Desmoplastic small round cell tumor

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ORPHA:83469C48.2
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8Active trials31Specialists8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Also known as:

Clinical phenotype terms— hover any for plain English:

Abnormal peritoneum morphologyHP:0002585IleusHP:0002595Neoplasm of the pancreasHP:0002894Testicular neoplasmHP:0010788Neoplasm of the central nervous systemHP:0100006SarcomaHP:0100242Neoplasm of the lungHP:0100526Ovarian neoplasmHP:0100615Mediastinal lymphadenopathyHP:0100721
Orphanet ↗NORD ↗

FDA & Trial Timeline

8 events
Nov 2025Clinical Study in Patients With DSRCT

Italian Sarcoma Group — PHASE2

TrialRECRUITING
Dec 2024Pasireotide as Maintenance Treatment in Synovial Sarcoma and Desmoplastic Small Round Cell Tumor

University Hospital Heidelberg — PHASE2

TrialRECRUITING
Jul 2023Lurbinectedin in FET-Fused Tumors

Children's Hospital of Philadelphia — PHASE1, PHASE2

TrialRECRUITING
Dec 2020Registry to Collect Health Information About Desmoplastic Small Round Cell Tumor

Memorial Sloan Kettering Cancer Center

TrialRECRUITING
Jan 2020CAMPFIRE: A Study of Ramucirumab (LY3009806) in Children and Young Adults With Desmoplastic Small Round Cell Tumor

Eli Lilly and Company — PHASE1, PHASE2

TrialACTIVE NOT RECRUITING
Jul 2019A Study of the Drug I131-Omburtamab in People With Desmoplastic Small Round Cell Tumors and Other Solid Tumors in the Peritoneum

Memorial Sloan Kettering Cancer Center — PHASE2

TrialACTIVE NOT RECRUITING
Dec 2013Therapeutic Trial for Patients With Ewing Sarcoma Family of Tumor and Desmoplastic Small Round Cell Tumors

St. Jude Children's Research Hospital — PHASE2

TrialACTIVE NOT RECRUITING
Aug 2010Irinotecan, Temozolomide and Bevacizumab in Combination With Existing High Dose Alkylator Based Chemotherapy for Treatment of Newly Diagnosed Patients With Desmoplastic Small Round Cell Tumor

Memorial Sloan Kettering Cancer Center — EARLY_PHASE1

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Desmoplastic small round cell tumor.

8 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

8 recruitingView all trials with filters →
Phase 24 trials
Therapeutic Trial for Patients With Ewing Sarcoma Family of Tumor and Desmoplastic Small Round Cell Tumors
Phase 2
Active
PI: Sara M. Federico, MD (St. Jude Children's Research Hospital) · Sites: Memphis, Tennessee · Age: 025 yrs
Clinical Study in Patients With DSRCT
Phase 2
Actively Recruiting
PI: Silvia Syecchiotti, MD (Findazione IRCCS Istituto Nazionale Tumori Milano) · Sites: Milan, MI · Age: 1599 yrs
A Study of the Drug I131-Omburtamab in People With Desmoplastic Small Round Cell Tumors and Other Solid Tumors in the Peritoneum
Phase 2
Active
PI: Emily Slotkin, MD (Memorial Sloan Kettering Cancer Center) · Sites: New York, New York · Age: 199 yrs
Pasireotide as Maintenance Treatment in Synovial Sarcoma and Desmoplastic Small Round Cell Tumor
Phase 2
Actively Recruiting
PI: Richard F. Schlenk, Professor (National Center for Tumour Diseases, University Ho) · Sites: Heidelberg, Baden-Wurttemberg; Stuttgart, Baden-Wurttemberg +2 more · Age: 1350 yrs
Other1 trial
Registry to Collect Health Information About Desmoplastic Small Round Cell Tumor
Actively Recruiting
PI: Emily Slotkin, MD (Memorial Sloan Kettering Cancer Center) · Sites: New York, New York

Specialists

Showing 25 of 31View all specialists →
AM
Andrea Hayes-Jordan, MD
Specialist
PI on 3 active trials
RP
Richard F. Schlenk, Professor
CLEVELAND, OH
Specialist
PI on 1 active trial2 Desmoplastic small round cell tumor publications
SM
Silvia Syecchiotti, MD
Specialist
PI on 1 active trial
CM
Carola A. S. Arndt, MD
ROCHESTER, MN
Specialist
PI on 1 active trial
XZ
Xing Zhang
PAOLI, PA
Specialist
PI on 4 active trials
SM
Sara M. Federico, MD
MEMPHIS, TN
Specialist
PI on 3 active trials
RP
Robert Maki, MD, PhD
PHILADELPHIA, PA
Specialist
PI on 8 active trials
ZX
Zhang Xing
Specialist
PI on 1 active trial9 Desmoplastic small round cell tumor publications
EM
Emily Slotkin, MD
NEW YORK, NY
Specialist
PI on 6 active trials
JM
Jaume Mora, MD
Specialist
PI on 1 active trial
CM
Catherine Albert, MD
Specialist
PI on 3 active trials
JM
Javier Martínez Trufero, MD
Specialist
PI on 1 active trial
JM
Jordan Milner, MD
GAINESVILLE, FL
Specialist
PI on 5 active trials
JM
Javier Martin Broto, MD
Specialist
PI on 1 active trial
JM
José Antonio López-Martín, MD
Specialist
PI on 1 active trial
RM
Roberto Díaz, MD
Specialist
PI on 1 active trial
MB
Mason Bond
Specialist
PI on 1 active trial5 Desmoplastic small round cell tumor publications
DM
David Shulman, MD
Specialist
PI on 2 active trials
CM
Chris DeRenzo, MD
MEMPHIS, TN
Specialist
PI on 1 active trial
AM
Antonio López Pousa, MD
Specialist
PI on 1 active trial
FM
Francisco Bautista, MD
Specialist
PI on 1 active trial
MM
Mary L. Keohan, MD
NEW YORK, NY
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Desmoplastic small round cell tumor.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Desmoplastic small round cell tumor

Disease timeline:

New recruiting trial: Lurbinectedin in FET-Fused Tumors

A new clinical trial is recruiting patients for Desmoplastic small round cell tumor

New recruiting trial: Registry to Collect Health Information About Desmoplastic Small Round Cell Tumor

A new clinical trial is recruiting patients for Desmoplastic small round cell tumor

New recruiting trial: Clinical Study in Patients With DSRCT

A new clinical trial is recruiting patients for Desmoplastic small round cell tumor

New recruiting trial: Pasireotide as Maintenance Treatment in Synovial Sarcoma and Desmoplastic Small Round Cell Tumor

A new clinical trial is recruiting patients for Desmoplastic small round cell tumor

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Common questions about Desmoplastic small round cell tumor

Are there clinical trials for Desmoplastic small round cell tumor?

Yes — 8 recruiting clinical trials are currently listed for Desmoplastic small round cell tumor on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Desmoplastic small round cell tumor?

25 specialists and care centers treating Desmoplastic small round cell tumor are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.