Pancreatic solid pseudopapillary neoplasm

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3Active trials8Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Pancreatic solid pseudopapillary neoplasm (SPN), also called solid pseudopapillary tumor (SPT) or Frantz tumor, is a rare type of pancreatic tumor. Unlike most pancreatic cancers, this tumor tends to grow slowly and is usually considered low-grade, meaning it is not as aggressive as other pancreatic cancers. It gets its name from how it looks under a microscope — it has both solid and papillary (finger-like) structures mixed together. This tumor most commonly affects young women, especially those in their teens, twenties, and thirties. It can grow in any part of the pancreas — the head, body, or tail. As the tumor grows, it may press on nearby organs and cause symptoms like belly pain, a feeling of fullness, or a lump you can feel in the abdomen. Many people are diagnosed by accident when imaging is done for another reason. The good news is that surgery to remove the tumor is usually curative. Most people who have the tumor fully removed do very well long-term. In rare cases, the tumor can spread to the liver or nearby tissues, but even then, treatment options exist. Overall, the outlook for this condition is much better than for most other pancreatic tumors.

Also known as:

Key symptoms:

Dull or aching pain in the upper belly or abdomenA feeling of fullness or bloating after eating small amountsA lump or mass you can feel in the abdomenNausea or vomitingUnexplained weight lossLoss of appetiteBack painFatigue or tirednessJaundice (yellowing of the skin or eyes) if the tumor blocks the bile ductAccidental discovery on imaging done for another reason (no symptoms at all)

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Juvenile

Begins in the teen years

Orphanet ↗NORD ↗

FDA & Trial Timeline

10 events
Jan 2026Smoking Cessation Before Bronchoscopy or CT-guided Puncture

RWTH Aachen University

TrialRECRUITING
Sep 2025An Exploratory Clinical Study on the Safety and Efficacy of Autologous NK Cells in the Treatment of Pulmonary Nodules

The First Affiliated Hospital with Nanjing Medical University — EARLY_PHASE1

TrialRECRUITING
Sep 2025The Effect of the Timing of Supplemental Parenteral Nutrition on the Prognosis of Critically Ill Patients (T-SPN)

Dong Zhang — NA

TrialRECRUITING
Sep 2025Multicentric Database for Solid Pseudopapillary Neoplasm of the Pancreas

Fudan University

TrialRECRUITING
Mar 2025Tamoxifen for Advanced Solid Pseudopapillary Tumor of the Pancreas

Fudan University — PHASE2

TrialRECRUITING
Jan 2025Confocal Laser Endomicroscopy Guided Cryobiopsy in the Diagnosis of Interstitial Lung Disease

China-Japan Friendship Hospital — NA

TrialNOT YET RECRUITING
Dec 2024In-depth Analysis of the Immune Responses in the Upper Respiratory Tract in Older Adults Infected or Colonized With Streptococcus Pneumoniae (Spn)

University Hospital, Geneva

TrialRECRUITING
Dec 2024A Prospective, Non-interventional Cohort Study of Subsolid Pulmonary Nodules

Guangdong Provincial People's Hospital

TrialNOT YET RECRUITING
Nov 2024Robotic Versus Electromagnetic Bronchoscopy for Pulmonary LesIon AssessmeNT Using Integrated Intraprocedural Imaging

Vanderbilt University Medical Center — NA

TrialACTIVE NOT RECRUITING
Jun 2024Differentiation of Benign and Malignant Pulmonary Nodules by Volatile Organic Compounds in Human Exhaled Breath

ChromX Health

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Pancreatic solid pseudopapillary neoplasm.

