Functioning pituitary adenoma

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ORPHA:314753
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9Active trials32Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

A functioning pituitary adenoma is a non-cancerous (benign) tumor that grows in the pituitary gland, a small pea-sized gland located at the base of the brain. What makes these tumors 'functioning' is that they actively produce excess hormones, which disrupts the body's normal hormonal balance. The pituitary gland is often called the 'master gland' because it controls many other glands and hormones throughout the body, so a tumor here can cause widespread effects. The symptoms depend on which hormone the tumor overproduces. For example, tumors that make too much growth hormone can cause acromegaly (enlarged hands, feet, and facial features in adults) or gigantism in children. Tumors producing excess prolactin (called prolactinomas) can cause irregular periods, breast milk production in non-pregnant women, and sexual dysfunction in men. Tumors that overproduce ACTH lead to Cushing's disease, causing weight gain, round face, easy bruising, and high blood sugar. Some tumors produce excess thyroid-stimulating hormone, leading to hyperthyroidism. Treatment depends on the type and size of the tumor. Options include medications that can shrink certain tumors (especially prolactinomas), surgery to remove the tumor (usually through the nose in a procedure called transsphenoidal surgery), and radiation therapy. Many patients can be effectively managed with proper treatment, though long-term monitoring is usually needed. Early diagnosis and treatment are important to prevent complications from prolonged hormone excess.

Also known as:

Key symptoms:

Unexplained weight gain, especially around the midsection and faceHeadachesVision problems, especially loss of side (peripheral) visionIrregular or absent menstrual periodsBreast milk production when not pregnant or breastfeedingDecreased sex drive or erectile dysfunctionEnlarged hands, feet, or facial featuresExcessive sweatingEasy bruising and thin skinHigh blood sugar or new diabetesHigh blood pressureFatigue and muscle weaknessJoint painMood changes, anxiety, or depressionInfertility

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

FDA & Trial Timeline

10 events
Mar 2026Study of 18FET PET in Functional Pituitary Adenomas With Indeterminate MRI Findings

University Hospital, Lille — PHASE2

TrialNOT YET RECRUITING
Jan 2026Use of [18F] Fluoroethyl-L-tyrosine PET/MRI for Identifying Small Functional Pituitary Adenomas

Mayo Clinic — PHASE1

TrialRECRUITING
Jan 2026How Estrogen Fluctuations Before Diagnosis Affect the Size Prolactin-secreting Tumors

Hospices Civils de Lyon

TrialRECRUITING
Sep 2025Metabolic Outcomes in Patients With Prolactinomas Under Dopamine Agonist Treatment

University Hospital, Basel, Switzerland — PHASE4

TrialRECRUITING
Sep 2024Molecular Pituitary Imaging Using 18F-FET PET

University of Cambridge — NA

TrialRECRUITING
Apr 2024Physical Attendance Versus Telephone or Video Follow-up in Patients With Non-functioning Pituitary Tumors.

Zealand University Hospital — NA

TrialENROLLING BY INVITATION
Feb 2024Individualized Physical Activity or Patients With Non Functioning Pituitary Adenoma

Vastra Gotaland Region — NA

TrialRECRUITING
Jan 2023Effects of Growth Hormone Therapy on Metabolic Function in Fatty Liver Post-Pituitary Adenoma Surgery

Shanghai Zhongshan Hospital — PHASE4

TrialRECRUITING
Jun 2019PRolaCT - Three Prolactinoma RCTs

Leiden University Medical Center — PHASE4

TrialRECRUITING
Nov 2014Dopamine Agonist Treatment of Non-functioning Pituitary Adenomas

St. Olavs Hospital — PHASE3

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Functioning pituitary adenoma.

9 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

9 recruitingView all trials with filters →
Phase 31 trial
Dopamine Agonist Treatment of Non-functioning Pituitary Adenomas
Phase 3
Active
PI: Sven M Carlsen, prof md (Norwegian University of Science and Technology) · Sites: Oslo; Trondheim +1 more · Age: 1875 yrs
Phase 43 trials
PRolaCT - Three Prolactinoma RCTs
Phase 4
Actively Recruiting
PI: Nienke R Biermasz, MD, prof. (Endocrinologist LUMC) · Sites: Amsterdam-Zuidoost, North Holland; Delft, South Holland +1 more · Age: 1899 yrs
Metabolic Outcomes in Patients With Prolactinomas Under Dopamine Agonist Treatment
Phase 4
Actively Recruiting
PI: Cihan Atila, Dr. (University Hospital Basel, Dept. of Endocrinology,) · Sites: Basel · Age: 1899 yrs
Effects of Growth Hormone Therapy on Metabolic Function in Fatty Liver Post-Pituitary Adenoma Surgery
Phase 4
Actively Recruiting
PI: Tao Xie (Fudan University) · Sites: Shanghai · Age: 1860 yrs
Phase 11 trial
Use of [18F] Fluoroethyl-L-tyrosine PET/MRI for Identifying Small Functional Pituitary Adenomas
Phase 1
Actively Recruiting
PI: Neetu Soni, MBBS, MD (Mayo Clinic) · Sites: Jacksonville, Florida · Age: 1875 yrs
N/A3 trials
Individualized Physical Activity or Patients With Non Functioning Pituitary Adenoma
N/A
Actively Recruiting
· Sites: Gothenburg, Västra Götaland County · Age: 1875 yrs
Physical Attendance Versus Telephone or Video Follow-up in Patients With Non-functioning Pituitary Tumors.
N/A
Enrolling by Invitation
PI: Jesper Krogh, DMSc (Zealand University Hospital) · Sites: Køge, Region Sjælland · Age: 1899 yrs
Molecular Pituitary Imaging Using 18F-FET PET
N/A
Actively Recruiting
PI: Mark Gurnell, MD, PhD (Cambridge University Hospitals NHS Foundation Trus) · Sites: Cambridge, Cambridgeshire · Age: 18100 yrs
Other1 trial
How Estrogen Fluctuations Before Diagnosis Affect the Size Prolactin-secreting Tumors
Actively Recruiting
· Sites: Bron, Rhone · Age: 1899 yrs

