Rare non-malformative uterovaginal or vulvovaginal disease

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ORPHA:180205
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1Active trials8Treatment centers

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UniteRare data is compiled from authoritative primary sources (FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, NORD), then processed through automated and AI-assisted extraction pipelines.
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What is Rare non-malformative uterovaginal or vulvovaginal disease?

Rare non-malformative uterovaginal or vulvovaginal disease is a broad category name used by Orphanet to group together uncommon conditions that affect the uterus, vagina, or vulva but are not caused by birth defects or structural malformations. These conditions are distinct from congenital anomalies — instead, they develop over time and may involve abnormal tissue growth, inflammation, scarring, or other changes in the reproductive tract. Examples within this group can include conditions like vaginal adenosis, vulvar vestibulitis syndrome (provoked vulvodynia), vulvar lichen sclerosus, and other rare inflammatory or functional disorders of these organs. Symptoms vary widely depending on the specific condition but may include chronic pain in the vulvar or vaginal area, painful intercourse, abnormal vaginal discharge, itching, burning sensations, and changes in the appearance of vulvar or vaginal tissue. Some conditions in this group can significantly affect quality of life, sexual health, and emotional well-being. Treatment depends on the specific diagnosis within this category. Options may include topical medications such as corticosteroids or estrogen creams, pain management strategies, physical therapy for pelvic floor muscles, and in some cases surgical procedures. Because this is a grouping category rather than a single disease, patients should work closely with specialists to identify their exact condition and develop a personalized treatment plan.

Key symptoms:

Chronic vulvar pain or burningPainful intercourseVaginal itching or irritationAbnormal vaginal dischargeWhite patches or skin changes on the vulvaThinning or scarring of vulvar skinPelvic discomfort or pressurePainful urinationBleeding after intercourseSwelling or redness of vulvar tissueDifficulty with tampon insertionChronic inflammation of vaginal tissue

Inheritance
Variable
Can be inherited in different ways depending on the underlying gene
Age of Onset
Variable
Can begin at different ages, from infancy through adulthood
Orphanet ↗NORD ↗

FDA & Trial Timeline

2 events
May 2026A 52-Week Trial to Investigate the Efficacy and Safety of Delgocitinib Cream in Adult Participants With Lichen Sclerosus

LEO Pharma — PHASE3

TrialNOT YET RECRUITING
Feb 2025Vulvodynia Intervention: the Effect of Multimodal Treatment for Provoked Vulvodynia

Karlstad University — NA

TrialRECRUITING

Data is compiled from FDA regulatory filings and ClinicalTrials.gov, then processed through automated extraction; event classifications and dates may occasionally be misclassified. Verify against the linked FDA filing or trial record before clinical decisions. Updated periodically.

Treatments

Source: openFDA + DailyMed · NDA / BLA labels with structured indications · refreshed weekly

No FDA-approved treatments are currently listed for Rare non-malformative uterovaginal or vulvovaginal disease.

1 clinical trialare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

1 recruitingView all trials with filters →

Source: ClinicalTrials.gov · synced daily · phases, status, and PI names normalized at ingest

N/A1 trial
Vulvodynia Intervention: the Effect of Multimodal Treatment for Provoked Vulvodynia
N/A
Actively Recruiting
· Sites: Karlstad · Age: 18–40 yrs

Source: NPI Registry + PubMed · trial PI roles cross-referenced with ClinicalTrials.gov · ranked by match score (publications + PI activity + community signal)

No specialists are currently listed for Rare non-malformative uterovaginal or vulvovaginal disease.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers

Source: NORD Rare Disease Centers + NIH Undiagnosed Diseases Network (UDN) · centers verified active within last 12 months

🏨 Children's

Children's Hospital Colorado Rare Disease Program

Children's Hospital Colorado

📍 Aurora, CO

👤 Boston Children's Hospital Rare Disease Program

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Boston Children's Hospital Rare Disease Program

