Classic neuroendocrine tumor of appendix

Classic neuroendocrine tumor of the appendix, also known as a carcinoid tumor of the appendix, is a slow-growing tumor that develops from special hormone-producing cells (neuroendocrine cells) in the lining of the appendix. The appendix is a small, finger-shaped pouch attached to the large intestine. These tumors are the most common type of tumor found in the appendix and are often discovered by chance when someone has surgery to remove their appendix for other reasons, such as appendicitis. Most of these tumors are small (less than 2 centimeters) and behave in a benign or low-grade manner, meaning they grow slowly and rarely spread to other parts of the body. When the tumor is small and confined to the appendix, simply removing the appendix (appendectomy) is usually all the treatment that is needed. Larger tumors or those that have grown into deeper layers of the appendix wall may require more extensive surgery, such as removal of part of the colon (right hemicolectomy). In rare cases where the tumor has spread, additional treatments such as somatostatin analogs or other targeted therapies may be considered. Many people with this condition have no symptoms at all. When symptoms do occur, they may mimic appendicitis with right lower abdominal pain. Rarely, larger or advanced tumors can cause carcinoid syndrome, which involves flushing, diarrhea, and wheezing, though this is uncommon with appendiceal tumors. The overall outlook for most patients is excellent, with very high survival rates after appropriate surgical treatment.

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Bring these to your next appointment

• Q1.What was the exact size of my tumor, and was it completely removed?,Do I need any additional surgery beyond the appendectomy?,What was the grade of my tumor, and what does that mean for my outlook?,How often will I need follow-up appointments, blood tests, or imaging scans?,Are there any symptoms I should watch for that might suggest the tumor has come back?,Should I be referred to a specialist center with experience in neuroendocrine tumors?,Is there anything I need to change about my diet or lifestyle after treatment?

Common questions about Classic neuroendocrine tumor of appendix