Ulnar/fibula ray defect-brachydactyly syndrome

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:52056OMIM:608571Q73.8
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

Ulnar/fibula ray defect-brachydactyly syndrome is a very rare inherited condition that affects the development of the limbs, particularly the bones of the hands, feet, arms, and legs. The name describes the two main features: defects in the 'ulnar ray' (the little-finger side of the arm and hand) and the 'fibula ray' (the outer bone of the lower leg and the little-toe side of the foot), combined with brachydactyly, which means unusually short fingers and/or toes. This condition is also sometimes referred to by its Orphanet classification number (ORPHA:52056) in medical literature. People with this syndrome are typically born with visible differences in their limbs. These may include missing or underdeveloped bones on the outer side of the arms or legs, shortened fingers or toes, and in some cases, missing digits. The severity can vary from person to person, even within the same family. The condition does not usually affect intelligence or internal organs, so most people with this syndrome have a normal life expectancy. Treatment focuses on managing the physical differences rather than curing the underlying cause. Orthopedic surgery, physical therapy, and the use of prosthetics or orthotics can help improve function and quality of life. A team of specialists including orthopedic surgeons, hand surgeons, and physical therapists typically work together to support affected individuals from childhood onward.

Also known as:

Key symptoms:

Short fingers or toes (brachydactyly)Missing or underdeveloped bones on the little-finger side of the hand or arm (ulnar ray defect)Missing or underdeveloped bones on the outer side of the lower leg or foot (fibula ray defect)Absent or reduced number of fingers or toesDifferences in the shape or length of the forearmDifferences in the shape or length of the lower legDifficulty with fine motor tasks due to hand differencesDifferences in foot shape that may affect walking

Clinical phenotype terms (12)— hover any for plain English
Postaxial oligodactylyHP:0006210Aplasia/Hypoplasia of the fibulaHP:0006492Aplasia/Hypoplasia of the ulnaHP:0006495Short 5th fingerHP:0009237
Inheritance

Autosomal dominant

Passed on from just one parent; each child has about a 50% chance of inheriting it

Age of Onset

Neonatal

Begins at or shortly after birth (first 4 weeks)

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Ulnar/fibula ray defect-brachydactyly syndrome.

View clinical trials →

No actively recruiting trials found for Ulnar/fibula ray defect-brachydactyly syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Ulnar/fibula ray defect-brachydactyly syndrome community →

No specialists are currently listed for Ulnar/fibula ray defect-brachydactyly syndrome.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Ulnar/fibula ray defect-brachydactyly syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

Open Ulnar/fibula ray defect-brachydactyly syndromeForum →

No community posts yet. Be the first to share your experience with Ulnar/fibula ray defect-brachydactyly syndrome.

Start the conversation →

Latest news about Ulnar/fibula ray defect-brachydactyly syndrome

No recent news articles for Ulnar/fibula ray defect-brachydactyly syndrome.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific bones are affected in my child, and how will this change as they grow?,Should we do genetic testing, and what might it tell us about the cause and risk for other family members?,What surgeries, if any, would you recommend and at what age?,What therapies should we start now to help with hand and leg function?,Are there any adaptive tools or devices that would help my child with daily activities?,What should I watch for that would mean we need to come back sooner or see another specialist?,Are there any clinical trials or research studies we could participate in?

Common questions about Ulnar/fibula ray defect-brachydactyly syndrome

What is Ulnar/fibula ray defect-brachydactyly syndrome?

Ulnar/fibula ray defect-brachydactyly syndrome is a very rare inherited condition that affects the development of the limbs, particularly the bones of the hands, feet, arms, and legs. The name describes the two main features: defects in the 'ulnar ray' (the little-finger side of the arm and hand) and the 'fibula ray' (the outer bone of the lower leg and the little-toe side of the foot), combined with brachydactyly, which means unusually short fingers and/or toes. This condition is also sometimes referred to by its Orphanet classification number (ORPHA:52056) in medical literature. People with

How is Ulnar/fibula ray defect-brachydactyly syndrome inherited?

Ulnar/fibula ray defect-brachydactyly syndrome follows a autosomal dominant inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Ulnar/fibula ray defect-brachydactyly syndrome typically begin?

Typical onset of Ulnar/fibula ray defect-brachydactyly syndrome is neonatal. Age of onset can vary across affected individuals.