Isolated focal palmoplantar keratoderma

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Overview

Isolated focal palmoplantar keratoderma is a rare skin condition where thick, hard patches of skin develop on specific pressure points of the palms of the hands and the soles of the feet. Unlike other forms of palmoplantar keratoderma that affect the entire palm or sole, this focal type causes thickened skin mainly in areas that experience the most friction or pressure, such as the balls of the feet, the heels, and the fingertips or base of the fingers. The condition is sometimes called focal nonepidermolytic palmoplantar keratoderma. The thickened skin patches, called calluses or keratoses, can be painful and may crack or fissure, making walking and manual tasks uncomfortable. The condition typically worsens with physical activity and repeated pressure on the affected areas. It usually appears during childhood or adolescence, often becoming more noticeable when a child begins walking more or engaging in sports. There is currently no cure for this condition. Treatment focuses on managing symptoms and improving comfort. This includes regular use of moisturizers, keratolytic creams (which help soften and remove thickened skin), careful trimming of calluses by a dermatologist or podiatrist, and wearing cushioned or custom-fitted footwear. In some cases, oral retinoids may be prescribed for more severe thickening. With proper skin care and management, most people with this condition can lead active, normal lives.

Also known as:

Key symptoms:

Thick, hard patches of skin on the palms of the handsThick, hard patches of skin on the soles of the feetPainful calluses on pressure points of the feetCalluses on the balls of the feet and heelsThickened skin at the base of the fingersCracking or fissuring of thickened skinPain when walking or standing for long periodsWorsening of calluses with physical activityDiscomfort when gripping objectsYellowish or waxy appearance of thickened skin patches

Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Isolated focal palmoplantar keratoderma.

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No actively recruiting trials found for Isolated focal palmoplantar keratoderma at this time.

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No specialists are currently listed for Isolated focal palmoplantar keratoderma.

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Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Isolated focal palmoplantar keratoderma.

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Community

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Caregiver Resources

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Questions for your doctor

Bring these to your next appointment

  • Q1.What type of palmoplantar keratoderma does my child have, and how was it confirmed?,Should we pursue genetic testing to identify the specific gene involved?,What is the best daily skin care routine to manage the thickened skin?,Are there prescription creams or medications that could help reduce the calluses?,What type of footwear or insoles do you recommend?,How often should we schedule follow-up visits for callus management?,Are there any new treatments or clinical trials we should know about?

Common questions about Isolated focal palmoplantar keratoderma

What is Isolated focal palmoplantar keratoderma?

Isolated focal palmoplantar keratoderma is a rare skin condition where thick, hard patches of skin develop on specific pressure points of the palms of the hands and the soles of the feet. Unlike other forms of palmoplantar keratoderma that affect the entire palm or sole, this focal type causes thickened skin mainly in areas that experience the most friction or pressure, such as the balls of the feet, the heels, and the fingertips or base of the fingers. The condition is sometimes called focal nonepidermolytic palmoplantar keratoderma. The thickened skin patches, called calluses or keratoses,

How is Isolated focal palmoplantar keratoderma inherited?

Isolated focal palmoplantar keratoderma follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Isolated focal palmoplantar keratoderma typically begin?

Typical onset of Isolated focal palmoplantar keratoderma is childhood. Age of onset can vary across affected individuals.