MAN1B1-CDG

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:397941E77.8
Who is this for?
Show terms as
16Specialists8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

MAN1B1-CDG (also known as MAN1B1-congenital disorder of glycosylation, or formerly congenital disorder of glycosylation type IIu) is a rare inherited metabolic condition that affects how the body processes sugars attached to proteins, a process called glycosylation. It is caused by changes (mutations) in the MAN1B1 gene, which provides instructions for making an enzyme involved in trimming sugar chains on proteins inside cells. When this enzyme does not work properly, proteins do not get the correct sugar modifications they need to function normally. The condition primarily affects the brain and development. Most individuals with MAN1B1-CDG have intellectual disability, which can range from mild to moderate. Delayed speech and motor development are common, and many children take longer to reach milestones like walking and talking. Some individuals may also have behavioral issues, obesity, and distinctive facial features. Seizures have been reported in some cases but are not universal. There is currently no cure for MAN1B1-CDG. Treatment is supportive and focuses on managing symptoms. This includes speech therapy, physical therapy, occupational therapy, and educational support to help individuals reach their full potential. Behavioral interventions and weight management strategies may also be important parts of care. Research into congenital disorders of glycosylation is ongoing, and scientists continue to work toward better understanding and potential therapies for this group of conditions.

Also known as:

Key symptoms:

Intellectual disability (mild to moderate)Delayed speech developmentDelayed motor milestones (late walking)Obesity or tendency to gain weight easilyBehavioral problemsDistinctive facial featuresLow muscle tone (feeling floppy as a baby)Seizures in some individualsShort stature in some casesDifficulty with fine motor skillsLearning difficultiesSocial and emotional challenges

Clinical phenotype terms (50)— hover any for plain English
Type II transferrin isoform profileHP:0012301
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for MAN1B1-CDG.

View clinical trials →

No actively recruiting trials found for MAN1B1-CDG at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the MAN1B1-CDG community →

Specialists

16 foundView all specialists →
YW
Yoshinao Wada
Specialist
2 MAN1B1-CDG publications
EP
Eva Morava-Kozicz, MD, PhD
ROCHESTER, MN
Specialist
PI on 7 active trials
CM
Christine Muti
Specialist
1 MAN1B1-CDG publication
CK
Cigdem Seher Kasapkara
Specialist
1 MAN1B1-CDG publication
SW
Samer Wehbi
Specialist
1 MAN1B1-CDG publication
BI
Bertrand Isidor
Specialist
1 MAN1B1-CDG publication
BC
Benjamin Cogne
Specialist
1 MAN1B1-CDG publication
ES
Emmanuelle Schmitt
Specialist
1 MAN1B1-CDG publication
CB
Céline Bonnet
Specialist
1 MAN1B1-CDG publication
BL
Bruno Leheup
Specialist
1 MAN1B1-CDG publication
FF
François Feillet
Specialist
1 MAN1B1-CDG publication
TD
Trost Detleft
Specialist
1 MAN1B1-CDG publication
SS
Soraya Sakhi
Specialist
1 MAN1B1-CDG publication
FF
François Fenaille
Specialist
1 MAN1B1-CDG publication
AB
Arnaud Bruneel
Specialist
1 MAN1B1-CDG publication
SC
Sophie Cholet
Specialist
1 MAN1B1-CDG publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to MAN1B1-CDG.

Search all travel grants →NORD Financial Assistance ↗

Community

Open MAN1B1-CDGForum →

No community posts yet. Be the first to share your experience with MAN1B1-CDG.

Start the conversation →

Latest news about MAN1B1-CDG

No recent news articles for MAN1B1-CDG.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What type of MAN1B1 mutations does my child have, and what do they mean for the expected course of the condition?,What therapies (speech, physical, occupational) should we start, and how often?,How should we monitor and manage weight gain?,Does my child need seizure monitoring or an EEG?,What educational supports and accommodations should we request at school?,Are there any clinical trials or research studies we could participate in?,What is the chance of having another child with this condition, and should we consider genetic counseling?

Common questions about MAN1B1-CDG

What is MAN1B1-CDG?

MAN1B1-CDG (also known as MAN1B1-congenital disorder of glycosylation, or formerly congenital disorder of glycosylation type IIu) is a rare inherited metabolic condition that affects how the body processes sugars attached to proteins, a process called glycosylation. It is caused by changes (mutations) in the MAN1B1 gene, which provides instructions for making an enzyme involved in trimming sugar chains on proteins inside cells. When this enzyme does not work properly, proteins do not get the correct sugar modifications they need to function normally. The condition primarily affects the brain

How is MAN1B1-CDG inherited?

MAN1B1-CDG follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does MAN1B1-CDG typically begin?

Typical onset of MAN1B1-CDG is infantile. Age of onset can vary across affected individuals.

Which specialists treat MAN1B1-CDG?

16 specialists and care centers treating MAN1B1-CDG are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.