Feingold syndrome type 1

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ORPHA:391641OMIM:164280Q87.8
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15Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Feingold syndrome type 1 (also called oculodigitoesophagoduodenal syndrome or ODED syndrome) is a rare genetic condition that affects several parts of the body. It is caused by changes (mutations) in the MYCN gene, which plays an important role in how the body develops before birth. People with this condition are typically born with certain physical features, including short fingers and toes (brachydactyly), especially shortening of the second and fifth fingers, and the fingers or toes may be joined together (syndactyly). One of the most medically significant features is atresia (blockage) of parts of the digestive tract, most commonly the esophagus (the tube connecting the mouth to the stomach) or the duodenum (the first part of the small intestine). These blockages often require surgery shortly after birth. Many individuals with Feingold syndrome type 1 also have a smaller-than-average head size (microcephaly) and mild to moderate learning difficulties or intellectual disability, though intelligence can be normal. Some people may have facial features such as a short space between the nose and upper lip, small ears, or a narrow opening of the eyelids. Hearing loss and kidney abnormalities can also occur. The severity of symptoms varies widely, even among members of the same family. Treatment focuses on managing specific symptoms, particularly surgical correction of digestive tract blockages in newborns, and supportive therapies for learning and developmental needs. With appropriate medical care, many individuals lead fulfilling lives.

Also known as:

Key symptoms:

Short fingers and toes (brachydactyly)Fingers or toes that are joined together (syndactyly)Blockage of the esophagus (esophageal atresia)Blockage of the duodenum (duodenal atresia)Smaller-than-average head size (microcephaly)Mild to moderate learning difficultiesShort statureSmall earsNarrow eye openingsShort space between nose and upper lipHearing lossKidney abnormalitiesFeeding difficulties in infancySpeech delays

Clinical phenotype terms (35)— hover any for plain English
Gastrointestinal atresiaHP:0002589Short middle phalanx of fingerHP:0005819Esophageal atresiaHP:0002032Short middle phalanx of the 5th fingerHP:00042202-3 toe syndactylyHP:00046914-5 toe syndactylyHP:0004692Short middle phalanx of the 2nd fingerHP:0009577Short palpebral fissureHP:0012745
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Feingold syndrome type 1.

View clinical trials →

No actively recruiting trials found for Feingold syndrome type 1 at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Feingold syndrome type 1 community →

Specialists

15 foundView all specialists →
BR
Bérénice Roy-Doray
Specialist
1 Feingold syndrome type 1 publication
PM
Pauline Marzin
Specialist
1 Feingold syndrome type 1 publication
MS
Marta Spondenkiewicz
Specialist
1 Feingold syndrome type 1 publication
GM
Godelieve Morel
Specialist
1 Feingold syndrome type 1 publication
FP
Frédérique Payet
Specialist
1 Feingold syndrome type 1 publication
MR
Mathilde Remy
Specialist
1 Feingold syndrome type 1 publication
FF
Fanny Ferroul
Specialist
1 Feingold syndrome type 1 publication
GL
Gaëlle Leterme
Specialist
1 Feingold syndrome type 1 publication
KM
Kheira Mezouaghi
Specialist
1 Feingold syndrome type 1 publication
MK
Marie Kieffer-Traversier
Specialist
1 Feingold syndrome type 1 publication
TC
Tristan Celse
Specialist
1 Feingold syndrome type 1 publication
JD
Jessica Dospeux
Specialist
1 Feingold syndrome type 1 publication
TH
Thomas Huby
Specialist
1 Feingold syndrome type 1 publication
LS
Laetitia Sennsfelder
Specialist
1 Feingold syndrome type 1 publication
SS
Sarah Snanoudj
Specialist
1 Feingold syndrome type 1 publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Feingold syndrome type 1.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Feingold syndrome type 1

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Does my child have any digestive tract blockages that need surgery?,How will we monitor my child's development and learning over time?,Should my child have hearing and kidney tests, and how often?,What therapies (speech, occupational, educational) should we start and when?,What is the chance of passing this condition to future children?,Are there any clinical trials or research studies we should know about?,What specialists should be part of my child's care team?

Common questions about Feingold syndrome type 1

What is Feingold syndrome type 1?

Feingold syndrome type 1 (also called oculodigitoesophagoduodenal syndrome or ODED syndrome) is a rare genetic condition that affects several parts of the body. It is caused by changes (mutations) in the MYCN gene, which plays an important role in how the body develops before birth. People with this condition are typically born with certain physical features, including short fingers and toes (brachydactyly), especially shortening of the second and fifth fingers, and the fingers or toes may be joined together (syndactyly). One of the most medically significant features is atresia (blockage) of

How is Feingold syndrome type 1 inherited?

Feingold syndrome type 1 follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Feingold syndrome type 1 typically begin?

Typical onset of Feingold syndrome type 1 is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Feingold syndrome type 1?

15 specialists and care centers treating Feingold syndrome type 1 are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.