Oncogenic osteomalacia

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:352540M83.8
Who is this for?
Show terms as
2Active trials21Specialists8Treatment centers2Financial resources

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Oncogenic osteomalacia, also known as tumor-induced osteomalacia (TIO), is a rare condition where a usually small, slow-growing tumor produces too much of a hormone called fibroblast growth factor 23 (FGF23). This hormone tells the kidneys to get rid of phosphorus, a mineral that is essential for strong bones. When FGF23 levels are too high, phosphorus levels in the blood drop very low, causing the bones to become soft and weak — a condition called osteomalacia. The most common symptoms include bone pain, muscle weakness, and fractures that happen with little or no injury. Many patients also experience fatigue and difficulty walking. Because the symptoms develop slowly and can look like other conditions, it often takes years before the correct diagnosis is made. The tumors responsible are usually benign (not cancerous) and can be found almost anywhere in the body, including bones, soft tissues, and the skin. The good news is that oncogenic osteomalacia can often be cured if the tumor is found and completely removed through surgery. When the tumor cannot be located or fully removed, patients are treated with phosphorus supplements and active vitamin D (calcitriol) to manage symptoms. A newer medication called burosumab (Crysvita), which blocks FGF23, has also been approved for use in certain cases of tumor-induced osteomalacia where the tumor cannot be removed or found.

Also known as:

Key symptoms:

Bone pain, especially in the hips, back, and legsMuscle weaknessFractures from minor injuries or stress fracturesDifficulty walking or waddling gaitFatigue and low energyHeight loss over timeJoint painTrouble getting up from a chair or climbing stairsGeneralized body achesBone tenderness when pressedDecreased mobilityMultiple stress fractures in the feet or legs

Clinical phenotype terms (35)— hover any for plain English
Renal phosphate wastingHP:0000117HyperphosphaturiaHP:0003109Increased susceptibility to fracturesHP:0002659OsteomalaciaHP:0002749Neoplasm of the skeletal systemHP:0010622Low serum calcitriolHP:0012052Abnormal circulating fibroblast growth factor 23 concentrationHP:6000489
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

FDA & Trial Timeline

4 events
Mar 2023Al18F-NOTA-LM3 PET/CT in Patients With TIO

Peking Union Medical College Hospital — NA

TrialRECRUITING
Jan 2022Tumor-induced Osteomalacia Disease Monitoring Program

Ultragenyx Pharmaceutical Inc

TrialACTIVE NOT RECRUITING
Jun 2020

Crysvita: FDA approved

Crysvita (burosumab-twza) is indicated for the treatment of FGF23-related hypophosphatemia in tumor-induced osteomalacia (TIO) associated with phosphaturic mesenchymal tumors that cannot be curatively resected or localized.

FDAcompleted
Aug 2001

Zometa, Zabel: FDA approved

Treatment of hypercalcemia of malignancy.

FDAcompleted

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Oncogenic osteomalacia.

2 clinical trialsare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

2 recruitingView all trials with filters →
N/A1 trial
Al18F-NOTA-LM3 PET/CT in Patients With TIO
N/A
Actively Recruiting
· Sites: Beijing, Beijing Municipality · Age: 1880 yrs
Other1 trial
Tumor-induced Osteomalacia Disease Monitoring Program
Active
PI: Medical Director (Ultragenyx Pharmaceutical Inc) · Sites: New Haven, Connecticut; Bloomington, Indiana +4 more

