Somatomammotropinoma

Last reviewed

🖨 Print for my doctorAdvocacy Hub →
ORPHA:314769D35.2
Who is this for?
Show terms as
8Treatment centers

Where are you in your journey?

UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
Report missing data

Overview

A somatomammotropinoma is a rare, usually benign (non-cancerous) tumor of the pituitary gland, a small gland located at the base of the brain. This tumor produces too much of two hormones: growth hormone (GH) and prolactin (PRL). Growth hormone controls how the body grows, while prolactin is involved in breast milk production and affects reproductive function. Because the tumor overproduces both hormones at the same time, patients can experience symptoms related to excess of each. When growth hormone levels are too high in adults, it leads to a condition called acromegaly, which causes gradual enlargement of the hands, feet, and facial features, along with joint pain, excessive sweating, and fatigue. In children or adolescents who are still growing, excess growth hormone can cause gigantism, meaning unusually rapid and tall growth. At the same time, high prolactin levels can cause irregular or absent menstrual periods in women, breast milk production unrelated to pregnancy, decreased sex drive, and fertility problems in both men and women. The tumor itself can also cause problems by pressing on nearby structures in the brain, leading to headaches and vision changes, especially loss of peripheral (side) vision. Treatment typically involves a combination of surgery, medications, and sometimes radiation therapy. The goal is to remove or shrink the tumor, bring hormone levels back to normal, and relieve pressure on surrounding brain tissue. With proper treatment, many patients can achieve good control of their symptoms and hormone levels.

Also known as:

Key symptoms:

Enlargement of hands and feetChanges in facial features such as a larger jaw or browHeadachesLoss of side vision (peripheral vision loss)Irregular or absent menstrual periodsUnexpected breast milk productionDecreased sex driveFertility problemsExcessive sweatingJoint pain and stiffnessFatigue and low energyWeight gainThickening of the skinSleep apnea or snoringErectile dysfunction in men

Clinical phenotype terms (50)— hover any for plain English
Anterior hypopituitarismHP:0000830Elevated circulating growth hormone concentrationHP:0000845Broad footHP:0001769Deep plantar creasesHP:0001869
Inheritance

Sporadic

Usually appears on its own, not inherited from a parent

Age of Onset

Adult

Begins in adulthood (age 18 or older)

Orphanet ↗NORD ↗

Treatments

No FDA-approved treatments are currently listed for Somatomammotropinoma.

View clinical trials →

No actively recruiting trials found for Somatomammotropinoma at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Somatomammotropinoma community →

No specialists are currently listed for Somatomammotropinoma.

View NORD Rare Disease Centers ↗Undiagnosed Disease Network ↗

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Somatomammotropinoma.

Search all travel grants →NORD Financial Assistance ↗

Community

Open SomatomammotropinomaForum →

No community posts yet. Be the first to share your experience with Somatomammotropinoma.

Start the conversation →

Latest news about Somatomammotropinoma

No recent news articles for Somatomammotropinoma.

Follow this condition to be notified when news becomes available.

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What is the size of my tumor, and is it pressing on any important structures?,Is surgery recommended in my case, and what are the chances it will cure the condition?,What medications will I need, and what are their side effects?,How often will I need blood tests and MRI scans for monitoring?,Could this tumor be part of a genetic syndrome, and should my family members be tested?,What are the long-term health risks I should watch for, even after treatment?,Will this condition affect my ability to have children, and are there options to preserve fertility?

Common questions about Somatomammotropinoma

What is Somatomammotropinoma?

A somatomammotropinoma is a rare, usually benign (non-cancerous) tumor of the pituitary gland, a small gland located at the base of the brain. This tumor produces too much of two hormones: growth hormone (GH) and prolactin (PRL). Growth hormone controls how the body grows, while prolactin is involved in breast milk production and affects reproductive function. Because the tumor overproduces both hormones at the same time, patients can experience symptoms related to excess of each. When growth hormone levels are too high in adults, it leads to a condition called acromegaly, which causes gradua

How is Somatomammotropinoma inherited?

Somatomammotropinoma follows a sporadic inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Somatomammotropinoma typically begin?

Typical onset of Somatomammotropinoma is adult. Age of onset can vary across affected individuals.