Tropical endomyocardial fibrosis

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10Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Tropical endomyocardial fibrosis (EMF) is a serious heart disease that mainly affects people living in tropical regions of the world. It causes scar tissue (fibrosis) to build up inside the heart, particularly in the lower chambers (ventricles). Over time, this scarring makes the heart walls stiff and reduces the heart's ability to fill with blood properly. The disease can affect the right side of the heart, the left side, or both sides at the same time. It is also sometimes called tropical restrictive cardiomyopathy. As the scarring progresses, the heart becomes less efficient at pumping blood around the body. This leads to symptoms of heart failure, such as swelling in the legs and abdomen, shortness of breath, and extreme tiredness. The valves inside the heart can also be affected, causing blood to leak backward. In some cases, blood clots can form inside the heart, raising the risk of stroke. Treatment focuses on managing symptoms of heart failure using medications such as diuretics (water pills) to reduce fluid buildup, and blood thinners to prevent clots. In more advanced cases, surgery to remove the scar tissue (called pericardiectomy or endocardiectomy) or to repair heart valves may be considered. There is currently no cure, and the disease can progress despite treatment, making early diagnosis very important.

Also known as:

Key symptoms:

Swelling of the legs, ankles, or feetSwollen or bloated abdomen due to fluid buildupShortness of breath, especially when lying down or during activityExtreme tiredness and low energyRapid or irregular heartbeat (palpitations)Chest pain or discomfortCoughing, sometimes with pink or frothy mucusReduced ability to exercise or do physical activityFainting or dizzinessWeight loss and poor appetiteBluish tinge to the lips or fingertips (in severe cases)Stroke-like symptoms if a blood clot travels to the brain

Clinical phenotype terms (48)— hover any for plain English
Endocardial fibrosisHP:0006685Restrictive cardiomyopathyHP:0001723Atrioventricular blockHP:0001678Prolonged QRS complexHP:0006677Complete right bundle branch blockHP:0011712Left bundle branch blockHP:0011713Abnormal ST segmentHP:0012249OrthopneaHP:0012764
Inheritance

Multifactorial

Caused by a mix of several genes and environmental factors

Age of Onset

Variable

Can begin at different ages, from infancy through adulthood

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Tropical endomyocardial fibrosis.

View clinical trials →

No actively recruiting trials found for Tropical endomyocardial fibrosis at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Tropical endomyocardial fibrosis community →

Specialists

10 foundView all specialists →
HJ
Hamid Jallal
Specialist
1 Tropical endomyocardial fibrosis publication
SB
Soufiane Belabbes
Specialist
1 Tropical endomyocardial fibrosis publication
AK
Ali Khatouri
Specialist
1 Tropical endomyocardial fibrosis publication
SC
Sofía Cuenca
Specialist
1 Tropical endomyocardial fibrosis publication
MB
Marie Philomène Bitchou
Specialist
1 Tropical endomyocardial fibrosis publication
GM
Gonzalo Morales-Jiménez
Specialist
1 Tropical endomyocardial fibrosis publication
BS
Barbara Segulin
Specialist
1 Tropical endomyocardial fibrosis publication
NM
Nikolaos Miaris
Specialist
1 Tropical endomyocardial fibrosis publication
MC
Mohssen Chabok
Specialist
1 Tropical endomyocardial fibrosis publication
CB
Chiara Bucciarelli-Ducci
Specialist
1 Tropical endomyocardial fibrosis publication

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Tropical endomyocardial fibrosis.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Tropical endomyocardial fibrosis

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.Which side of my heart is affected, and how severe is the scarring right now?,What medications do I need, and what are the side effects I should watch for?,Am I a candidate for surgery, and what would that involve?,How often do I need follow-up echocardiograms or other heart tests?,What warning signs should make me go to the emergency room immediately?,Are there any dietary or activity restrictions I need to follow?,What is the likely progression of my disease, and what can I do to slow it down?

Common questions about Tropical endomyocardial fibrosis

What is Tropical endomyocardial fibrosis?

Tropical endomyocardial fibrosis (EMF) is a serious heart disease that mainly affects people living in tropical regions of the world. It causes scar tissue (fibrosis) to build up inside the heart, particularly in the lower chambers (ventricles). Over time, this scarring makes the heart walls stiff and reduces the heart's ability to fill with blood properly. The disease can affect the right side of the heart, the left side, or both sides at the same time. It is also sometimes called tropical restrictive cardiomyopathy. As the scarring progresses, the heart becomes less efficient at pumping blo

How is Tropical endomyocardial fibrosis inherited?

Tropical endomyocardial fibrosis follows a multifactorial inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

Which specialists treat Tropical endomyocardial fibrosis?

10 specialists and care centers treating Tropical endomyocardial fibrosis are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.