Midline cerebral malformation

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ORPHA:268926
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8Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Midline cerebral malformation is a rare group of brain abnormalities that affect the structures located along the center (midline) of the brain. These structures include the corpus callosum (the band of nerve fibers connecting the two halves of the brain), the septum pellucidum, and other midline brain structures. When these structures do not form properly during fetal development, it can lead to a range of neurological problems. The severity of midline cerebral malformations varies widely. Some individuals may have mild symptoms, while others can experience significant developmental delays, intellectual disability, seizures, vision problems, and hormonal imbalances. The specific symptoms depend on which midline structures are affected and how severely they are malformed. Some patients may also have abnormalities of the pituitary gland, leading to hormone deficiencies. There is currently no cure for midline cerebral malformations. Treatment focuses on managing symptoms and supporting development. This may include anti-seizure medications, hormone replacement therapy, physical therapy, occupational therapy, speech therapy, and special education services. Early intervention programs can help children reach their full developmental potential. A team of specialists typically works together to provide comprehensive care tailored to each patient's specific needs.

Also known as:

Key symptoms:

Developmental delaysIntellectual disabilitySeizures or epilepsyVision problemsHormonal imbalancesDifficulty with coordination and balanceSpeech and language delaysLearning difficultiesAbnormal head size (too large or too small)Feeding difficulties in infancyMuscle tone problems (too stiff or too floppy)Behavioral challengesSleep disturbancesGrowth problems

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

2 events
May 2023Evaluation of Anterior Middle Brain Structures With Cerebrovascular Flow in Fetuses With Fetal Growth Restriction

Ankara Etlik City Hospital

TrialACTIVE NOT RECRUITING
Dec 2022Erythropoietin for Neonatal Encephalopathy in LMIC (EMBRACE Trial)

Imperial College London — PHASE3

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Midline cerebral malformation.

View clinical trials →

No actively recruiting trials found for Midline cerebral malformation at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Midline cerebral malformation community →

Specialists

8 foundView all specialists →
JP
Jerome Engel, Jr., M.D., Ph.D.
LOS ANGELES, CA
Specialist
PI on 1 active trial
SM
Shivaani Kummar, MD
PORTLAND, OR
Specialist
PI on 5 active trials
SP
Sudhin Thayyil, PhD
Specialist
PI on 1 active trial
YP
Yves Agid, MD, PhD
Specialist
PI on 2 active trials
KM
Kevin J Black, M.D.
Specialist
PI on 1 active trial
XP
Xuemei Peng, Ph.d
Specialist
PI on 1 active trial
KM
Kevin J Black, MD
Specialist
PI on 1 active trial
WM
Wayne Goodman, MD
GAINESVILLE, FL
Specialist
PI on 1 active trial1 Midline cerebral malformation publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Midline cerebral malformation.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Midline cerebral malformationForum →

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Latest news about Midline cerebral malformation

Disease timeline:

New recruiting trial: Erythropoietin for Neonatal Encephalopathy in LMIC (EMBRACE Trial)

A new clinical trial is recruiting patients for Midline cerebral malformation

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific midline brain structures are affected in my child, and what does that mean for their development?,Should we pursue genetic testing to look for an underlying cause, and how would the results change our care plan?,Are there any hormone deficiencies we need to test for and treat?,What therapies (physical, occupational, speech) should we start, and how often?,What is the risk of seizures, and what should I do if one occurs?,Is there a risk of hydrocephalus, and what signs should I watch for?,Are there any clinical trials or research studies that might be relevant for us?

Common questions about Midline cerebral malformation

What is Midline cerebral malformation?

Midline cerebral malformation is a rare group of brain abnormalities that affect the structures located along the center (midline) of the brain. These structures include the corpus callosum (the band of nerve fibers connecting the two halves of the brain), the septum pellucidum, and other midline brain structures. When these structures do not form properly during fetal development, it can lead to a range of neurological problems. The severity of midline cerebral malformations varies widely. Some individuals may have mild symptoms, while others can experience significant developmental delays,

At what age does Midline cerebral malformation typically begin?

Typical onset of Midline cerebral malformation is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Midline cerebral malformation?

8 specialists and care centers treating Midline cerebral malformation are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.