Rare odontal or periodontal disorder

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ORPHA:164001
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Overview

Rare odontal or periodontal disorders are a group of uncommon conditions that affect the teeth (odontal) or the tissues that support the teeth, such as the gums, bone, and ligaments (periodontal). These disorders can cause a wide range of dental and oral problems that go beyond what is seen in common dental disease. Patients may experience abnormal tooth development, missing teeth, teeth that are unusually shaped or sized, early tooth loss, or severe gum disease that starts at a young age. Some of these conditions are present from birth or early childhood, while others may not become apparent until later in life. Because this is a broad category of rare disorders, the specific symptoms and severity can vary greatly from person to person. Some patients may have isolated dental problems, while others may have dental issues as part of a larger genetic syndrome that affects other parts of the body. The underlying cause can be genetic, involving mutations in genes important for tooth and gum development, or in some cases the cause remains unknown. Treatment is generally focused on managing symptoms and preserving dental health for as long as possible. This may include regular dental cleanings, specialized periodontal treatments, dental implants, dentures, orthodontic work, or surgical procedures. Early diagnosis and a strong relationship with a dental specialist are important for the best possible outcomes. Research into the genetic causes of these conditions is ongoing, which may lead to more targeted treatments in the future.

Key symptoms:

Missing teeth from birth (congenitally absent teeth)Teeth that are abnormally shaped or smaller than usualEarly or premature loss of baby teeth or adult teethSevere gum disease starting at a young ageGum swelling, redness, or bleedingLoose teeth without an obvious causeDelayed eruption of teethExtra teeth or teeth in unusual positionsThin or weakened tooth enamelBone loss around the teethDifficulty chewing or bitingTooth sensitivity or painBad breath that does not improve with regular brushing

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Rare odontal or periodontal disorder.

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No actively recruiting trials found for Rare odontal or periodontal disorder at this time.

New trials open frequently. Follow this disease to get notified.

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No specialists are currently listed for Rare odontal or periodontal disorder.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Rare odontal or periodontal disorder.

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Community

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Latest news about Rare odontal or periodontal disorder

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific rare dental or periodontal condition does my child or I have?,Is genetic testing recommended, and what would it tell us?,How often should dental check-ups and cleanings be scheduled?,What are the best options for replacing missing teeth at this age?,Are there any treatments that can slow down tooth loss or gum disease?,Should other family members be evaluated for this condition?,Are there any clinical trials or new treatments being studied for this condition?

Common questions about Rare odontal or periodontal disorder

What is Rare odontal or periodontal disorder?

Rare odontal or periodontal disorders are a group of uncommon conditions that affect the teeth (odontal) or the tissues that support the teeth, such as the gums, bone, and ligaments (periodontal). These disorders can cause a wide range of dental and oral problems that go beyond what is seen in common dental disease. Patients may experience abnormal tooth development, missing teeth, teeth that are unusually shaped or sized, early tooth loss, or severe gum disease that starts at a young age. Some of these conditions are present from birth or early childhood, while others may not become apparent