Specialists

21 foundView all specialists →
SP
Shyang-Rong Shih, PhD
Specialist
PI on 2 active trials
SK
Santhosh D G Kumar
ATLANTA, GA
Specialist
1 Oncogenic osteomalacia publication
MD
Mohammad Hossein Dabbaghmanesh
Specialist
1 Oncogenic osteomalacia publication
IN
Iraj Nabipour
Specialist
1 Oncogenic osteomalacia publication
MR
Mohammdreza Ravanbod
Specialist
1 Oncogenic osteomalacia publication
MA
Majid Assadi
Specialist
1 Oncogenic osteomalacia publication
SK
Subramanian Kannan
FARMINGTON, CT
Specialist
1 Oncogenic osteomalacia publication
SK
Srikamakshi Kothandaraman
Specialist
1 Oncogenic osteomalacia publication
VY
Vishal Yadav
Specialist
1 Oncogenic osteomalacia publication
NC
Naveen H Chandrasekhar
Specialist
1 Oncogenic osteomalacia publication
HS
H V Sunil
Specialist
1 Oncogenic osteomalacia publication
RR
Rishi Raj
PIKEVILLE, KY
Specialist
1 Oncogenic osteomalacia publication
SH
Samaneh Hasanzadeh
Specialist
1 Oncogenic osteomalacia publication
MD
Mitra Dashtizadeh
Specialist
1 Oncogenic osteomalacia publication
MK
Mohammadreza Kalantarhormozi
Specialist
1 Oncogenic osteomalacia publication
KV
Katayoun Vahdat
Specialist
1 Oncogenic osteomalacia publication
SM
Stephen M Broski, MD
ROCHESTER, MN
Specialist
PI on 1 active trial
MM
Matthew Drake, MD
Specialist
PI on 1 active trial
HJ
Hongli Jing
Specialist
PI on 2 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Financial Resources

2 resources

Crysvita

Kyowa Kirin, Inc.

Crysvita — Contact Kyowa Kirin, Inc.

Unverified — confirm before calling
Patient Assistance
Manufacturer Program
Accepting applications

Zometa, Zabel

Novartis Pharmaceuticals Corp.

Unverified — confirm before calling
copay card
copay assistancePatient Assistance
Accepting applications

Travel Grants

No travel grants are currently matched to Oncogenic osteomalacia.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Oncogenic osteomalaciaForum →

No community posts yet. Be the first to share your experience with Oncogenic osteomalacia.

Start the conversation →

Latest news about Oncogenic osteomalacia

Disease timeline:

New recruiting trial: Al18F-NOTA-LM3 PET/CT in Patients With TIO

A new clinical trial is recruiting patients for Oncogenic osteomalacia

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Has the tumor been located, and if so, can it be surgically removed?,What imaging tests are available to help find the tumor if it hasn't been located yet?,Am I a candidate for burosumab (Crysvita) treatment?,How often will I need blood tests and follow-up imaging?,What are the risks of long-term phosphorus and vitamin D supplementation?,How will we know if the tumor comes back after surgery?,Are there clinical trials or specialized centers I should consider?

Common questions about Oncogenic osteomalacia

What is Oncogenic osteomalacia?

Oncogenic osteomalacia, also known as tumor-induced osteomalacia (TIO), is a rare condition where a usually small, slow-growing tumor produces too much of a hormone called fibroblast growth factor 23 (FGF23). This hormone tells the kidneys to get rid of phosphorus, a mineral that is essential for strong bones. When FGF23 levels are too high, phosphorus levels in the blood drop very low, causing the bones to become soft and weak — a condition called osteomalacia. The most common symptoms include bone pain, muscle weakness, and fractures that happen with little or no injury. Many patients also

How is Oncogenic osteomalacia inherited?

Oncogenic osteomalacia follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Oncogenic osteomalacia typically begin?

Typical onset of Oncogenic osteomalacia is adult. Age of onset can vary across affected individuals.

Are there clinical trials for Oncogenic osteomalacia?

Yes — 2 recruiting clinical trials are currently listed for Oncogenic osteomalacia on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Oncogenic osteomalacia?

21 specialists and care centers treating Oncogenic osteomalacia are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.

What treatment and support options exist for Oncogenic osteomalacia?

2 patient support programs are currently tracked on UniteRare for Oncogenic osteomalacia. See the treatments and support programs sections for copay assistance, eligibility, and contact details.