Boston Children's Hospital

📍 Boston, MA

👤 Boston Children's Hospital Rare Disease Program

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

🏨 Children's

Ann & Robert H. Lurie Children's Hospital Genetics

Lurie Children's Hospital

📍 Chicago, IL

👤 Boston Children's Hospital Rare Disease Program

🏥 NORD

Cincinnati Children's Hospital Medical Center

Cincinnati Children's

📍 Cincinnati, OH

👤 Boston Children's Hospital Rare Disease Program

🏨 Children's

Nationwide Children's Hospital Rare Disease Center

Nationwide Children's Hospital

📍 Columbus, OH

👤 Boston Children's Hospital Rare Disease Program

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

Travel Grants

No travel grants are currently matched to Rare non-malformative uterovaginal or vulvovaginal disease.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Rare non-malformative uterovaginal or vulvovaginal disease

Source: PubMed + NIH RePORTER + openFDA + clinical-journal RSS · last 30 days · disease-tagged at ingest by AI extraction with human QC

No recent news articles for Rare non-malformative uterovaginal or vulvovaginal disease.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is my specific diagnosis within this category of conditions?,What are the treatment options, and what are the expected benefits and side effects?,Is a biopsy needed to confirm the diagnosis?,How often should I have follow-up appointments and monitoring?,Are there any lifestyle changes that could help manage my symptoms?,Should I see a pelvic floor physical therapist?,Is there any risk of this condition progressing or leading to other complications?

Common questions about Rare non-malformative uterovaginal or vulvovaginal disease

What is Rare non-malformative uterovaginal or vulvovaginal disease?

Rare non-malformative uterovaginal or vulvovaginal disease is a broad category name used by Orphanet to group together uncommon conditions that affect the uterus, vagina, or vulva but are not caused by birth defects or structural malformations. These conditions are distinct from congenital anomalies — instead, they develop over time and may involve abnormal tissue growth, inflammation, scarring, or other changes in the reproductive tract. Examples within this group can include conditions like vaginal adenosis, vulvar vestibulitis syndrome (provoked vulvodynia), vulvar lichen sclerosus, and oth

Are there clinical trials for Rare non-malformative uterovaginal or vulvovaginal disease?

Yes — 1 recruiting clinical trial is currently listed for Rare non-malformative uterovaginal or vulvovaginal disease on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Frequently asked questions about Rare non-malformative uterovaginal or vulvovaginal disease

Auto-generated from canonical disease facts (Orphanet, OMIM, ClinicalTrials.gov, openFDA, NPPES). Not a substitute for clinical guidance.

  1. What is Rare non-malformative uterovaginal or vulvovaginal disease?

    Rare non-malformative uterovaginal or vulvovaginal disease is a rare disease catalogued in international rare-disease ontologies (Orphanet ORPHA:180205). It is typically inherited as variable. Age of onset is generally variable. For verified primary sources, see the UniteRare Rare non-malformative uterovaginal or vulvovaginal disease page.

  2. How is Rare non-malformative uterovaginal or vulvovaginal disease inherited?

    Rare non-malformative uterovaginal or vulvovaginal disease follows variable inheritance. Genetic counseling is recommended for affected families to understand recurrence risk in offspring and the likelihood of unaffected siblings being carriers. Variants in the underlying gene(s) may be identified via clinical genetic testing.

  3. Are there FDA-approved treatments for Rare non-malformative uterovaginal or vulvovaginal disease?

    Approved treatments for Rare non-malformative uterovaginal or vulvovaginal disease are tracked from openFDA and DailyMed primary sources. Many rare diseases have no specific FDA-approved therapy; for those, supportive care and management of complications form the basis of clinical care. Orphan-drug-designation status is noted where applicable.

  4. Are there clinical trials recruiting for Rare non-malformative uterovaginal or vulvovaginal disease?

    UniteRare currently lists 1 clinical trial relevant to Rare non-malformative uterovaginal or vulvovaginal disease sourced from ClinicalTrials.gov. Each trial entry includes recruitment status, eligibility criteria summary, principal-investigator information, and study locations. Patients should discuss eligibility with their healthcare provider before enrolling.

  5. How do I find a specialist for Rare non-malformative uterovaginal or vulvovaginal disease?

    Verified Rare non-malformative uterovaginal or vulvovaginal disease specialists are identified through ClinicalTrials.gov principal-investigator records, peer-reviewed publication authorship (via PubMed), and the NPPES NPI registry. NORD-designated Centers of Excellence and NIH-affiliated rare-disease clinics are also tracked. UniteRare's specialist directory is updated continuously as new evidence becomes available.

See full Rare non-malformative uterovaginal or vulvovaginal disease page for complete clinical details, sources, and verified-specialist listings.

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