Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome

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ORPHA:314394OMIM:614813Q87.1
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2Specialists8Treatment centers

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UniteRare data is sourced from FDA.gov, ClinicalTrials.gov, Orphanet, OMIM, and NORD.
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Overview

Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome (sometimes abbreviated as SOFT syndrome or referred to by its descriptive name) is an extremely rare genetic condition that affects several parts of the body. The hallmark features include shorter-than-expected height (short stature), abnormalities of the nails (onychodysplasia), distinctive facial features (facial dysmorphism), and thin or sparse hair (hypotrichosis). Children with this condition are often noticeably smaller than their peers from early in life, and their nails may appear underdeveloped, thin, or abnormally shaped. Facial features can include a broad forehead, a flat or underdeveloped midface, a small nose, and other subtle differences. Hair on the scalp and body tends to be sparse and fine. Because this syndrome is so rare, the full range of symptoms and their severity can vary from person to person. Some individuals may have additional findings such as mild developmental differences or dental abnormalities. There is currently no cure for this condition, and treatment focuses on managing individual symptoms. Growth hormone therapy may be considered for short stature, and dermatological care can help with nail and hair concerns. Regular follow-up with a team of specialists is important to monitor growth, development, and any emerging health issues. Research into the genetic basis of this syndrome is ongoing, and genetic counseling is recommended for affected families.

Also known as:

Key symptoms:

Short stature or growth delayAbnormal or underdeveloped nailsThin or sparse hair on the scalpSparse body hairDistinctive facial featuresBroad or prominent foreheadFlat or underdeveloped midfaceSmall noseDental abnormalitiesThin or dry skinDelayed bone age

Inheritance

Autosomal recessive

Passed on when both parents carry the same gene change; often skips generations

Age of Onset

Childhood

Begins in childhood, roughly ages 1 to 12

Orphanet ↗OMIM ↗NORD ↗

FDA & Trial Timeline

10 events
Mar 2026Evaluation of the Safety and Performance of the Medical Device RDM36 in the Treatment of Periodontal Gingival Contraction and in Black Triangles Syndrome (BTS)

Mastelli S.r.l — NA

TrialNOT YET RECRUITING
Feb 2026Effectiveness of Instrumental Assisted Soft Tissue Mobilization Versus Conventional Treatment on Administrative Staff for Text Neck Syndrome

University of Health Sciences Lahore — NA

TrialACTIVE NOT RECRUITING
Feb 2026Effects of Myofascial Chain Tension Modulation Combined With Scapular Corrective Exercise on Scapular Movement Performance and Functional Outcomes in Tennis Players With Subacromial Impingement Syndrome

China Medical University Hospital — NA

TrialNOT YET RECRUITING
Jan 2026IASTM Effects on Pain, Functionality, and Proprioception in Subacromial Impingement

Istanbul Medipol University Hospital — NA

TrialRECRUITING
Nov 2025Clinical Study in Adult Patients With Purulent-inflammatory Processes of the Skin and Soft Tissues, Phase I-II of the Wound Process

Research Institute for Physical Chemical Problems of the Belarusian State University — PHASE2, PHASE3

TrialNOT YET RECRUITING
Feb 2025Performance and Safety of LightForce® Therapy Lasers on Shoulder Soft Tissue Inflammation Pain Reduction

DJO UK Ltd — NA

TrialRECRUITING
Oct 2024Comparison of IASTM and Muscle Energy Technique in Patellofemoral Pain Syndrome.

Riphah International University — NA

TrialRECRUITING
Mar 2023Autologous Fat Grafting in Radiated Soft Tissue Reconstruction

University of Chicago

TrialENROLLING BY INVITATION
Dec 2022Safety and Effectiveness of the Genio® bilAteral Stimulation for Treatment of Complete Concentric CollapsE and OSA.

Nyxoah S.A. — NA

TrialACTIVE NOT RECRUITING
Mar 2011The All Ireland Infectious Diseases Cohort Project

University College Dublin

TrialRECRUITING

Data sourced from FDA regulatory filings and ClinicalTrials.gov. Updated periodically.

