Fetal lung interstitial tumor

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Overview

Fetal lung interstitial tumor (FLIT) is an extremely rare benign lung tumor that develops in babies before or shortly after birth. It is a type of congenital lung lesion, meaning it forms during fetal development. FLIT was first described in 2010 and is classified as a distinct entity among pediatric lung tumors. The tumor arises from the tissue between the air sacs (interstitium) of the lung and is made up of immature lung cells that resemble fetal lung tissue at a certain stage of development. Babies with FLIT may present with breathing difficulties at birth or shortly after, and the tumor is sometimes detected on prenatal ultrasound as a mass in the chest. In some cases, the tumor can cause the affected part of the lung to become enlarged. The mass may compress surrounding lung tissue and affect normal breathing. The primary treatment for FLIT is surgical removal of the affected portion of the lung (lobectomy or wedge resection). The prognosis after complete surgical removal is generally excellent, and the tumor is considered benign with no known tendency to spread to other parts of the body or recur after complete removal. Because this tumor is so rare, with only a small number of cases reported in the medical literature, knowledge about it continues to evolve as more cases are identified and studied.

Also known as:

Key symptoms:

Breathing difficulty at birth or shortly afterRapid breathingLow oxygen levelsA mass or lump seen on chest imagingEnlarged area of the lungRespiratory distress in the newborn periodPrenatal detection of a chest mass on ultrasoundDifficulty feeding due to breathing problems

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Fetal lung interstitial tumor.

View clinical trials →

No actively recruiting trials found for Fetal lung interstitial tumor at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Fetal lung interstitial tumor community →

No specialists are currently listed for Fetal lung interstitial tumor.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Fetal lung interstitial tumor.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Fetal lung interstitial tumor

1 articles
ResearchPUBMEDApr 22, 2026
Linear Interstitial Keratitis - A Retrospective Chart Review of a Rare Entity.
Linear interstitial keratitis (LIK) is a very rare eye condition where a thin line of cloudiness forms in the clear part of the eye (the cornea). This study loo
See all news about Fetal lung interstitial tumor

Caregiver Resources

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What part of my baby's lung is affected, and how much tissue needs to be removed?,What are the risks of the surgery, and what is the expected recovery time?,Will my baby need any breathing support before or after surgery?,How will losing part of the lung affect my child's long-term breathing and physical activity?,How often will my child need follow-up imaging after surgery?,Is there any chance this tumor could come back or be related to other conditions?,Are there any signs or symptoms I should watch for at home after discharge?

Common questions about Fetal lung interstitial tumor

What is Fetal lung interstitial tumor?

Fetal lung interstitial tumor (FLIT) is an extremely rare benign lung tumor that develops in babies before or shortly after birth. It is a type of congenital lung lesion, meaning it forms during fetal development. FLIT was first described in 2010 and is classified as a distinct entity among pediatric lung tumors. The tumor arises from the tissue between the air sacs (interstitium) of the lung and is made up of immature lung cells that resemble fetal lung tissue at a certain stage of development. Babies with FLIT may present with breathing difficulties at birth or shortly after, and the tumor

How is Fetal lung interstitial tumor inherited?

Fetal lung interstitial tumor follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Fetal lung interstitial tumor typically begin?

Typical onset of Fetal lung interstitial tumor is neonatal. Age of onset can vary across affected individuals.