Rare Disease Library

Browse Orphanet-curated rare diseases with HPO phenotype annotations, synonyms, and linked support programs. Search by name, abbreviation, or synonym.

Try: "IgA nephropathy", "C3G", "Berger's disease", "PKU", "Duchenne"

5 matching diseasesClear search ×

Beta-ketothiolase deficiency

3-ketothiolase deficiency · 3-oxothiolase deficiency

ORPHA:134

2-aminoadipic 2-oxoadipic aciduria

Alpha-aminoadipic aciduria

ORPHA:79154

2-methylbutyryl-CoA dehydrogenase deficiency

2-methylbutyric aciduria · Developmental delay due to 2-methylbutyryl-CoA dehydrogenase deficiency

ORPHA:79157

3-methylglutaconic aciduria

ORPHA:289902

Neurodegeneration due to 3-hydroxyisobutyryl-CoA hydrolase deficiency

HIBCH deficiency · Methacrylic aciduria

ORPHA:88639