Rare Disease Library

Browse Orphanet-curated rare diseases with HPO phenotype annotations, synonyms, and linked support programs. Search by name, abbreviation, or synonym.

Try: "IgA nephropathy", "C3G", "Berger's disease", "PKU", "Duchenne"

9 matching diseasesClear search ×

Crigler-Najjar syndrome type 1

Bilirubin uridinediphosphate glucuronosyltransferase deficiency type 1 · Bilirubin-UGT deficiency type 1

ORPHA:79234

Adenine phosphoribosyltransferase deficiency

2,8-dihydroxyadenine urolithiasis · APRT deficiency

ORPHA:976

ALG1-CDG

CDG syndrome type Ik · CDG-Ik

ORPHA:79327

ALG6-CDG

CDG syndrome type Ic · CDG-Ic

ORPHA:79320

ALG8-CDG

CDG syndrome type Ih · CDG-Ih

ORPHA:79325

Classic galactosemia

GALT deficiency · Galactose-1-phosphate uridyltransferase deficiency

ORPHA:79239

Crigler-Najjar syndrome

Bilirubin uridinediphosphate glucuronosyltransferase deficiency · Bilirubin-UGT deficiency

ORPHA:205

Crigler-Najjar syndrome type 2

Bilirubin uridinediphosphate glucuronosyltransferase deficiency type 2 · Bilirubin-UGT deficiency type 2

ORPHA:79235

Galactose epimerase deficiency

Epimerase deficiency galactosemia · GALE deficiency

ORPHA:79238