Vasculitis

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ORPHA:52759
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13Active trials52Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Vasculitis is a group of diseases where the immune system mistakenly attacks and inflames the walls of blood vessels. This inflammation can affect arteries, veins, or small capillaries anywhere in the body. When blood vessel walls become swollen and damaged, blood flow to organs and tissues can be reduced or blocked, which can cause serious harm. There are many different types of vasculitis, including Giant Cell Arteritis, Granulomatosis with Polyangiitis (formerly called Wegener's granulomatosis), Polyarteritis Nodosa, Takayasu Arteritis, Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss syndrome), Microscopic Polyangiitis, and IgA Vasculitis (Henoch-Schönlein Purpura), among others. Each type tends to affect different blood vessel sizes and different parts of the body. Symptoms vary widely depending on which vessels are involved, but common signs include fatigue, fever, skin rashes, joint pain, and organ damage. Some forms mainly affect the skin, while others can damage the kidneys, lungs, nerves, or eyes. Because vasculitis can look like many other conditions, it is often difficult to diagnose quickly. Treatment usually involves medicines that calm the immune system, such as corticosteroids like prednisone, and stronger immunosuppressants like cyclophosphamide, azathioprine, methotrexate, or rituximab. Some forms of vasculitis can go into remission with treatment, while others require long-term management. Early diagnosis and treatment are key to preventing permanent organ damage.

Also known as:

Key symptoms:

Extreme tiredness and fatigueFever and night sweatsSkin rashes, red or purple spots, or soresJoint pain and swellingMuscle achesNumbness or tingling in hands and feetShortness of breath or coughBlood in urine or reduced kidney functionHeadachesVision changes or vision lossAbdominal painUnintended weight lossSinus problems or nosebleedsHigh blood pressureSwollen lymph nodes

Inheritance

Multifactorial

Caused by a mix of several genes and environmental factors

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

FDA & Trial Timeline

10 events
Mar 2026Role of Vessel Wall MRI in Differentiaition Between Intracranial Atherosclerotic Disease and Vasculitis as Causes of Ischemic Stroke

Assiut University — NA

TrialNOT YET RECRUITING
Nov 2025Prevention of Phlebitis, Infiltration and Extravasation With Infusion Monitoring System

Ordu University — NA

TrialNOT YET RECRUITING
Oct 2025The RheumSafer Study: Improving Medication Appropriateness in People With Rheumatic Conditions

McGill University Health Centre/Research Institute of the McGill University Health Centre

TrialRECRUITING
Dec 2024Vaccination Against Herpes Zoster in Patients With Inflammatory Rheumatic Diseases

Region Skane — PHASE4

TrialENROLLING BY INVITATION
Dec 2024Characterization of "Bamboo" and Other Vocal Cord Lesions Responsible for Dysphonia in Patients With Systemic Autoimmune Diseases (BAMBOO)

University Hospital, Brest

TrialRECRUITING
Nov 2024MEMRI and Kidney Disease

University of Edinburgh

TrialRECRUITING
Nov 2024The Effect of Catheter Protector on Catheter Dwell Time and Complications

Karamanoğlu Mehmetbey University — NA

TrialNOT YET RECRUITING
Jan 2024ROLE of PLATELETS in the PATHOPHYSIOLOGY of SYSTEMIC LUPUS

University Hospital, Strasbourg, France

TrialRECRUITING
Jan 2024Prediction of Risk of Vascular Structural Damage in Patients With Large Vessel Vasculitis (LVV) Based on PET/MRA Image Evaluation System

Nanjing Medical University

TrialRECRUITING
Mar 2023Longitudinal Study for Central Nervous System Vasculitis

University of Pennsylvania

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Vasculitis.

13 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

13 recruitingView all trials with filters →
Phase 41 trial
Vaccination Against Herpes Zoster in Patients With Inflammatory Rheumatic Diseases
Phase 4
Enrolling by Invitation
· Sites: Lund · Age: 1899 yrs
N/A2 trials
Biomarkers in Autoimmune Diseases, Vasculitis and Auto Inflammatory Diseases
N/A
Actively Recruiting
PI: David Saadoun, Professor (Assistance Publique - Hôpitaux de Paris) · Sites: Paris, France · Age: 1899 yrs
Leflunomide for Henoch-Schonlein Purpura
N/A
Actively Recruiting
PI: Weiping Tan, PhD (Sun Yat-Sen Memorial Hospital of Sun Yat-Sen Unive) · Sites: Guangzhou, Guangdong · Age: 118 yrs
Other10 trials
Special Drug Use-results Survey for Long-term Use(Avacopan)
Actively Recruiting
· Sites: Multiple Locations
Characterization of "Bamboo" and Other Vocal Cord Lesions Responsible for Dysphonia in Patients With Systemic Autoimmune Diseases (BAMBOO)
Actively Recruiting
· Sites: Brest · Age: 1899 yrs
Whole Exome Sequencing of Familial and Pediatric Forms of Vasculitis
Actively Recruiting
PI: Benjamin Terrier, MD, PhD (French Vasculitis Study Group) · Sites: Paris, Île-de-France Region
Longitudinal Study for Central Nervous System Vasculitis
Actively Recruiting
PI: Rula Hajj-Ali, MD (The Cleveland Clinic) · Sites: Rochester, Minnesota; Cleveland, Ohio +4 more · Age: 1899 yrs
ROLE of PLATELETS in the PATHOPHYSIOLOGY of SYSTEMIC LUPUS
Actively Recruiting
· Sites: Strasbourg, France · Age: 1870 yrs
Vasculitis Pregnancy Registry
Actively Recruiting
PI: Megan Clowse, MD, MPH (Duke University) · Sites: Tampa, Florida · Age: 1850 yrs
The RheumSafer Study: Improving Medication Appropriateness in People With Rheumatic Conditions
Actively Recruiting
PI: Arielle Mendel, MD MSc (RI-MUHC/MUHC) · Sites: Montreal, Quebec · Age: 6099 yrs
Prediction of Risk of Vascular Structural Damage in Patients With Large Vessel Vasculitis (LVV) Based on PET/MRA Image Evaluation System
Actively Recruiting
· Sites: Nanjing, Jiangsu · Age: 1899 yrs
JOURNEY II XR Safety and Effectiveness PMCF
Active
· Sites: Loma Linda, California; Fort Lauderdale, Florida +12 more · Age: 2275 yrs
MEMRI and Kidney Disease
Actively Recruiting
· Sites: Edinburgh · Age: 1899 yrs