3 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

3 recruitingView all trials with filters →
Phase 21 trial
Tamoxifen for Advanced Solid Pseudopapillary Tumor of the Pancreas
Phase 2
Actively Recruiting
PI: Guopei Luo Prof, MD (Shanghai Cancer Center) · Sites: Shanghai · Age: 1480 yrs
Other2 trials
Cross-sectional Follow-up on Digestive and Social Functions of SPN
Actively Recruiting
PI: Qiaofei Liu (Department of General Surgery, Peking Union Medica) · Sites: Beijing, Beijing Municipality
Multicentric Database for Solid Pseudopapillary Neoplasm of the Pancreas
Actively Recruiting
PI: Guopei Luo (Shanghai Cancer Center) · Sites: Shanghai, Special Administrative Region

Specialists

8 foundView all specialists →
GL
Guopei Luo
Specialist
PI on 1 active trial49 Pancreatic solid pseudopapillary neoplasm publications
SW
Sarah B Whittle
Specialist
PI on 1 active trial3 Pancreatic solid pseudopapillary neoplasm publications
GM
Guopei Luo Prof, MD
Specialist
PI on 1 active trial1 Pancreatic solid pseudopapillary neoplasm publication
AP
Anne Marie O'Broin-Lennon, MD, PhD
Specialist
PI on 1 active trial
QL
Qiaofei Liu
Specialist
PI on 1 active trial
XP
Xinghua Cheng, Ph.D
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Pancreatic solid pseudopapillary neoplasm.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Pancreatic solid pseudopapillary neoplasm

Disease timeline:

New recruiting trial: An Exploratory Clinical Study on the Safety and Efficacy of Autologous NK Cells in the Treatment of Pulmonary Nodules

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: In-depth Analysis of the Immune Responses in the Upper Respiratory Tract in Older Adults Infected or Colonized With Streptococcus Pneumoniae (Spn)

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: A Trial to Compare Robotic Assisted Bronchoscopy Ion's Clinical Utility for Peripheral Lung Nodule Access and Diagnosis to ENB

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: DOLCE: Determining the Impact of Optellum's Lung Cancer Prediction Solution

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: Plasma Metabolomics as a Tool to Distinguish PET-positive Malignant From PET-positive Benign Nodules

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: Biomarkers for Risk Stratification in Lung Cancer

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: The Effect of the Timing of Supplemental Parenteral Nutrition on the Prognosis of Critically Ill Patients (T-SPN)

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: Differentiation of Benign and Malignant Pulmonary Nodules by Volatile Organic Compounds in Human Exhaled Breath

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: Assessment of a Radiomics-based Computer-Aided Diagnosis Tool for Pulmonary nodulES

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

New recruiting trial: Virtual Bronchoscopic Navigation to Increase Diagnostic Yield in Patients With Pulmonary Nodules

A new clinical trial is recruiting patients for Pancreatic solid pseudopapillary neoplasm

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Is my tumor completely removable with surgery, and what type of surgery do you recommend?,What are the risks of surgery, and how long will recovery take?,Will I need any additional treatment like chemotherapy or radiation after surgery?,How often will I need follow-up scans, and what are you looking for?,Could removing part of my pancreas affect my digestion or cause diabetes?,What are the chances the tumor could come back, and what would we do if it does?,Should I be seen at a specialized pancreatic cancer center for my care?

Common questions about Pancreatic solid pseudopapillary neoplasm

What is Pancreatic solid pseudopapillary neoplasm?

Pancreatic solid pseudopapillary neoplasm (SPN), also called solid pseudopapillary tumor (SPT) or Frantz tumor, is a rare type of pancreatic tumor. Unlike most pancreatic cancers, this tumor tends to grow slowly and is usually considered low-grade, meaning it is not as aggressive as other pancreatic cancers. It gets its name from how it looks under a microscope — it has both solid and papillary (finger-like) structures mixed together. This tumor most commonly affects young women, especially those in their teens, twenties, and thirties. It can grow in any part of the pancreas — the head, body,

How is Pancreatic solid pseudopapillary neoplasm inherited?

Pancreatic solid pseudopapillary neoplasm follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Pancreatic solid pseudopapillary neoplasm typically begin?

Typical onset of Pancreatic solid pseudopapillary neoplasm is juvenile. Age of onset can vary across affected individuals.

Are there clinical trials for Pancreatic solid pseudopapillary neoplasm?

Yes — 3 recruiting clinical trials are currently listed for Pancreatic solid pseudopapillary neoplasm on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Pancreatic solid pseudopapillary neoplasm?

8 specialists and care centers treating Pancreatic solid pseudopapillary neoplasm are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.