Urban-Rogers-Meyer syndrome

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ORPHA:3409OMIM:264010Q87.8
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Overview

Urban-Rogers-Meyer syndrome, also known as Urban syndrome or digitorenocerebral syndrome, is an extremely rare genetic condition that affects multiple body systems. It was first described in medical literature in the 1970s and involves a combination of birth defects affecting the fingers and toes, kidneys, and brain. People with this syndrome typically show abnormalities of the fingers and toes (such as short fingers or unusual bone development), kidney malformations, and intellectual disability or developmental delays. Some individuals may also have distinctive facial features and other skeletal abnormalities. The severity of symptoms can vary from person to person, but the combination of limb, kidney, and brain involvement is the hallmark of this condition. Because this syndrome is so rare, there is no specific cure or targeted treatment available. Management focuses on addressing each symptom individually. This may include special education support for developmental delays, monitoring kidney function, and orthopedic care for bone and limb abnormalities. A team of specialists working together provides the best approach to care. Early intervention services for developmental concerns can help children reach their full potential.

Also known as:

Key symptoms:

Short fingers and toesAbnormal bone development in the hands and feetKidney malformationsIntellectual disabilityDevelopmental delaysUnusual facial featuresSmall head sizeSkeletal abnormalitiesLow muscle toneGrowth delays

Clinical phenotype terms (28)— hover any for plain English
Abnormality of the philtrumHP:0000288Abnormal diaphysis morphologyHP:0000940Flexion contracture of toeHP:0005830
Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Urban-Rogers-Meyer syndrome.

View clinical trials →

No actively recruiting trials found for Urban-Rogers-Meyer syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Urban-Rogers-Meyer syndrome community →

No specialists are currently listed for Urban-Rogers-Meyer syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Urban-Rogers-Meyer syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Urban-Rogers-Meyer syndrome

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.How severe is my child's kidney involvement, and what monitoring schedule do we need?,What developmental therapies should we start, and how soon?,Are there any genetic tests that could help confirm the diagnosis or identify the specific cause?,What signs of kidney problems should I watch for at home?,Will my child need surgery for any of the bone or limb abnormalities?,What is the chance of having another child with this condition?,Are there any specialists or centers with experience in this syndrome that you would recommend?

Common questions about Urban-Rogers-Meyer syndrome

What is Urban-Rogers-Meyer syndrome?

Urban-Rogers-Meyer syndrome, also known as Urban syndrome or digitorenocerebral syndrome, is an extremely rare genetic condition that affects multiple body systems. It was first described in medical literature in the 1970s and involves a combination of birth defects affecting the fingers and toes, kidneys, and brain. People with this syndrome typically show abnormalities of the fingers and toes (such as short fingers or unusual bone development), kidney malformations, and intellectual disability or developmental delays. Some individuals may also have distinctive facial features and other skel

How is Urban-Rogers-Meyer syndrome inherited?

Urban-Rogers-Meyer syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Urban-Rogers-Meyer syndrome typically begin?

Typical onset of Urban-Rogers-Meyer syndrome is neonatal. Age of onset can vary across affected individuals.