STT3B-CDG

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ORPHA:370924OMIM:615597E77.8
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8Treatment centers

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Overview

STT3B-CDG (also known as STT3B-congenital disorder of glycosylation) is an extremely rare inherited metabolic condition that affects how the body attaches sugar molecules to proteins, a process called glycosylation. This process is essential for many proteins to work properly throughout the body. The STT3B gene provides instructions for making a part of the protein complex responsible for this sugar attachment process in cells. When the STT3B gene has harmful changes (mutations), the glycosylation process does not work correctly, which can lead to problems in multiple organ systems. People with STT3B-CDG may experience intellectual disability, developmental delays, seizures, and problems with muscle tone. Some individuals may also have vision problems, feeding difficulties, and distinctive facial features. The severity of symptoms can vary from person to person. Because this condition is so rare, the full range of symptoms is still being understood as more patients are identified. There is currently no cure for STT3B-CDG. Treatment focuses on managing individual symptoms and providing supportive care. This may include physical therapy, occupational therapy, speech therapy, anti-seizure medications, and nutritional support. A team of specialists typically works together to address the various needs of affected individuals. Early intervention and ongoing monitoring are important to optimize quality of life.

Also known as:

Key symptoms:

Intellectual disabilityDevelopmental delaysSeizuresLow muscle tone (floppiness)Feeding difficultiesFailure to thrive or poor growthDistinctive facial featuresVision problemsSpeech and language delaysDelayed motor milestones like sitting and walkingBehavioral difficultiesAbnormal blood clotting

Clinical phenotype terms (17)— hover any for plain English
Abnormal glycosylationHP:0012345
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for STT3B-CDG.

View clinical trials →

No actively recruiting trials found for STT3B-CDG at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the STT3B-CDG community →

No specialists are currently listed for STT3B-CDG.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to STT3B-CDG.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about STT3B-CDG

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific mutations were found in my child's STT3B gene, and what do they mean for prognosis?,What therapies should we start right away to support development?,How should we monitor and manage seizures?,Are there any dietary or nutritional changes that could help?,How often should we schedule follow-up visits with each specialist?,Are there any clinical trials or research studies we could participate in?,Should other family members be tested to see if they are carriers?

Common questions about STT3B-CDG

What is STT3B-CDG?

STT3B-CDG (also known as STT3B-congenital disorder of glycosylation) is an extremely rare inherited metabolic condition that affects how the body attaches sugar molecules to proteins, a process called glycosylation. This process is essential for many proteins to work properly throughout the body. The STT3B gene provides instructions for making a part of the protein complex responsible for this sugar attachment process in cells. When the STT3B gene has harmful changes (mutations), the glycosylation process does not work correctly, which can lead to problems in multiple organ systems. People wi

How is STT3B-CDG inherited?

STT3B-CDG follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does STT3B-CDG typically begin?

Typical onset of STT3B-CDG is infantile. Age of onset can vary across affected individuals.