Venous thoracic outlet syndrome

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16Specialists8Treatment centers1Financial resources

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Overview

Venous thoracic outlet syndrome (also called Paget-Schroetter syndrome or effort thrombosis) is a condition where the large vein that carries blood from your arm back to your heart (the subclavian vein) becomes compressed or blocked in the narrow space between your collarbone and first rib. This area is called the thoracic outlet. When the vein is squeezed in this space, blood flow slows down and a blood clot can form. This condition most often affects young, otherwise healthy, and physically active people, particularly those who do repetitive overhead arm movements such as swimmers, baseball pitchers, weightlifters, or manual laborers. The main symptoms include sudden swelling of the arm, a feeling of heaviness or aching, bluish discoloration of the skin, and visible enlarged veins on the arm, shoulder, or chest. The condition typically affects one arm, usually the dominant one. Some people may notice their symptoms get worse with activity and improve with rest. Treatment usually involves a combination of approaches. Initially, blood-thinning medications (anticoagulants) are given to treat and prevent further clotting. Many patients also receive clot-dissolving therapy (thrombolysis) to break up the existing clot. In many cases, surgery is recommended to remove the first rib and relieve the compression on the vein. This procedure is called first rib resection. Without proper treatment, the condition can lead to long-term arm swelling, pain, and disability. With timely and appropriate treatment, most patients recover well and can return to their normal activities.

Also known as:

Key symptoms:

Sudden swelling of the armArm heaviness or achingBluish or purplish discoloration of the arm or handVisible enlarged veins on the arm, shoulder, or chestArm pain that worsens with activityFeeling of tightness in the armWarmth in the affected armNumbness or tingling in the hand or fingersWeakness in the affected armFatigue in the arm with useSwelling of the hand or fingers

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Venous thoracic outlet syndrome.

View clinical trials →

No actively recruiting trials found for Venous thoracic outlet syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Venous thoracic outlet syndrome community →

Specialists

16 foundView all specialists →
PS
Payam Salehi
BOSTON, MA
Specialist
2 Venous thoracic outlet syndrome publications
GB
Gert J de Borst
Specialist
5 Venous thoracic outlet syndrome publications
LS
Ludo Schropp
Specialist
4 Venous thoracic outlet syndrome publications
BP
Bart-Jeroen Petri
Specialist
4 Venous thoracic outlet syndrome publications
RT
Robert W Thompson
Specialist
3 Venous thoracic outlet syndrome publications
EH
Eline S van Hattum
Specialist
3 Venous thoracic outlet syndrome publications
MD
Mark G Davies
Specialist
2 Venous thoracic outlet syndrome publications
JH
Joseph P Hart
Specialist
2 Venous thoracic outlet syndrome publications
KR
Keivan Ranjbar
Specialist
2 Venous thoracic outlet syndrome publications
KI
Karl A Illig
TAMPA, FL
Specialist
2 Venous thoracic outlet syndrome publications
PK
Pavan K Kavali
SAINT LOUIS, MO
Specialist
2 Venous thoracic outlet syndrome publications
EV
Evert-Jan Vonken
Specialist
2 Venous thoracic outlet syndrome publications
JT
Joep A W Teijink
Specialist
2 Venous thoracic outlet syndrome publications
PH
Peiman Habibollahi
HOUSTON, TX
Specialist
1 Venous thoracic outlet syndrome publication
SP
Scott Cameron, MD, PhD
Specialist
PI on 1 active trial
AA
Abdulhameed Aziz
ATLANTA, GA
Specialist
2 Venous thoracic outlet syndrome publications

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Financial Resources

1 resources

Ceprotin

Baxalta US, Inc.

Ceprotin — Contact Baxalta US, Inc.

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Patient Assistance
Manufacturer Program
Accepting applications

Travel Grants

No travel grants are currently matched to Venous thoracic outlet syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Venous thoracic outlet syndrome

No recent news articles for Venous thoracic outlet syndrome.

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is the blood clot, and has it caused any permanent damage to my vein?,Do I need clot-dissolving therapy, surgery, or both?,How long will I need to take blood-thinning medication?,When can I return to work, sports, or normal daily activities?,What are the risks of the clot coming back after treatment?,Should I avoid certain activities or exercises in the future?,Are there any signs or symptoms I should watch for that would require emergency care?

Common questions about Venous thoracic outlet syndrome

What is Venous thoracic outlet syndrome?

Venous thoracic outlet syndrome (also called Paget-Schroetter syndrome or effort thrombosis) is a condition where the large vein that carries blood from your arm back to your heart (the subclavian vein) becomes compressed or blocked in the narrow space between your collarbone and first rib. This area is called the thoracic outlet. When the vein is squeezed in this space, blood flow slows down and a blood clot can form. This condition most often affects young, otherwise healthy, and physically active people, particularly those who do repetitive overhead arm movements such as swimmers, baseball

How is Venous thoracic outlet syndrome inherited?

Venous thoracic outlet syndrome follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Venous thoracic outlet syndrome typically begin?

Typical onset of Venous thoracic outlet syndrome is adult. Age of onset can vary across affected individuals.

Which specialists treat Venous thoracic outlet syndrome?

16 specialists and care centers treating Venous thoracic outlet syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.

What treatment and support options exist for Venous thoracic outlet syndrome?

1 patient support program are currently tracked on UniteRare for Venous thoracic outlet syndrome. See the treatments and support programs sections for copay assistance, eligibility, and contact details.