Focal palmoplantar keratoderma

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Overview

Focal palmoplantar keratoderma (also called focal keratoderma of the palms and soles) is a rare inherited skin condition in which thick, hard patches of skin develop on specific pressure points of the palms of the hands and the soles of the feet. Unlike diffuse forms of palmoplantar keratoderma that affect the entire palm or sole, the focal type causes thickened skin (calluses or callus-like plaques) mainly in areas that experience the most friction or pressure, such as the balls of the feet, the heels, and the fingertips or areas of the palms used for gripping. These thickened patches can be painful, may crack or fissure, and can make walking or using the hands uncomfortable. The condition is usually caused by mutations in genes that produce keratin proteins, which are essential building blocks of the outer layer of skin. Symptoms typically begin in childhood or adolescence and tend to worsen with physical activity or manual labor. In some forms, the nails may also be affected, becoming thickened or abnormally shaped. The condition is lifelong, but it is not life-threatening. Treatment focuses on managing symptoms and improving comfort. This includes regular use of moisturizers, keratolytic creams (which help soften and remove thickened skin), careful trimming of calluses by a dermatologist or podiatrist, and wearing well-cushioned footwear. In more severe cases, oral retinoids may be prescribed to help reduce skin thickening. There is currently no cure, but with consistent care, most people can manage their symptoms effectively.

Also known as:

Key symptoms:

Thick, hard patches of skin on the palmsThick, hard patches of skin on the soles of the feetPainful calluses at pressure points on the feetCracking or fissuring of thickened skinDiscomfort or pain when walkingDifficulty gripping objects due to thickened palm skinCalluses that keep coming back after removalThickened or abnormal toenails or fingernailsBlisters that may form under thickened skinRedness around thickened skin areasWorsening of symptoms with physical activity or manual work

Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Focal palmoplantar keratoderma.

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No actively recruiting trials found for Focal palmoplantar keratoderma at this time.

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No specialists are currently listed for Focal palmoplantar keratoderma.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Focal palmoplantar keratoderma.

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Community

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Caregiver Resources

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Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific type of palmoplantar keratoderma do I have, and which gene is involved?,What is the best daily skin care routine to manage my symptoms?,Should I see a podiatrist regularly for callus management?,Are oral retinoids appropriate for my case, and what are the risks?,Is genetic testing recommended for my family members?,Are there any clinical trials or new treatments being studied for this condition?,What types of shoes or insoles do you recommend to reduce pain?

Common questions about Focal palmoplantar keratoderma

What is Focal palmoplantar keratoderma?

Focal palmoplantar keratoderma (also called focal keratoderma of the palms and soles) is a rare inherited skin condition in which thick, hard patches of skin develop on specific pressure points of the palms of the hands and the soles of the feet. Unlike diffuse forms of palmoplantar keratoderma that affect the entire palm or sole, the focal type causes thickened skin (calluses or callus-like plaques) mainly in areas that experience the most friction or pressure, such as the balls of the feet, the heels, and the fingertips or areas of the palms used for gripping. These thickened patches can be

How is Focal palmoplantar keratoderma inherited?

Focal palmoplantar keratoderma follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Focal palmoplantar keratoderma typically begin?

Typical onset of Focal palmoplantar keratoderma is childhood. Age of onset can vary across affected individuals.