Congenital genu flexum

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:295232Q68.2
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Congenital genu flexum, also known as congenital knee flexion contracture or congenital flexion deformity of the knee, is a rare condition present at birth in which one or both knees are bent (flexed) and cannot be fully straightened. The knee joint is essentially locked in a bent position due to shortening or tightness of the soft tissues around the knee, including muscles, tendons, and the joint capsule. This condition can range from mild, where the knee is only slightly bent, to severe, where the knee is significantly contracted and the leg cannot extend at all. Babies born with this condition may have difficulty with leg positioning, and as they grow, walking and other movements can be affected if the contracture is not treated. In some cases, congenital genu flexum occurs on its own (isolated), while in other cases it may be associated with other birth defects or conditions such as arthrogryposis, breech positioning in the womb, or neuromuscular disorders. Treatment depends on the severity of the contracture. Mild cases may respond well to physical therapy, gentle stretching exercises, and serial casting, where casts are applied and gradually adjusted to straighten the knee over time. More severe cases may require surgical intervention to release tight tissues and allow the knee to extend properly. Early treatment generally leads to better outcomes, and many children can achieve good knee function with appropriate care.

Key symptoms:

Knee stuck in a bent position at birthInability to fully straighten the kneeStiffness in the knee jointDifficulty with leg movementAbnormal leg positioningDelayed walking milestonesLimping or unusual walking patternLeg length difference if only one knee is affectedMuscle tightness behind the kneeDifficulty standing uprightReduced range of motion in the knee

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Congenital genu flexum.

View clinical trials →

No actively recruiting trials found for Congenital genu flexum at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Congenital genu flexum community →

No specialists are currently listed for Congenital genu flexum.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Congenital genu flexum.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Congenital genu flexumForum →

No community posts yet. Be the first to share your experience with Congenital genu flexum.

Start the conversation →

Latest news about Congenital genu flexum

No recent news articles for Congenital genu flexum.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is my child's knee contracture, and what is the expected outcome with treatment?,Is this an isolated condition, or could it be part of a larger syndrome that needs further testing?,What treatment approach do you recommend — physical therapy, casting, surgery, or a combination?,How long will treatment take, and how many follow-up visits will be needed?,What can I do at home to help improve my child's knee range of motion?,Is there a chance the contracture could come back after treatment?,Will my child be able to walk and participate in normal activities as they grow?

Common questions about Congenital genu flexum

What is Congenital genu flexum?

Congenital genu flexum, also known as congenital knee flexion contracture or congenital flexion deformity of the knee, is a rare condition present at birth in which one or both knees are bent (flexed) and cannot be fully straightened. The knee joint is essentially locked in a bent position due to shortening or tightness of the soft tissues around the knee, including muscles, tendons, and the joint capsule. This condition can range from mild, where the knee is only slightly bent, to severe, where the knee is significantly contracted and the leg cannot extend at all. Babies born with this condi

At what age does Congenital genu flexum typically begin?

Typical onset of Congenital genu flexum is neonatal. Age of onset can vary across affected individuals.