Malformation syndrome with short stature

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ORPHA:139021
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64Specialists8Treatment centers

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Overview

Malformation syndrome with short stature is a broad term used in medical classification to describe a group of rare genetic conditions where a person is born with both physical malformations (structural differences in the body) and notably short stature (being significantly shorter than expected for their age and sex). These conditions are present from birth or become apparent in early childhood. The specific features can vary widely depending on the exact underlying cause, but commonly include skeletal abnormalities, distinctive facial features, and growth problems that lead to short stature. Some individuals may also have differences in their internal organs, such as the heart or kidneys, and some may experience learning difficulties or developmental delays. Because this is a grouping of related conditions rather than a single well-defined disease, the exact symptoms, severity, and outlook depend heavily on the specific diagnosis within this category. Treatment is generally supportive and tailored to each person's needs. This may include growth hormone therapy to help with height, orthopedic care for bone and joint problems, surgery to correct structural differences, physical therapy, and developmental support services. Regular monitoring by a team of specialists is important to address the various aspects of the condition as a child grows. Genetic testing has become increasingly important in identifying the specific cause, which can help guide treatment decisions and provide families with more accurate information about what to expect.

Key symptoms:

Short stature or growth failureSkeletal abnormalities such as abnormal bone shape or sizeDistinctive facial featuresDelayed growth milestonesJoint problems or limited range of motionDifferences in hand or finger structureSpine curvature or other spinal abnormalitiesHeart defects present at birthKidney or urinary tract differencesDevelopmental delays or learning difficultiesFeeding difficulties in infancyLow muscle toneHearing problemsVision problems

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Malformation syndrome with short stature.

View clinical trials →

No actively recruiting trials found for Malformation syndrome with short stature at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Malformation syndrome with short stature community →

Specialists

Showing 25 of 64View all specialists →
AM
Adeline Vanderver, MD
Los Angeles, California
Specialist

Rare Disease Specialist

PI on 4 active trials1 Malformation syndrome with short stature publication
RP
Régis Coutant, MD PhD
Rennes, Ile Et Vilaine
Specialist

Rare Disease Specialist

PI on 1 active trial
PM
Patricia Bretones, MD
Specialist
PI on 1 active trial
MM
Michael R Sargen, M.D.
PHILADELPHIA, PA
Specialist
PI on 2 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Malformation syndrome with short stature.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Malformation syndrome with short stature

No recent news articles for Malformation syndrome with short stature.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the specific diagnosis within this category, and has genetic testing identified the cause?,Would growth hormone therapy be appropriate for my child?,What specialists should we be seeing regularly, and how often?,Are there any heart, kidney, or other organ problems we need to monitor?,What is the expected growth pattern and adult height for my child?,Is this condition inherited, and should other family members be tested?,What early intervention services and therapies would benefit my child the most?

Common questions about Malformation syndrome with short stature

What is Malformation syndrome with short stature?

Malformation syndrome with short stature is a broad term used in medical classification to describe a group of rare genetic conditions where a person is born with both physical malformations (structural differences in the body) and notably short stature (being significantly shorter than expected for their age and sex). These conditions are present from birth or become apparent in early childhood. The specific features can vary widely depending on the exact underlying cause, but commonly include skeletal abnormalities, distinctive facial features, and growth problems that lead to short stature.

At what age does Malformation syndrome with short stature typically begin?

Typical onset of Malformation syndrome with short stature is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Malformation syndrome with short stature?

25 specialists and care centers treating Malformation syndrome with short stature are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.