Tracheobronchopathia osteochondroplastica

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ORPHA:3348OMIM:189961J98.0
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8Treatment centers

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UniteRare data is compiled from authoritative primary sources (FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, NORD), then processed through automated and AI-assisted extraction pipelines.
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What is Tracheobronchopathia osteochondroplastica?

Tracheobronchopathia osteochondroplastica does not yet have FDA-approved treatments tracked on UniteRare.

Also known as:

Key symptoms:

Chronic coughShortness of breath, especially with activityWheezing or noisy breathingRecurrent respiratory infections or pneumoniaDifficulty clearing mucus from the airwaysCoughing up blood (hemoptysis)Hoarseness or voice changesFeeling of something stuck in the throatChest tightnessStridor (a high-pitched breathing sound)

Clinical phenotype terms (23)— hover any for plain English
  • Tracheal calcificationHP:0002787
  • Productive coughHP:0031245
  • Tracheal stenosisHP:0002777
  • Upper airway obstructionHP:0002781
  • Abnormal tracheobronchial morphologyHP:0005607
  • BronchitisHP:0012387
  • Abnormal bronchus morphologyHP:0025426
  • Abnormal sputumHP:0032016
  • Calcification of cartilageHP:0100593
  • EsophagitisHP:0100633
Inheritance
Sporadic
Usually appears on its own, not inherited from a parent
Age of Onset
Adult
Begins in adulthood (age 18 or older)
Orphanet ↗OMIM ↗NORD ↗

Treatments

Source: openFDA + DailyMed · NDA / BLA labels with structured indications · refreshed weekly

No FDA-approved treatments are currently listed for Tracheobronchopathia osteochondroplastica.

View clinical trials →

Source: ClinicalTrials.gov · synced daily · phases, status, and PI names normalized at ingest

No actively recruiting trials found for Tracheobronchopathia osteochondroplastica at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Tracheobronchopathia osteochondroplastica community →

Source: NPI Registry + PubMed · trial PI roles cross-referenced with ClinicalTrials.gov · ranked by match score (publications + PI activity + community signal)

No specialists are currently listed for Tracheobronchopathia osteochondroplastica.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers

Source: NORD Rare Disease Centers + NIH Undiagnosed Diseases Network (UDN) · centers verified active within last 12 months

🏨 Children's

Children's Hospital Colorado Rare Disease Program

Children's Hospital Colorado

📍 Aurora, CO

👤 Boston Children's Hospital Rare Disease Program

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Boston Children's Hospital Rare Disease Program

Boston Children's Hospital

📍 Boston, MA

👤 Boston Children's Hospital Rare Disease Program

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

🏨 Children's

Ann & Robert H. Lurie Children's Hospital Genetics

Lurie Children's Hospital

📍 Chicago, IL

👤 Boston Children's Hospital Rare Disease Program

🏥 NORD

Cincinnati Children's Hospital Medical Center

Cincinnati Children's

📍 Cincinnati, OH

👤 Boston Children's Hospital Rare Disease Program

🏨 Children's

Nationwide Children's Hospital Rare Disease Center

Nationwide Children's Hospital

📍 Columbus, OH

👤 Boston Children's Hospital Rare Disease Program

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

Travel Grants

No travel grants are currently matched to Tracheobronchopathia osteochondroplastica.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Tracheobronchopathia osteochondroplastica

Source: PubMed + NIH RePORTER + openFDA + clinical-journal RSS · last 30 days · disease-tagged at ingest by AI extraction with human QC

No recent news articles for Tracheobronchopathia osteochondroplastica.

Follow this condition to be notified when news becomes available.

Caregiver Resources

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is the narrowing in my airways, and is it affecting my lung function?,Do I need any treatment right now, or can we monitor the condition over time?,How often should I have follow-up bronchoscopies or CT scans?,What symptoms should prompt me to seek urgent medical care?,Are there any activities or environmental exposures I should avoid?,If my symptoms worsen, what treatment options would you recommend?,Could my recurrent respiratory infections be related to this condition?

Common questions about Tracheobronchopathia osteochondroplastica

What is Tracheobronchopathia osteochondroplastica?

Tracheobronchopathia osteochondroplastica (TO), sometimes called tracheobronchial osteochondroplastica or tracheopathia osteoplastica, is a rare, benign condition that affects the airways. In this disease, small bony and cartilage-like nodules grow from the walls of the trachea (windpipe) and large bronchi (the main airways leading to the lungs). These hard nodules project inward into the airway, which can narrow the breathing passages over time. Importantly, the back wall of the trachea (the membranous part) is typically spared, which is a hallmark feature that helps doctors distinguish it fr

How is Tracheobronchopathia osteochondroplastica inherited?

Tracheobronchopathia osteochondroplastica follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Tracheobronchopathia osteochondroplastica typically begin?

Typical onset of Tracheobronchopathia osteochondroplastica is adult. Age of onset can vary across affected individuals.

Frequently asked questions about Tracheobronchopathia osteochondroplastica

Auto-generated from canonical disease facts (Orphanet, OMIM, ClinicalTrials.gov, openFDA, NPPES). Not a substitute for clinical guidance.

  1. What is Tracheobronchopathia osteochondroplastica?

    Tracheobronchopathia osteochondroplastica is a rare disease catalogued in international rare-disease ontologies (Orphanet ORPHA:3348, OMIM 189961). It is typically inherited as sporadic. Age of onset is generally adult. For verified primary sources, see the UniteRare Tracheobronchopathia osteochondroplastica page.

  2. How is Tracheobronchopathia osteochondroplastica inherited?

    Tracheobronchopathia osteochondroplastica follows sporadic inheritance. Genetic counseling is recommended for affected families to understand recurrence risk in offspring and the likelihood of unaffected siblings being carriers. Variants in the underlying gene(s) may be identified via clinical genetic testing.

  3. Are there FDA-approved treatments for Tracheobronchopathia osteochondroplastica?

    Approved treatments for Tracheobronchopathia osteochondroplastica are tracked from openFDA and DailyMed primary sources. Many rare diseases have no specific FDA-approved therapy; for those, supportive care and management of complications form the basis of clinical care. Orphan-drug-designation status is noted where applicable.

  4. Are there clinical trials for Tracheobronchopathia osteochondroplastica?

    Active clinical trials for Tracheobronchopathia osteochondroplastica are tracked daily from ClinicalTrials.gov. Trial availability changes frequently; check the UniteRare trial listings for the current count and recruitment status. Sponsors of rare-disease research often welcome inquiries even when a trial is not actively recruiting at a given moment.

  5. How do I find a specialist for Tracheobronchopathia osteochondroplastica?

    Verified Tracheobronchopathia osteochondroplastica specialists are identified through ClinicalTrials.gov principal-investigator records, peer-reviewed publication authorship (via PubMed), and the NPPES NPI registry. NORD-designated Centers of Excellence and NIH-affiliated rare-disease clinics are also tracked. UniteRare's specialist directory is updated continuously as new evidence becomes available.

See full Tracheobronchopathia osteochondroplastica page for complete clinical details, sources, and verified-specialist listings.

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