Treatments

No FDA-approved treatments are currently listed for Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome.

View clinical trials →

No actively recruiting trials found for Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome at this time.

New trials open frequently. Follow this disease to get notified.

Search ClinicalTrials.gov ↗Join the Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome community →

Specialists

2 foundView all specialists →
JM
James L Gulley, M.D.
BETHESDA, MD
Specialist
PI on 7 active trials
KM
KINZA ANWAR, MS-OMPT
Specialist
PI on 4 active trials

Treatment Centers

8 centers
🏥 NORD

Baylor College of Medicine Rare Disease Center

Baylor College of Medicine

📍 Houston, TX

🏥 NORD

Stanford Medicine Rare Disease Center

Stanford Medicine

📍 Stanford, CA

🔬 UDN

NIH Clinical Center Undiagnosed Diseases Program

National Institutes of Health

📍 Bethesda, MD

🔬 UDN

UCLA UDN Clinical Site

UCLA Health

📍 Los Angeles, CA

🔬 UDN

Baylor College of Medicine UDN Clinical Site

Baylor College of Medicine

📍 Houston, TX

🔬 UDN

Harvard/MGH UDN Clinical Site

Massachusetts General Hospital

📍 Boston, MA

🏥 NORD

Mayo Clinic Center for Individualized Medicine

Mayo Clinic

📍 Rochester, MN

👤 Mayo Clinic Center for Individualized Medicine

🏥 NORD

UCLA Rare Disease Day Program

UCLA Health

📍 Los Angeles, CA

Travel Grants

No travel grants are currently matched to Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome.

Search all travel grants →NORD Financial Assistance ↗

Community

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Latest news about Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome

Disease timeline:

New recruiting trial: Comparison of IASTM and Muscle Energy Technique in Patellofemoral Pain Syndrome.

A new clinical trial is recruiting patients for Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome

New recruiting trial: Performance and Safety of LightForce® Therapy Lasers on Shoulder Soft Tissue Inflammation Pain Reduction

A new clinical trial is recruiting patients for Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome

New recruiting trial: IASTM Effects on Pain, Functionality, and Proprioception in Subacromial Impingement

A new clinical trial is recruiting patients for Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome

New recruiting trial: The All Ireland Infectious Diseases Cohort Project

A new clinical trial is recruiting patients for Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome

Caregiver Resources

NORD Caregiver Resources

Support, advocacy, and financial assistance for caregivers of rare disease patients.

Mental Health Support

Rare disease caregiving can be isolating. Connect with counseling and peer support.

Family & Caregiver Grants

Financial assistance programs specifically for caregivers of rare disease patients.

Social Security Disability

Learn how rare disease patients may qualify for SSDI/SSI benefits.

Questions for your doctor

Bring these to your next appointment

  • Q1.What specific genetic test confirmed my child's diagnosis, and what does the result mean?,Would growth hormone therapy be appropriate for my child, and what results can we expect?,How often should my child's growth and development be monitored?,Are there any treatments available for the nail or hair problems?,Should other family members be tested for this condition?,What specialists should be part of my child's care team?,Are there any clinical trials or research studies we could participate in?

Common questions about Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome

What is Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome?

Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome (sometimes abbreviated as SOFT syndrome or referred to by its descriptive name) is an extremely rare genetic condition that affects several parts of the body. The hallmark features include shorter-than-expected height (short stature), abnormalities of the nails (onychodysplasia), distinctive facial features (facial dysmorphism), and thin or sparse hair (hypotrichosis). Children with this condition are often noticeably smaller than their peers from early in life, and their nails may appear underdeveloped, thin, or abnormall

How is Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome inherited?

Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome follows a autosomal recessive inheritance pattern. Genetic counseling can help families understand recurrence risk and testing options.

At what age does Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome typically begin?

Typical onset of Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome is childhood. Age of onset can vary across affected individuals.

Which specialists treat Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome?

2 specialists and care centers treating Short stature-onychodysplasia-facial dysmorphism-hypotrichosis syndrome are listed on UniteRare, sourced from ClinicalTrials.gov principal investigators, published research, and the NPPES NPI registry.