Spondyloepiphyseal dysplasia, Reardon type

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ORPHA:163662OMIM:600561Q77.7
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Overview

Spondyloepiphyseal dysplasia, Reardon type is an extremely rare genetic skeletal disorder that affects the growth and development of bones, particularly the spine (spondylo-) and the ends of long bones called epiphyses. This condition belongs to a group of disorders known as spondyloepiphyseal dysplasias (SEDs), which are characterized by abnormal bone and cartilage development. The Reardon type is specifically associated with short stature, skeletal abnormalities, and distinctive changes visible on X-rays of the spine and joints. People with this condition typically show signs in early life, including short trunk, abnormalities of the vertebrae (the bones of the spine), and changes in the hip joints and other large joints. The limbs may appear relatively normal in proportion compared to the shortened trunk. Some individuals may also experience joint pain or stiffness as they grow older, and there may be associated features such as hearing loss, which has been described in some cases of this specific subtype. There is currently no cure for spondyloepiphyseal dysplasia, Reardon type. Treatment focuses on managing symptoms and preventing complications. This may include orthopedic interventions for skeletal problems, physical therapy to maintain mobility and strength, pain management, and monitoring for complications such as spinal cord compression. A team of specialists typically works together to provide comprehensive care for affected individuals.

Key symptoms:

Short stature with a short trunkAbnormal curvature of the spineFlattened vertebrae visible on X-rayUnderdeveloped hip jointsJoint stiffness or limited range of motionJoint pain, especially in the hips and kneesWaddling gait or difficulty walkingHearing loss (sensorineural)Barrel-shaped chestDelayed bone development at the ends of long bonesShort neck

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗OMIM ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Spondyloepiphyseal dysplasia, Reardon type.

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No actively recruiting trials found for Spondyloepiphyseal dysplasia, Reardon type at this time.

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No specialists are currently listed for Spondyloepiphyseal dysplasia, Reardon type.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Spondyloepiphyseal dysplasia, Reardon type.

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Community

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Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

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Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

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Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic testing should be done to confirm the diagnosis?,How often should my child have skeletal X-rays and orthopedic check-ups?,Should we screen for hearing loss, and how often?,What signs of spinal cord compression should I watch for?,Are there physical activities that should be avoided to protect the joints and spine?,What therapies or interventions can help maintain mobility and reduce pain?,Is genetic counseling recommended for our family regarding future pregnancies?

Common questions about Spondyloepiphyseal dysplasia, Reardon type

What is Spondyloepiphyseal dysplasia, Reardon type?

Spondyloepiphyseal dysplasia, Reardon type is an extremely rare genetic skeletal disorder that affects the growth and development of bones, particularly the spine (spondylo-) and the ends of long bones called epiphyses. This condition belongs to a group of disorders known as spondyloepiphyseal dysplasias (SEDs), which are characterized by abnormal bone and cartilage development. The Reardon type is specifically associated with short stature, skeletal abnormalities, and distinctive changes visible on X-rays of the spine and joints. People with this condition typically show signs in early life,

How is Spondyloepiphyseal dysplasia, Reardon type inherited?

Spondyloepiphyseal dysplasia, Reardon type follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Spondyloepiphyseal dysplasia, Reardon type typically begin?

Typical onset of Spondyloepiphyseal dysplasia, Reardon type is childhood. Age of onset can vary across affected individuals.