Specialists

Showing 25 of 52View all specialists →
FF
Francesco Ferro
Specialist
4 Vasculitis publications
SM
Sara Monti
Specialist
3 Vasculitis publications
RT
Rosaria Talarico
Specialist
4 Vasculitis publications
NI
Nazzareno Italiano
Specialist
2 Vasculitis publications
LQ
Luca Quartuccio
Specialist
3 Vasculitis publications
ET
Elena Treppo
Specialist
3 Vasculitis publications
GR
Gaetano La Rocca
Specialist
2 Vasculitis publications
PD
Paolo Delvino
Specialist
3 Vasculitis publications
RW
Richard A Watts
Specialist
2 Vasculitis publications
MM
Michele Moretti
Specialist
4 Vasculitis publications
CL
Carol A Langford
JAMAICA PLAIN, MA
Specialist
2 Vasculitis publications
FC
Federica Di Cianni
Specialist
3 Vasculitis publications
CB
Chiara Baldini
Specialist
4 Vasculitis publications
SM
Shubhasree Banerjee, MD
PHILADELPHIA, PA
Specialist
PI on 2 active trials
CM
Cornelia D Cudrici, M.D.
BETHESDA, MD
Specialist
PI on 2 active trials
BP
Benjamin Terrier, MD, PhD
Specialist
PI on 2 active trials
AD
ARLET Philippe, D
Specialist
PI on 1 active trial
RM
Rennie Rhee, MD
PHILADELPHIA, PA
Specialist
PI on 1 active trial
TM
Thomas Maldiney
Specialist
PI on 2 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Vasculitis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Vasculitis

Disease timeline:

New recruiting trial: ROLE of PLATELETS in the PATHOPHYSIOLOGY of SYSTEMIC LUPUS

A new clinical trial is recruiting patients for Vasculitis

New recruiting trial: The RheumSafer Study: Improving Medication Appropriateness in People With Rheumatic Conditions

A new clinical trial is recruiting patients for Vasculitis

New recruiting trial: Effects of Topical Sesame Oil in the Prevention of Peripheral Venous Catheter Phlebitis: Clinical Trial.

A new clinical trial is recruiting patients for Vasculitis

New recruiting trial: Prediction of Risk of Vascular Structural Damage in Patients With Large Vessel Vasculitis (LVV) Based on PET/MRA Image Evaluation System

A new clinical trial is recruiting patients for Vasculitis

New recruiting trial: Characterization of "Bamboo" and Other Vocal Cord Lesions Responsible for Dysphonia in Patients With Systemic Autoimmune Diseases (BAMBOO)

A new clinical trial is recruiting patients for Vasculitis

New recruiting trial: Longitudinal Study for Central Nervous System Vasculitis

A new clinical trial is recruiting patients for Vasculitis

New recruiting trial: Whole Exome Sequencing of Familial and Pediatric Forms of Vasculitis

A new clinical trial is recruiting patients for Vasculitis

New recruiting trial: MEMRI and Kidney Disease

A new clinical trial is recruiting patients for Vasculitis

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which specific type of vasculitis do I have, and how does that affect my treatment plan?,Which organs are currently affected, and how do we monitor for damage over time?,What are the side effects of the medications you are recommending, and how will we manage them?,How will we know if the treatment is working, and what does remission look like for my type of vasculitis?,What are the warning signs of a flare or a serious complication that should prompt me to go to the emergency room?,Are there any clinical trials or newer treatments I should consider?,What lifestyle changes, vaccinations, or precautions should I take while on immunosuppressive therapy?

Common questions about Vasculitis

What is Vasculitis?

Vasculitis is a group of diseases where the immune system mistakenly attacks and inflames the walls of blood vessels. This inflammation can affect arteries, veins, or small capillaries anywhere in the body. When blood vessel walls become swollen and damaged, blood flow to organs and tissues can be reduced or blocked, which can cause serious harm. There are many different types of vasculitis, including Giant Cell Arteritis, Granulomatosis with Polyangiitis (formerly called Wegener's granulomatosis), Polyarteritis Nodosa, Takayasu Arteritis, Eosinophilic Granulomatosis with Polyangiitis (Churg-S

How is Vasculitis inherited?

Vasculitis follows a multifactorial inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Are there clinical trials for Vasculitis?

Yes — 13 recruiting clinical trials are currently listed for Vasculitis on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Vasculitis?

25 specialists and care centers treating Vasculitis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.