Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome

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ORPHA:508476OMIM:621063Q87.8
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8Treatment centers

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Overview

Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome is a very rare condition that affects multiple parts of the body from birth. It is sometimes referred to by its Orphanet code ORPHA:508476. This syndrome combines several features: a cleft lip and/or palate (a gap or split in the upper lip and the roof of the mouth), unusual facial features, a heart defect that is present at birth, and hearing loss. Because these problems appear together as a group, doctors call this a 'syndrome.' The cleft lip and palate can make feeding, speaking, and breathing more difficult for babies and young children. The heart defect varies from person to person and may range from mild to more serious, sometimes requiring surgery. Hearing loss can affect speech development and learning if not identified and treated early. The unusual facial features are typically noticed at birth or during a prenatal ultrasound. Treatment focuses on managing each feature separately. Surgical repair of the cleft lip and palate is usually done in stages during infancy and early childhood. Heart defects are evaluated by a pediatric cardiologist and treated based on their type and severity. Hearing aids or other devices can help with hearing loss. A team of specialists working together gives children the best chance at a good quality of life.

Also known as:

Key symptoms:

Cleft lip (a split or gap in the upper lip)Cleft palate (a gap in the roof of the mouth)Unusual facial features such as widely spaced eyes or a small jawHeart defect present from birthHearing loss (may be partial or complete)Feeding difficulties in infancySpeech and language delaysPossible breathing difficulties

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome.

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No actively recruiting trials found for Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome at this time.

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No specialists are currently listed for Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome.

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Community

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Latest news about Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome

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Caregiver Resources

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Questions for your doctor

Bring these to your next appointment

  • Q1.What specific heart defect does my child have, and what treatment does it need?,What type and degree of hearing loss is present, and what is the best hearing device for my child?,What is the surgical plan for the cleft lip and palate, and what should I expect at each stage?,Should we have genetic testing, and what might it tell us about the cause and recurrence risk?,What early therapies — such as speech therapy or feeding support — should we start right away?,Are there any activity restrictions because of the heart condition?,What signs or symptoms should prompt me to seek emergency care?

Common questions about Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome

What is Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome?

Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome is a very rare condition that affects multiple parts of the body from birth. It is sometimes referred to by its Orphanet code ORPHA:508476. This syndrome combines several features: a cleft lip and/or palate (a gap or split in the upper lip and the roof of the mouth), unusual facial features, a heart defect that is present at birth, and hearing loss. Because these problems appear together as a group, doctors call this a 'syndrome.' The cleft lip and palate can make feeding, speaking, and breathing more

At what age does Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome typically begin?

Typical onset of Cleft lip and palate-craniofacial dysmorphism-congenital heart defect-hearing loss syndrome is neonatal. Age of onset can vary across affected individuals.