Squamous cell carcinoma of liver and intrahepatic biliary tract

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Overview

Squamous cell carcinoma of the liver and intrahepatic biliary tract is a very rare type of cancer that starts in the liver or in the bile ducts located inside the liver. The bile ducts are small tubes that carry bile (a digestive fluid) from the liver to the small intestine. This cancer is called 'squamous cell' because it grows from a specific type of flat cell that is not normally found in large numbers in the liver or bile ducts, making it unusual and different from the more common liver cancers like hepatocellular carcinoma or cholangiocarcinoma. This cancer can affect how the liver works, which is an organ responsible for filtering the blood, producing proteins, and helping with digestion. As the tumor grows, it can block bile flow, damage liver tissue, and spread to nearby organs or lymph nodes. Common symptoms include yellowing of the skin and eyes (jaundice), abdominal pain, unexplained weight loss, fatigue, and loss of appetite. Treatment usually involves a combination of surgery (if the tumor can be removed), chemotherapy, and sometimes radiation therapy. Because this cancer is so rare, there are no treatments specifically approved just for this type, and doctors often follow guidelines used for other liver or bile duct cancers. Early detection gives the best chance for treatment to work, but many cases are found at a late stage, making treatment more challenging.

Also known as:

Key symptoms:

Yellowing of the skin and whites of the eyes (jaundice)Pain or discomfort in the upper right side of the abdomenUnexplained weight lossFeeling very tired or weakLoss of appetiteDark-colored urinePale or clay-colored stoolsNausea or vomitingSwelling or bloating in the bellyItchy skinFever without a clear cause

Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

FDA & Trial Timeline

1 event
Mar 2006

Erbitux: FDA approved

For use in combination with radiation therapy, for the treatment of locally or regionally advanced squamous cell carcinoma of the head and neck (SCCHN) and for use as a single agent for the treatment of patients with recurrent or metastatic SCCHN for whom prior platinum-based therapy has failed

FDAcompleted

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

1 available

Erbitux

cetuximab· ImClone Systems Incorporated■ Boxed WarningOrphan Drug
For use in combination with radiation therapy, for the treatment of locally or regionally advanced squamous cell carcinoma of the head and neck (SCCHN) and for use as a single agent for the treatment

For use in combination with radiation therapy, for the treatment of locally or regionally advanced squamous cell carcinoma of the head and neck (SCCHN) and for use as a single agent for the treatment of patients with recurrent or metastatic SCCHN for whom prior platinum-based therapy has failed

No actively recruiting trials found for Squamous cell carcinoma of liver and intrahepatic biliary tract at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Squamous cell carcinoma of liver and intrahepatic biliary tract community →

No specialists are currently listed for Squamous cell carcinoma of liver and intrahepatic biliary tract.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Squamous cell carcinoma of liver and intrahepatic biliary tract.

Search all travel grants →NORD Financial Assistance ↗

Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What stage is my cancer, and has it spread beyond the liver?,Is surgery or any other curative treatment an option for me?,Should my tumor be tested for specific genetic changes that might guide treatment?,Are there any clinical trials I might be eligible for?,What chemotherapy or other systemic treatments do you recommend, and what are the side effects?,How will we know if the treatment is working, and how often will I be monitored?,What palliative care or support services are available to help manage my symptoms and quality of life?

Common questions about Squamous cell carcinoma of liver and intrahepatic biliary tract

What is Squamous cell carcinoma of liver and intrahepatic biliary tract?

Squamous cell carcinoma of the liver and intrahepatic biliary tract is a very rare type of cancer that starts in the liver or in the bile ducts located inside the liver. The bile ducts are small tubes that carry bile (a digestive fluid) from the liver to the small intestine. This cancer is called 'squamous cell' because it grows from a specific type of flat cell that is not normally found in large numbers in the liver or bile ducts, making it unusual and different from the more common liver cancers like hepatocellular carcinoma or cholangiocarcinoma. This cancer can affect how the liver works

How is Squamous cell carcinoma of liver and intrahepatic biliary tract inherited?

Squamous cell carcinoma of liver and intrahepatic biliary tract follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Squamous cell carcinoma of liver and intrahepatic biliary tract typically begin?

Typical onset of Squamous cell carcinoma of liver and intrahepatic biliary tract is adult. Age of onset can vary across affected individuals.