Upper limb hypertrophy

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1Active trials6Specialists8Treatment centers

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Overview

Upper limb hypertrophy is a rare congenital condition in which one or both arms or hands are noticeably larger than normal. This overgrowth can involve the bones, muscles, fat, skin, or a combination of these tissues in the upper limbs. The condition is typically present at birth or becomes apparent during early childhood as the affected limb grows disproportionately compared to the rest of the body. It falls under the broader category of limb overgrowth disorders. People with upper limb hypertrophy may notice that one arm or hand is significantly bigger than the other, which can affect grip strength, fine motor skills, and the ability to perform everyday tasks. The degree of enlargement varies widely — some individuals have mild asymmetry while others experience substantial size differences that can impact function and appearance. In some cases, the overgrowth may be part of a broader overgrowth syndrome affecting other parts of the body. Treatment is generally tailored to the individual and focuses on improving function and appearance. Options may include physical therapy, occupational therapy, orthopedic interventions, and in some cases surgery to reduce the size of the affected limb or correct skeletal abnormalities. There is currently no single cure, and management is typically supportive and multidisciplinary. Early evaluation by specialists can help guide the best approach for each patient.

Key symptoms:

One arm or hand noticeably larger than the otherIncreased length of the affected armIncreased girth or thickness of the affected arm or handEnlarged fingers on the affected sideAsymmetry between the two upper limbsDifficulty with fine motor tasks like writing or buttoning clothesReduced range of motion in the affected limbSoft tissue swelling in the arm or handBone overgrowth visible on X-rayCosmetic concerns about limb appearancePossible vascular abnormalities in the affected limb

Inheritance

Variable

Can be inherited in different ways depending on the underlying gene

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗NORD ↗

FDA & Trial Timeline

6 events
Jan 2026A Study to Assess the Real-World Effectiveness of Mavacamten in Adult Patients With Obstructive Hypertrophic Cardiomyopathy in China

Bristol-Myers Squibb

TrialRECRUITING
Sep 2025A Study of Mavacamten in Adults With Obstructive Hypertrophic Cardiomyopathy in India (ROVER)

Bristol-Myers Squibb — PHASE4

TrialRECRUITING
Jun 2025A Study to Learn More About How Well Aficamten Works in Japanese Participants With Symptomatic Obstructive Hypertrophic Cardiomyopathy

Bayer — PHASE3

TrialACTIVE NOT RECRUITING
Aug 2024Applicability of Tissue Flossing for Blood Flow Restriction in the Upper Limb: Reliability and Performance Analysis

Paulista University — NA

TrialENROLLING BY INVITATION
Mar 2024Septal Ablation for Obstructive HCM

SuZhou Sinus Medical Technologies Co.,Ltd — NA

TrialACTIVE NOT RECRUITING
Jan 2024A Study to Evaluate Mavacamten Impact on Myocardial Structure in Participants With Symptomatic Obstructive Hypertrophic Cardiomyopathy

Bristol-Myers Squibb — PHASE4

TrialACTIVE NOT RECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Upper limb hypertrophy.

1 clinical trialare actively recruiting — trials can provide access to cutting-edge therapies.

View clinical trials →

Clinical Trials

1 recruitingView all trials with filters →
N/A1 trial
Applicability of Tissue Flossing for Blood Flow Restriction in the Upper Limb: Reliability and Performance Analysis
N/A
Enrolling by Invitation
· Sites: Presidente Prudente, São Paulo · Age: 1830 yrs

Specialists

6 foundView all specialists →
KP
Karolina Grąt, PhD
Specialist
PI on 1 active trial
KP
Kyu-Sung Lee, Ph.D
Specialist
PI on 2 active trials
CP
Cameron J Mitchell, PhD
Specialist
PI on 1 active trial
CM
Claude Schulman, MD
Specialist
PI on 1 active trial
SP
Stuart Phillips, PhD
Specialist
PI on 1 active trial

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Upper limb hypertrophy.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Upper limb hypertrophy

Disease timeline:

New recruiting trial: A Study of Mavacamten in Adults With Obstructive Hypertrophic Cardiomyopathy in India (ROVER)

A new clinical trial is recruiting patients for Upper limb hypertrophy

New recruiting trial: TANGO-LIVER Three Arm Nuclear Growth Observation in Liver Surgery

A new clinical trial is recruiting patients for Upper limb hypertrophy

New recruiting trial: A Study to Assess the Real-World Effectiveness of Mavacamten in Adult Patients With Obstructive Hypertrophic Cardiomyopathy in China

A new clinical trial is recruiting patients for Upper limb hypertrophy

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is causing the overgrowth in my child's arm, and could it be part of a genetic syndrome?,Should we pursue genetic testing, and if so, what type of testing is recommended?,How likely is the size difference to increase as my child grows?,What treatment options are available, and when is surgery recommended?,Are there any targeted medications, like alpelisib, that might be appropriate for our situation?,What therapies can help improve hand function and daily activities?,How often should we schedule follow-up visits to monitor the condition?

Common questions about Upper limb hypertrophy

What is Upper limb hypertrophy?

Upper limb hypertrophy is a rare congenital condition in which one or both arms or hands are noticeably larger than normal. This overgrowth can involve the bones, muscles, fat, skin, or a combination of these tissues in the upper limbs. The condition is typically present at birth or becomes apparent during early childhood as the affected limb grows disproportionately compared to the rest of the body. It falls under the broader category of limb overgrowth disorders. People with upper limb hypertrophy may notice that one arm or hand is significantly bigger than the other, which can affect grip

At what age does Upper limb hypertrophy typically begin?

Typical onset of Upper limb hypertrophy is neonatal. Age of onset can vary across affected individuals.

Are there clinical trials for Upper limb hypertrophy?

Yes — 1 recruiting clinical trial is currently listed for Upper limb hypertrophy on UniteRare. See the clinical trials section on this page for phase, sponsor, and site details sourced from ClinicalTrials.gov.

Which specialists treat Upper limb hypertrophy?

6 specialists and care centers treating Upper limb hypertrophy are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.