X-linked intellectual disability, Cilliers type

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Overview

X-linked intellectual disability, Cilliers type (also known as Cilliers syndrome) is an extremely rare genetic condition that primarily affects males. It was first described by Dr. Cilliers and is characterized by intellectual disability combined with distinctive physical features. The condition is caused by a change on the X chromosome, which is why it mainly affects boys and men, while females who carry the gene change are usually unaffected or only mildly affected. Key features of this condition include intellectual disability that can range from mild to severe, along with characteristic facial features and possible skeletal abnormalities. Some individuals may also have growth delays and other developmental differences. Because the condition is so rare, with only a handful of cases described in the medical literature, the full range of symptoms is not completely understood. There is currently no cure for this condition. Treatment focuses on managing symptoms and supporting development. This typically includes special education services, speech therapy, occupational therapy, and physical therapy as needed. Early intervention programs can help children reach their full potential. Regular follow-up with a team of specialists is important to monitor development and address any new concerns as they arise.

Also known as:

Key symptoms:

Intellectual disabilityDelayed speech and language developmentDistinctive facial featuresGrowth delaysDelayed motor milestones such as sitting and walkingSkeletal abnormalitiesLearning difficultiesBehavioral challengesLow muscle tonePossible seizures

Clinical phenotype terms (25)— hover any for plain English
Small nailHP:0001792Absence of secondary sex characteristicsHP:0008187
Inheritance

X-linked recessive

Carried on the X chromosome; typically affects males more than females

Age of Onset

Infantile

Begins in infancy, roughly 1 month to 2 years old

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for X-linked intellectual disability, Cilliers type.

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No actively recruiting trials found for X-linked intellectual disability, Cilliers type at this time.

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No specialists are currently listed for X-linked intellectual disability, Cilliers type.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to X-linked intellectual disability, Cilliers type.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the severity of my child's intellectual disability, and what level of support will they need?,What therapies should we start right away, and how often should they occur?,Should we pursue genetic testing to try to identify the exact gene involved?,Is there a risk of seizures, and what should I watch for?,What educational programs or early intervention services do you recommend?,What is the chance that future children in our family could be affected?,Are there any clinical trials or research studies we should know about?

Common questions about X-linked intellectual disability, Cilliers type

What is X-linked intellectual disability, Cilliers type?

X-linked intellectual disability, Cilliers type (also known as Cilliers syndrome) is an extremely rare genetic condition that primarily affects males. It was first described by Dr. Cilliers and is characterized by intellectual disability combined with distinctive physical features. The condition is caused by a change on the X chromosome, which is why it mainly affects boys and men, while females who carry the gene change are usually unaffected or only mildly affected. Key features of this condition include intellectual disability that can range from mild to severe, along with characteristic f

How is X-linked intellectual disability, Cilliers type inherited?

X-linked intellectual disability, Cilliers type follows a x-linked recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does X-linked intellectual disability, Cilliers type typically begin?

Typical onset of X-linked intellectual disability, Cilliers type is infantile. Age of onset can vary across affected individuals.