Specialists

Showing 25 of 32View all specialists →
MP
Mark Gurnell, MD, PhD
Specialist
PI on 1 active trial
JM
Jakub Lubojacký, MD
Specialist
PI on 2 active trials
HU
Hafiz Zubair Ullah
Specialist
2 Functioning pituitary adenoma publications
DM
David S McLaren
COLUMBIA, MO
Specialist
2 Functioning pituitary adenoma publications
PL
Paul Benjamin Loughrey
Specialist
2 Functioning pituitary adenoma publications
EB
Efstathios Bonanos
Specialist
2 Functioning pituitary adenoma publications
SS
Shah Khalid Shinwari
Specialist
2 Functioning pituitary adenoma publications
KM
Kirsten Mitchell
Specialist
2 Functioning pituitary adenoma publications
SS
Syed Shah
Specialist
2 Functioning pituitary adenoma publications
MM
Mike Matheou
Specialist
2 Functioning pituitary adenoma publications
KI
Kristina Isand
Specialist
2 Functioning pituitary adenoma publications
AJ
Anuradha Jayasuriya
Specialist
2 Functioning pituitary adenoma publications
KK
Katarina Klaucane
Specialist
2 Functioning pituitary adenoma publications
RH
Ross Hamblin
Specialist
2 Functioning pituitary adenoma publications
AF
Athanasios Fountas
Specialist
2 Functioning pituitary adenoma publications
KL
Kirstie Lithgow
Specialist
2 Functioning pituitary adenoma publications
GC
Gilda Cennamo
Specialist
PI on 7 active trials8 Functioning pituitary adenoma publications
SM
Sven M Carlsen, prof md
Specialist
PI on 1 active trial
TX
Tao Xie
Specialist
PI on 3 active trials33 Functioning pituitary adenoma publications
MP
Mônica R. Gadelha, PhD
Specialist
PI on 1 active trial
LG
Lydia Grixti
Specialist
2 Functioning pituitary adenoma publications
NM
Neetu Soni, MBBS, MD
JACKSONVILLE, FL
Specialist
PI on 1 active trial
AB
Ambika Babu
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Functioning pituitary adenoma.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Functioning pituitary adenoma

Disease timeline:

New recruiting trial: How Estrogen Fluctuations Before Diagnosis Affect the Size Prolactin-secreting Tumors

A new clinical trial is recruiting patients for Functioning pituitary adenoma

New recruiting trial: Metabolic Outcomes in Patients With Prolactinomas Under Dopamine Agonist Treatment

A new clinical trial is recruiting patients for Functioning pituitary adenoma

New recruiting trial: Individualized Physical Activity or Patients With Non Functioning Pituitary Adenoma

A new clinical trial is recruiting patients for Functioning pituitary adenoma

New recruiting trial: Molecular Pituitary Imaging Using 18F-FET PET

A new clinical trial is recruiting patients for Functioning pituitary adenoma

New recruiting trial: Use of [18F] Fluoroethyl-L-tyrosine PET/MRI for Identifying Small Functional Pituitary Adenomas

A new clinical trial is recruiting patients for Functioning pituitary adenoma

New recruiting trial: Effects of Growth Hormone Therapy on Metabolic Function in Fatty Liver Post-Pituitary Adenoma Surgery

A new clinical trial is recruiting patients for Functioning pituitary adenoma

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What type of hormone is my tumor producing, and how is that affecting my body?,What is the size of my tumor, and is it pressing on any important structures like the optic nerves?,What treatment do you recommend first — medication, surgery, or radiation — and why?,What are the chances that treatment will fully normalize my hormone levels?,Will I need to take hormone replacement medications after treatment, and for how long?,How often will I need follow-up blood tests and MRI scans?,Should I or my family members be tested for a genetic cause of this tumor?

Common questions about Functioning pituitary adenoma

What is Functioning pituitary adenoma?

A functioning pituitary adenoma is a non-cancerous (benign) tumor that grows in the pituitary gland, a small pea-sized gland located at the base of the brain. What makes these tumors 'functioning' is that they actively produce excess hormones, which disrupts the body's normal hormonal balance. The pituitary gland is often called the 'master gland' because it controls many other glands and hormones throughout the body, so a tumor here can cause widespread effects. The symptoms depend on which hormone the tumor overproduces. For example, tumors that make too much growth hormone can cause acrome

How is Functioning pituitary adenoma inherited?

Functioning pituitary adenoma follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Functioning pituitary adenoma typically begin?

Typical onset of Functioning pituitary adenoma is adult. Age of onset can vary across affected individuals.

Are there clinical trials for Functioning pituitary adenoma?

Yes — 9 recruiting clinical trials are currently listed for Functioning pituitary adenoma on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Functioning pituitary adenoma?

25 specialists and care centers treating Functioning pituitary adenoma are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.