Xq12-q13.3 duplication syndrome

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ORPHA:314389Q99.8
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Overview

Xq12-q13.3 duplication syndrome is a very rare genetic condition caused by having an extra copy of a specific region on the X chromosome, between positions Xq12 and Xq13.3. This duplication means that certain genes in this region are present in more copies than usual, which can disrupt normal development. The condition primarily affects males more severely than females, since males have only one X chromosome and the extra genetic material has a greater impact. People with this syndrome typically show developmental delays, intellectual disability, and various physical features that may be noticeable from early childhood. Common findings can include low muscle tone (hypotonia), feeding difficulties in infancy, speech and language delays, and distinctive facial features. Some individuals may also experience seizures or behavioral challenges. The severity of symptoms can vary depending on the exact size of the duplication and which genes are involved. There is currently no cure for Xq12-q13.3 duplication syndrome. Treatment focuses on managing individual symptoms and supporting development. This may include speech therapy, physical therapy, occupational therapy, and special education services. Seizures, if present, are managed with anti-seizure medications. Early intervention programs can help children reach their full developmental potential. A team of specialists typically works together to provide comprehensive care tailored to each person's needs.

Also known as:

Key symptoms:

Intellectual disabilityDelayed speech and language developmentLow muscle tone (floppiness)Feeding difficulties in infancyDistinctive facial featuresDelayed motor milestones like sitting and walkingSeizures or epilepsyBehavioral difficultiesLearning disabilitiesPoor coordinationGrowth delaysGenital abnormalities in males

Clinical phenotype terms (37)— hover any for plain English
Cutaneous finger syndactylyHP:0010554
Inheritance

X-linked dominant

Carried on the X chromosome; a single copy can cause the condition

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Xq12-q13.3 duplication syndrome.

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No actively recruiting trials found for Xq12-q13.3 duplication syndrome at this time.

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No specialists are currently listed for Xq12-q13.3 duplication syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Xq12-q13.3 duplication syndrome.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the exact size and location of my child's duplication, and which genes are involved?,How might this specific duplication affect my child's development over time?,What therapies should we start right away, and how often should they occur?,Should we be screening for seizures or other medical complications?,Is there a risk that other family members carry this duplication?,What educational supports should we request for my child at school?,Are there any research studies or registries we should consider joining?

Common questions about Xq12-q13.3 duplication syndrome

What is Xq12-q13.3 duplication syndrome?

Xq12-q13.3 duplication syndrome is a very rare genetic condition caused by having an extra copy of a specific region on the X chromosome, between positions Xq12 and Xq13.3. This duplication means that certain genes in this region are present in more copies than usual, which can disrupt normal development. The condition primarily affects males more severely than females, since males have only one X chromosome and the extra genetic material has a greater impact. People with this syndrome typically show developmental delays, intellectual disability, and various physical features that may be noti

How is Xq12-q13.3 duplication syndrome inherited?

Xq12-q13.3 duplication syndrome follows a x-linked dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Xq12-q13.3 duplication syndrome typically begin?

Typical onset of Xq12-q13.3 duplication syndrome is infantile. Age of onset can vary across affected individuals.