active trial
VP
Vishruth Reddy, MD, PhD
LOS ANGELES, CA
Specialist
PI on 1 active trial
MD
Mark Dickson
Specialist
PI on 1 active trial2 Myxofibrosarcoma publications
BP
Brian A Van Tine, M.D., Ph.D.
Specialist
PI on 2 active trials
LD
Lara E Davis
Specialist
PI on 2 active trials34 Myxofibrosarcoma publications

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Myxofibrosarcoma.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Myxofibrosarcoma

No recent news articles for Myxofibrosarcoma.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What grade is my tumor, and what does that mean for my treatment and prognosis?,Will I need radiation therapy in addition to surgery, and if so, will it be before or after the operation?,What are the chances the tumor will come back, and how will we monitor for that?,Should I be treated at a specialized sarcoma center, and can you refer me to one?,Are there any clinical trials I might be eligible for?,What are the expected side effects of treatment, and how will they affect my daily life?,How often will I need follow-up scans, and for how long?

Common questions about Myxofibrosarcoma

What is Myxofibrosarcoma?

Myxofibrosarcoma (sometimes called myxoid malignant fibrous histiocytoma or MFS) is a type of soft tissue cancer that grows in the connective tissues of the body — the tissues that support, connect, and surround muscles, fat, and other structures. It most often appears as a slow-growing lump or mass under the skin, most commonly in the arms or legs, though it can develop in the trunk or other areas. The tumor tends to have a jelly-like (myxoid) texture and can spread along tissue planes, which makes it tricky to remove completely. Myxofibrosarcoma is one of the more common soft tissue sarcoma

How is Myxofibrosarcoma inherited?

Myxofibrosarcoma follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Myxofibrosarcoma typically begin?

Typical onset of Myxofibrosarcoma is adult. Age of onset can vary across affected individuals.

Which specialists treat Myxofibrosarcoma?

12 specialists and care centers treating Myxofibrosarcoma are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.