Congenital knee dislocation

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Overview

Congenital knee dislocation, also known as congenital dislocation of the knee or congenital genu recurvatum, is a rare condition present at birth in which the knee joint is displaced or bent backward (hyperextended). In a normal knee, the shinbone (tibia) sits properly beneath the thighbone (femur). In this condition, the tibia is shifted forward and the knee may be locked in a hyperextended or even fully dislocated position. This can range from mild hyperextension to complete dislocation where the bones are entirely out of alignment. Babies born with this condition typically have one or both knees that appear bent the wrong way. The knee may feel stiff and resist being bent into a normal position. Congenital knee dislocation can occur on its own (isolated) or alongside other conditions such as hip dysplasia, clubfoot, or genetic syndromes like Larsen syndrome or arthrogryposis. About 40-80% of affected babies also have developmental dysplasia of the hip. Treatment usually begins shortly after birth. In many mild to moderate cases, gentle serial casting or bracing can gradually bring the knee into a normal position. Physical therapy plays an important role in maintaining range of motion. In more severe cases or when conservative treatment does not work, surgery may be needed to release tight structures around the knee and reposition the joint. With early and appropriate treatment, many children achieve good knee function and can walk normally. Delayed treatment can lead to long-term stiffness and difficulty walking.

Key symptoms:

Knee bent backward at birth (hyperextension)Inability to bend the knee normallyStiff knee jointVisible deformity of the knee at birthSkin creases or folds on the front of the kneeShortened quadriceps muscleLimited range of motion in the kneeDifficulty with crawling or walking milestonesHip dislocation in the same or opposite legClubfoot or other foot deformitiesMuscle tightness around the knee

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Congenital knee dislocation.

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No actively recruiting trials found for Congenital knee dislocation at this time.

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No specialists are currently listed for Congenital knee dislocation.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Congenital knee dislocation.

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Community

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Latest news about Congenital knee dislocation

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

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Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is my baby's knee dislocation, and what grade or classification is it?,Will serial casting be enough, or is surgery likely to be needed?,Has my baby been checked for hip dysplasia or other associated conditions?,Should we see a geneticist to rule out an underlying syndrome?,What physical therapy will my baby need, and how often?,What is the expected long-term outcome for my child's knee function?,Are there any signs I should watch for at home that would require urgent medical attention?

Common questions about Congenital knee dislocation

What is Congenital knee dislocation?

Congenital knee dislocation, also known as congenital dislocation of the knee or congenital genu recurvatum, is a rare condition present at birth in which the knee joint is displaced or bent backward (hyperextended). In a normal knee, the shinbone (tibia) sits properly beneath the thighbone (femur). In this condition, the tibia is shifted forward and the knee may be locked in a hyperextended or even fully dislocated position. This can range from mild hyperextension to complete dislocation where the bones are entirely out of alignment. Babies born with this condition typically have one or both

At what age does Congenital knee dislocation typically begin?

Typical onset of Congenital knee dislocation is neonatal. Age of onset can vary across affected individuals.