Idiopathic posterior uveitis

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ORPHA:280917H30.9
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1Specialists8Treatment centers

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Overview

Idiopathic posterior uveitis is an inflammatory condition that affects the back part of the eye, specifically the choroid (a layer of blood vessels behind the retina) and sometimes the retina itself. The word "idiopathic" means that no specific cause can be identified, even after thorough testing. This sets it apart from posterior uveitis caused by infections, autoimmune diseases, or other known conditions. The inflammation can lead to blurred vision, floaters (small spots or threads drifting across your field of vision), and sometimes flashes of light. In more severe cases, it can cause significant vision loss if not treated promptly. Some people experience mild symptoms that come and go, while others have chronic inflammation that requires long-term management. Treatment typically focuses on controlling the inflammation and preventing damage to the eye. Corticosteroids, given as eye drops, injections around or inside the eye, or oral tablets, are the most common first-line therapy. For patients who need long-term treatment or cannot tolerate steroids, immunosuppressive medications may be used. Early diagnosis and consistent follow-up with an eye specialist are essential to preserving vision and preventing complications such as macular edema, cataracts, or glaucoma.

Key symptoms:

Blurred or hazy visionFloaters (spots or threads in your vision)Flashes of lightGradual loss of visionDifficulty seeing in dim lightDistorted visionBlind spots or dark areas in your visual fieldEye redness (less common than in front-of-eye inflammation)Sensitivity to lightEye pain or discomfort (mild in many cases)

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Idiopathic posterior uveitis.

View clinical trials →

No actively recruiting trials found for Idiopathic posterior uveitis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Idiopathic posterior uveitis community →

Specialists

1 foundView all specialists →

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Idiopathic posterior uveitis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Idiopathic posterior uveitis

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What part of my eye is affected, and how severe is the inflammation right now?,Have all possible causes been ruled out, and what tests were done?,What treatment do you recommend, and what are the potential side effects?,How often will I need follow-up appointments and eye exams?,What are the warning signs that I should come back sooner than my next scheduled visit?,Is there a risk of permanent vision loss, and what can we do to minimize it?,Should I see any other specialists, such as a rheumatologist?

Common questions about Idiopathic posterior uveitis

What is Idiopathic posterior uveitis?

Idiopathic posterior uveitis is an inflammatory condition that affects the back part of the eye, specifically the choroid (a layer of blood vessels behind the retina) and sometimes the retina itself. The word "idiopathic" means that no specific cause can be identified, even after thorough testing. This sets it apart from posterior uveitis caused by infections, autoimmune diseases, or other known conditions. The inflammation can lead to blurred vision, floaters (small spots or threads drifting across your field of vision), and sometimes flashes of light. In more severe cases, it can cause sign

How is Idiopathic posterior uveitis inherited?

Idiopathic posterior uveitis follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Idiopathic posterior uveitis typically begin?

Typical onset of Idiopathic posterior uveitis is adult. Age of onset can vary across affected individuals.

Which specialists treat Idiopathic posterior uveitis?

1 specialists and care centers treating Idiopathic posterior uveitis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.