Van der Woude syndrome

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ORPHA:888OMIM:119300Q38.0
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13Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Van der Woude syndrome (VWS), also known as lip pit syndrome, is the most common syndromic form of cleft lip and/or cleft palate. It is a congenital craniofacial disorder primarily caused by mutations in the IRF6 gene (interferon regulatory factor 6) on chromosome 1q32-q41. The condition is characterized by the combination of lower lip pits (paramedian sinuses or fistulae of the lower lip), cleft lip with or without cleft palate, and/or cleft palate alone. Lower lip pits are the most distinctive feature and are present in approximately 80% of affected individuals. Hypodontia (missing teeth) is also a commonly associated finding. The syndrome primarily affects the craniofacial system, particularly the lips, palate, and dentition. The lower lip pits appear as small depressions or mounds on the vermilion border of the lower lip, often bilateral and symmetrical, and may produce mucous secretions. Cleft lip and/or cleft palate occurs in approximately 50% of affected individuals. A submucous cleft palate or bifid uvula may also be present. The expressivity of the syndrome is highly variable, even within the same family — some individuals may have only lip pits, while others may have a complete cleft lip and palate. Rarely, limb anomalies or other features may be present, which may suggest the allelic condition popliteal pterygium syndrome. Treatment for Van der Woude syndrome is primarily surgical and supportive. Cleft lip and palate are repaired through standard surgical approaches, typically in infancy and early childhood. Lip pits may be surgically excised for cosmetic reasons or if they cause recurrent drainage or infection. Dental anomalies may require orthodontic treatment or dental prosthetics. Speech therapy may be needed for individuals with palatal clefts. Genetic counseling is recommended for affected families given the autosomal dominant inheritance pattern. With appropriate multidisciplinary care, individuals with VWS generally have an excellent prognosis and normal life expectancy.

Also known as:

Clinical phenotype terms— hover any for plain English:

Lip pitHP:0100267Lower lip pitHP:0000196Abnormal salivary gland morphologyHP:0010286AnkyloglossiaHP:0010296
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

FDA & Trial Timeline

7 events
Dec 2025Retention of Pits and Fissure Sealants on Non Carious vs Initial Carious Enamel Lesions in Posterior Teeth

Foundation University Islamabad

TrialNOT YET RECRUITING
Sep 2025Comparison of the Efficacy of Three Preventive Methods to Reduce the Incidence of Coronal Caries in Schoolchildren

Universidad Nacional Autonoma de Mexico — NA

TrialRECRUITING
Aug 2025Wear Resistance Of Bioactive With And Without Etching Vs. Conventional Resin-Based Fissure Sealants

Cairo University — NA

TrialNOT YET RECRUITING
Mar 2025Evaluation of the Clinical Success of Hydrophilic Fissure Sealants

Afyonkarahisar Health Sciences University — NA

TrialACTIVE NOT RECRUITING
Jan 2025Resin Infiltrate As Pit and Fissure Sealant in Permanent Molars

Tanta University — PHASE4

TrialNOT YET RECRUITING
Nov 2024Clinical Evaluation of Two Different Pit and Fissure Sealants

Baskent University — NA

TrialRECRUITING
Aug 2024Clinical Efficiency of Bioactive Pit and Fissure Sealant

Cairo University — PHASE2

TrialNOT YET RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Van der Woude syndrome.

View clinical trials →

No actively recruiting trials found for Van der Woude syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Van der Woude syndrome community →

Specialists

13 foundView all specialists →
KD
Kelly Moreira, DDS
Specialist
PI on 1 active trial
KP
Kamila Kantovitz, Phd
Specialist
PI on 1 active trial
SL
Simge POLAT, Lecturer
Specialist
PI on 1 active trial1 Van der Woude syndrome publication
AD
Ana Carolina G Luciano, DDS
Specialist
PI on 1 active trial
KS
Kelly MS Moreira, MS Student
SUNRISE, FL
Specialist
PI on 1 active trial
RS
Raquel V Rodrigues, PhD Student
NEWARK, NJ
Specialist
PI on 1 active trial
MP
Michèle Muller-Bolla, Pr
Specialist
PI on 1 active trial
JC
Juliana Camargo
Specialist
PI on 1 active trial4 Van der Woude syndrome publications
BP
Baoying Liu, PhD
Specialist
PI on 1 active trial
EA
Eman Abouauf, Ass.prof
Specialist
PI on 1 active trial
KM
Kelly Moreira
SUNRISE, FL
Specialist
PI on 1 active trial2 Van der Woude syndrome publications
JP
Jose Carlos P Imparato, PhD
Specialist
PI on 1 active trial
MP
Martin Clodi, MD, Associate Professor
Specialist
PI on 1 active trial1 Van der Woude syndrome publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Van der Woude syndrome.

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Community

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Latest news about Van der Woude syndrome

Disease timeline:

New recruiting trial: Clinical Evaluation of Two Different Pit and Fissure Sealants

A new clinical trial is recruiting patients for Van der Woude syndrome

New recruiting trial: Comparison of the Efficacy of Three Preventive Methods to Reduce the Incidence of Coronal Caries in Schoolchildren

A new clinical trial is recruiting patients for Van der Woude syndrome

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Common questions about Van der Woude syndrome

What is Van der Woude syndrome?

Van der Woude syndrome (VWS), also known as lip pit syndrome, is the most common syndromic form of cleft lip and/or cleft palate. It is a congenital craniofacial disorder primarily caused by mutations in the IRF6 gene (interferon regulatory factor 6) on chromosome 1q32-q41. The condition is characterized by the combination of lower lip pits (paramedian sinuses or fistulae of the lower lip), cleft lip with or without cleft palate, and/or cleft palate alone. Lower lip pits are the most distinctive feature and are present in approximately 80% of affected individuals. Hypodontia (missing teeth) is

How is Van der Woude syndrome inherited?

Van der Woude syndrome follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Van der Woude syndrome typically begin?

Typical onset of Van der Woude syndrome is neonatal. Age of onset can vary across affected individuals.

Which specialists treat Van der Woude syndrome?

13 specialists and care centers treating Van der Woude syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.