Japanese encephalitis

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1FDA treatments41Specialists8Treatment centers

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Overview

Japanese encephalitis (JE) is a serious viral infection that affects the brain. It is caused by the Japanese encephalitis virus (JEV), which belongs to a family of viruses called flaviviruses — the same family that includes West Nile virus and dengue virus. The virus is spread to humans through the bites of infected Culex mosquitoes, mainly in rural and agricultural areas of Asia and the western Pacific. You cannot catch it directly from another person. Once the virus enters the body, it can travel to the brain and cause dangerous swelling (encephalitis). Most people who are infected — about 99 out of 100 — never develop serious symptoms. But in those who do, the illness can be life-threatening. Symptoms usually start with fever, headache, and vomiting, and can quickly progress to confusion, seizures, and loss of consciousness. Children are especially vulnerable to severe disease. There is no specific antiviral drug to treat Japanese encephalitis. Care focuses on managing symptoms in a hospital setting, such as controlling seizures and reducing brain swelling. Vaccination is the most effective way to prevent the disease. A safe and effective vaccine is available and is recommended for travelers to high-risk areas and for people living in regions where the virus is common.

Key symptoms:

High feverSevere headacheNausea and vomitingStiff neckConfusion or disorientationSeizures or convulsionsWeakness or paralysis on one side of the bodyTremors or shakingLoss of consciousness or comaDifficulty speaking or understanding speechSensitivity to lightBehavioral changes or agitationMuscle stiffness or rigidity

Clinical phenotype terms (50)— hover any for plain English
Infectious encephalitisHP:0002383Facial grimacingHP:0000273Cogwheel rigidityHP:0002396Decreased motor nerve conduction velocityHP:0003431ParalysisHP:0003470Increased circulating IgM levelHP:0003496
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

1 event
May 2013

IXIARO: FDA approved

IXIARO is a vaccine indicated for the prevention of disease caused by Japanese encephalitis virus (JEV). IXIARO is approved for use in individuals 2 months of age and older.

FDAcompleted

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

1 available

IXIARO

Japanese encephalitis vaccine, inactivated, adsorbed· Intercell AGOrphan Drug

IXIARO is a vaccine indicated for the prevention of disease caused by Japanese encephalitis virus (JEV). IXIARO is approved for use in individuals 2 months of age and older.

No actively recruiting trials found for Japanese encephalitis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Japanese encephalitis community →

Specialists

Showing 25 of 41View all specialists →
KP
Kulkanya Chokephaibulkit, Professor
Specialist
PI on 1 active trial
SE
Susanne Eder
SAN FRANCISCO, CA
Specialist
PI on 2 active trials3 Japanese encephalitis publications
AM
Anand Dubey, M.D
Specialist
PI on 1 active trial
SM
Susanne Eder, Mag.
Specialist
PI on 2 active trials
EH
Evelyn Hatzenbichler
Specialist
PI on 1 active trial
LM
Luis Angles, M.D.
Specialist
PI on 1 active trial
TP
Thiem D Vu, MD., PhD.
Specialist
PI on 3 active trials
BM
Bakul B. Javadekar, M.D.
Specialist
PI on 1 active trial
AD
Atul Shanker, Dr.
Specialist
PI on 1 active trial
HD
Herwig Kollaritsch, Prof. Dr.
Specialist
PI on 1 active trial
KM
Katrin L Dubischar-Kastner, MSc
Specialist
PI on 1 active trial
AP
Astrid Kaltenboeck, Ph.D.
Specialist
PI on 3 active trials
VK
Vera Kadlecek
Specialist
PI on 1 active trial
KM
K Zaman, MD
Specialist
PI on 2 active trials
SM
Steven G Hull, MD
Specialist
PI on 1 active trial
NH
Nicole Haas
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Japanese encephalitis.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Japanese encephalitisForum →

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Latest news about Japanese encephalitis

No recent news articles for Japanese encephalitis.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What tests will confirm whether this is Japanese encephalitis, and how long will results take?,What are the most important warning signs that mean I or my child needs emergency care right away?,What long-term effects should we watch for, and how soon will we know if there is lasting brain damage?,What rehabilitation services are available to help with recovery, such as speech therapy or physical therapy?,Should other family members or close contacts be vaccinated, and is it too late for vaccination to help?,Are there any clinical trials or new treatments we should know about?,How long will recovery take, and when is it safe to return to school or work?

Common questions about Japanese encephalitis

What is Japanese encephalitis?

Japanese encephalitis (JE) is a serious viral infection that affects the brain. It is caused by the Japanese encephalitis virus (JEV), which belongs to a family of viruses called flaviviruses — the same family that includes West Nile virus and dengue virus. The virus is spread to humans through the bites of infected Culex mosquitoes, mainly in rural and agricultural areas of Asia and the western Pacific. You cannot catch it directly from another person. Once the virus enters the body, it can travel to the brain and cause dangerous swelling (encephalitis). Most people who are infected — about

How is Japanese encephalitis inherited?

Japanese encephalitis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Which specialists treat Japanese encephalitis?

25 specialists and care centers treating Japanese encephalitis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.

What treatment and support options exist for Japanese encephalitis?

1 patient support program are currently tracked on UniteRare for Japanese encephalitis. See the treatments and support programs sections for copay assistance, eligibility, and contact details.