Graham Little-Piccardi-Lassueur syndrome

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Overview

Graham Little-Piccardi-Lassueur syndrome (also called Graham Little syndrome or GLPS) is a rare skin and hair condition that belongs to a group of disorders known as lichen planopilaris. It causes permanent hair loss in three different areas of the body at the same time: the scalp, the armpits, and the pubic region. The hair loss on the scalp is scarring, meaning the hair follicles are destroyed and hair cannot grow back in those areas. Along with hair loss, many people develop small, rough, spiny bumps on the skin of the body and limbs — a pattern called keratosis pilaris-like changes. The scalp may also show redness, scaling, and irritation around the remaining hair follicles. This condition most often affects middle-aged women, though men can also be diagnosed. The exact cause is not fully understood, but it is thought to involve the immune system mistakenly attacking hair follicles, leading to inflammation and scarring. Some cases have been linked to certain triggers such as medications, infections, or other autoimmune conditions. There is currently no cure for Graham Little syndrome. Treatment focuses on slowing down the hair loss and reducing inflammation and discomfort. Options include topical and oral corticosteroids, antimalarial drugs like hydroxychloroquine, and other immune-modifying medications. Early treatment is important because once hair follicles are scarred, the hair loss in those areas is permanent.

Also known as:

Key symptoms:

Permanent, scarring hair loss on the scalpHair loss in the armpits (axillary hair loss)Hair loss in the pubic areaSmall, rough, spiny skin bumps on the body and limbs (follicular papules)Redness and scaling around hair follicles on the scalpItching or burning sensation on the scalpPatchy bald areas on the scalp that may slowly grow largerThinning or complete loss of eyebrow or eyelash hair in some casesSkin irritation or tenderness in affected areas

Clinical phenotype terms (7)— hover any for plain English
Sparse axillary hairHP:0002215Sparse pubic hairHP:0002225Perifollicular hyperkeratosisHP:0007468LichenificationHP:0100725
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Graham Little-Piccardi-Lassueur syndrome.

View clinical trials →

No actively recruiting trials found for Graham Little-Piccardi-Lassueur syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Graham Little-Piccardi-Lassueur syndrome community →

No specialists are currently listed for Graham Little-Piccardi-Lassueur syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Graham Little-Piccardi-Lassueur syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Graham Little-Piccardi-Lassueur syndrome

Disease timeline:

New recruiting trial: Nemolizumab to Treat Lichen Planopilaris, a Noncontrolled, Prospective, Pilot Study.

A new clinical trial is recruiting patients for Graham Little-Piccardi-Lassueur syndrome

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How quickly is my hair loss likely to progress, and what can we do to slow it down?,Which treatment do you recommend for me first, and how long before I might see results?,Are there any tests I should have to check for related autoimmune conditions?,What are the side effects of hydroxychloroquine, and do I need regular eye exams while taking it?,Is there any chance the hair loss could be reversed, or is it permanent in the areas already affected?,Are there any clinical trials or newer treatments I should know about?,Can you refer me to a counselor or support group for people dealing with hair loss?

Common questions about Graham Little-Piccardi-Lassueur syndrome

What is Graham Little-Piccardi-Lassueur syndrome?

Graham Little-Piccardi-Lassueur syndrome (also called Graham Little syndrome or GLPS) is a rare skin and hair condition that belongs to a group of disorders known as lichen planopilaris. It causes permanent hair loss in three different areas of the body at the same time: the scalp, the armpits, and the pubic region. The hair loss on the scalp is scarring, meaning the hair follicles are destroyed and hair cannot grow back in those areas. Along with hair loss, many people develop small, rough, spiny bumps on the skin of the body and limbs — a pattern called keratosis pilaris-like changes. The sc

How is Graham Little-Piccardi-Lassueur syndrome inherited?

Graham Little-Piccardi-Lassueur syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Graham Little-Piccardi-Lassueur syndrome typically begin?

Typical onset of Graham Little-Piccardi-Lassueur syndrome is adult. Age of onset can vary across affected individuals.